Materiały źródłowe

• #1 Total anomalous pulmonary venous return (TAPVR) – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/total-anomalous-pulmonary-venous-return/cdc-20385613

  In total anomalous pulmonary venous return (TAPVR), the pulmonary veins incorrectly send blood to the heart’s upper right chamber. That chamber is called the right atrium. As a result, oxygen-rich blood mixes with oxygen-poor blood, as shown in purple. In a typical heart, shown on the left, oxygen-rich blood flows from the pulmonary veins to the upper left chamber, also called the left atrium. […] Total anomalous pulmonary venous return (TAPVR) is a rare heart condition that’s present at birth. That means it’s a congenital heart defect. […] Symptoms of total anomalous pulmonary venous return (TAPVR) in babies may include trouble breathing, poor feeding and a weak pulse. The baby’s skin may look gray or blue due to low oxygen levels. This is called cyanosis. Depending on skin color, these changes may be easier or harder to see. […] Symptoms of TAPVR may appear soon after birth. But some people don’t have symptoms until later in life.

• #2 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #3 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #4 Total anomalous pulmonary venous return (TAPVR) – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/total-anomalous-pulmonary-venous-return/cdc-20385613

  In total anomalous pulmonary venous return (TAPVR), the pulmonary veins incorrectly send blood to the heart’s upper right chamber. That chamber is called the right atrium. As a result, oxygen-rich blood mixes with oxygen-poor blood, as shown in purple. In a typical heart, shown on the left, oxygen-rich blood flows from the pulmonary veins to the upper left chamber, also called the left atrium. […] Total anomalous pulmonary venous return (TAPVR) is a rare heart condition that’s present at birth. That means it’s a congenital heart defect. […] Symptoms of total anomalous pulmonary venous return (TAPVR) in babies may include trouble breathing, poor feeding and a weak pulse. The baby’s skin may look gray or blue due to low oxygen levels. This is called cyanosis. Depending on skin color, these changes may be easier or harder to see. […] Symptoms of TAPVR may appear soon after birth. But some people don’t have symptoms until later in life.

• #5 Total Anomalous Pulmonary Venous Return (TAPVR) | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/total-anomalous-pulmonary-venous-return

  Most babies born with total anomalous pulmonary venous return (TAPVR) are very ill soon after birth. Symptoms may include: A bluish tint to the skin and lips […] Trouble breathing […] Rapid breathing […] Poor feeding or poor growth. If your child has any of these symptoms, your pediatrician may refer you to a pediatric cardiologist for testing. Children with TAPVR will need surgery in infancy to repair the problem. Newborns with severe TAPVR will need emergency surgery shortly after birth. They often need to be admitted to the cardiac intensive care unit (CICU) and require intensive support with medications and a ventilator (breathing machine). Some babies with severe TAPVR may need a specialized life support system called ECMO (extracorporeal membrane oxygenation), an advanced technology that functions as a replacement for a critically ill child’s heart and lungs. Babies with less severe TAPVR usually have surgery in the days or weeks after they’re diagnosed. Thanks to updates in surgical techniques for repairing TAPVR, the long-term outlook is continually improving. Children who have had a repair for TAPVR will require lifelong checkups with a cardiologist to make sure their veins remain open. If the veins become narrowed, they may need catheterizations or surgeries to repair these veins.

• #6 Total Anomalous Pulmonary Venous Return (TAPVR) – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=total-anomalous-pulmonary-venous-return-tapvr-90-P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to his or her body. Other symptoms can include fast or troubled breathing, fast heart rate, cool, clammy skin, tiredness and little movement, poor feeding, poor pulses, enlarged liver, and heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Your child will need to see a heart doctor for regular checkups for the rest of their life. Many children with TAPVR will grow and develop normally after they have surgery.

• #7 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #8 Total anomalous pulmonary venous return (TAPVR) – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/total-anomalous-pulmonary-venous-return/cdc-20385613

  In total anomalous pulmonary venous return (TAPVR), the pulmonary veins incorrectly send blood to the heart’s upper right chamber. That chamber is called the right atrium. As a result, oxygen-rich blood mixes with oxygen-poor blood, as shown in purple. In a typical heart, shown on the left, oxygen-rich blood flows from the pulmonary veins to the upper left chamber, also called the left atrium. […] Total anomalous pulmonary venous return (TAPVR) is a rare heart condition that’s present at birth. That means it’s a congenital heart defect. […] Symptoms of total anomalous pulmonary venous return (TAPVR) in babies may include trouble breathing, poor feeding and a weak pulse. The baby’s skin may look gray or blue due to low oxygen levels. This is called cyanosis. Depending on skin color, these changes may be easier or harder to see. […] Symptoms of TAPVR may appear soon after birth. But some people don’t have symptoms until later in life.

• #9 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #10 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #11 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #12 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #13 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #14 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #15 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #16 Anomalous pulmonary venous connection – Wikipedia

  https://en.wikipedia.org/wiki/Anomalous_pulmonary_venous_connection

  TAPVC with obstruction will clinically present with cyanosis, tachypnea, dyspnea, and hypoxemia. Chest x-ray may show a ground-glass appearance due to pulmonary edema resulting from increased pressure in the obstructed pulmonary veins. […] Cases of TAPVC with obstruction are considered a surgical emergency. […] In TAPVC without obstruction, surgical redirection can be performed within the first month of life. The operation is performed under general anesthesia. The four pulmonary veins are reconnected to the left atrium, and any associated heart defects such as atrial septal defect, ventricular septal defect, patent foramen ovale, and/or patent ductus arteriosus are surgically closed. With obstruction, surgery should be undertaken urgently.

• #17 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #18 Total Anomalous Pulmonary Venous Return | Thoracic Key

  https://thoracickey.com/total-anomalous-pulmonary-venous-return/

  When PVO is severe, neonates are critically ill with pulmonary venous hypertension resulting in pulmonary edema, reflex pulmonary arterial vasoconstriction, and pulmonary arterial hypertension with associated decreased pulmonary blood flow. […] The level of preoperative support required will reflect the pathophysiologic state of the patient and depends on the degree of PVO and pulmonary blood flow.

• #19 Total Anomalous Pulmonary Venous Return (TAPVR) – Children’s Health Issues – Merck Manual Consumer Version

  https://www.merckmanuals.com/home/children-s-health-issues/birth-defects-of-the-heart/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins, blood vessels that normally carry oxygenated blood from the lungs to the left side of the heart, connect instead to the right side of the heart. This blood then flows to the left heart through a hole in the wall separating the left and right heart chambers. […] Children with more mild forms of TAPVR may only have mild feeding and breathing problems in infancy. […] Children with more severe TAPVR may have bluish discoloration of the skin (cyanosis), shortness of breath, and fatigue. […] Children with the most severe forms of this defect may develop severe respiratory distress and cyanosis shortly after birth. […] Newborns with a severe form of TAPVR have difficulty breathing and bluish coloration of the skin (cyanosis). […] In milder forms, symptoms of heart failure may be present but be more difficult to detect. Symptoms of heart failure include shortness of breath, a bluish color to the skin (cyanosis), and fatigue. The level of oxygen is usually lower than normal, but some infants may have no symptoms or cyanosis.

• #20 Total Anomalous Pulmonary Venous Return (TAPVR) | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/total-anomalous-pulmonary-venous-return

  Most babies born with total anomalous pulmonary venous return (TAPVR) are very ill soon after birth. Symptoms may include: A bluish tint to the skin and lips […] Trouble breathing […] Rapid breathing […] Poor feeding or poor growth. If your child has any of these symptoms, your pediatrician may refer you to a pediatric cardiologist for testing. Children with TAPVR will need surgery in infancy to repair the problem. Newborns with severe TAPVR will need emergency surgery shortly after birth. They often need to be admitted to the cardiac intensive care unit (CICU) and require intensive support with medications and a ventilator (breathing machine). Some babies with severe TAPVR may need a specialized life support system called ECMO (extracorporeal membrane oxygenation), an advanced technology that functions as a replacement for a critically ill child’s heart and lungs. Babies with less severe TAPVR usually have surgery in the days or weeks after they’re diagnosed. Thanks to updates in surgical techniques for repairing TAPVR, the long-term outlook is continually improving. Children who have had a repair for TAPVR will require lifelong checkups with a cardiologist to make sure their veins remain open. If the veins become narrowed, they may need catheterizations or surgeries to repair these veins.

• #21 Total Anomalous Pulmonary Venous Return | Thoracic Key

  https://thoracickey.com/total-anomalous-pulmonary-venous-return/

  When PVO is severe, neonates are critically ill with pulmonary venous hypertension resulting in pulmonary edema, reflex pulmonary arterial vasoconstriction, and pulmonary arterial hypertension with associated decreased pulmonary blood flow. […] The level of preoperative support required will reflect the pathophysiologic state of the patient and depends on the degree of PVO and pulmonary blood flow.

• #22 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #23 Total Anomalous Pulmonary Venous Return (TAPVR) | University Hospitals

  https://www.uhhospitals.org/rainbow/services/congenital-heart/conditions-and-treatments/article/Diseases-and-Conditions—Pediatrics/total-anomalous-pulmonary-venous-return

  All children with a TAPVR will need to have surgery to fix it. Your baby will need to go into the intensive care unit (ICU) for treatment. […] The complications of TAPVR include: Enlarged heart, Lung problems, including respiratory failure and high blood pressure in the lungs, Abnormal heart rhythms, Shock, Heart failure, Slowed growth and development, Enlarged liver, Need for another surgery, Infection, Death. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will still need to see a heart doctor for regular checkups for the rest of their life.

• #24 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #25 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #26 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #27 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #28 Total Anomalous Pulmonary Venous Return (TAPVR) – Children’s Health Issues – Merck Manual Consumer Version

  https://www.merckmanuals.com/home/children-s-health-issues/birth-defects-of-the-heart/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins, blood vessels that normally carry oxygenated blood from the lungs to the left side of the heart, connect instead to the right side of the heart. This blood then flows to the left heart through a hole in the wall separating the left and right heart chambers. […] Children with more mild forms of TAPVR may only have mild feeding and breathing problems in infancy. […] Children with more severe TAPVR may have bluish discoloration of the skin (cyanosis), shortness of breath, and fatigue. […] Children with the most severe forms of this defect may develop severe respiratory distress and cyanosis shortly after birth. […] Newborns with a severe form of TAPVR have difficulty breathing and bluish coloration of the skin (cyanosis). […] In milder forms, symptoms of heart failure may be present but be more difficult to detect. Symptoms of heart failure include shortness of breath, a bluish color to the skin (cyanosis), and fatigue. The level of oxygen is usually lower than normal, but some infants may have no symptoms or cyanosis.

• #29 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #30 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #31 Partners in Care | Total Anomalous Pulmonary Venous Return treatment…

  https://partnersincare.health/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect in which the veins that bring oxygen-rich blood to the heart return to an abnormal location. […] Symptoms of TAVPR vary based on where the veins connect and whether there is obstruction to the blood flow through the veins at the abnormal connection. If the veins are obstructed, the child may become very sick very quickly and can require emergency surgery. If the veins are not obstructed, the child may not require surgical intervention for weeks to months after being born. […] Symptoms of TAPVR may include: Difficulty breathing, Face or chest appear blue in color, Fast breathing, Poor feeding, Poor growth. […] Treatment of a TAPVR requires open-heart surgery. If the pulmonary venous pathway is obstructed, surgery may need to be performed as an emergency surgery shortly after birth. If the pathway is not obstructed, surgery may be able to be performed electively later during infancy.

• #32 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #33 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #34 Total anomalous pulmonary venous return (TAPVR) – Children’s Health Cardiology

  https://www.childrens.com/specialties-services/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) makes it hard for the heart to pump oxygen-rich blood to the rest of the body. […] TAPVR develops during the first four to six weeks of pregnancy because the child’s heart doesnt develop normally. In TAPVR, a child’s blood vessels (pulmonary veins) connect to the wrong side of the heart. When this happens, the oxygen in the lungs can’t be brought to the rest of the body efficiently. […] In some cases, signs of TAPVR show up during prenatal tests, such as a fetal ultrasound. Children can develop symptoms within the first weeks, months or year of their life. […] These symptoms include: Skin that appears ashen or blue from poor circulation (also called cyanosis), Rapid breathing or shortness of breath, Heart murmur, Weak pulse, Difficulty feeding, Rapid heartbeat.

• #35 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #36 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #37 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #38 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #39 Total Anomalous Pulmonary Venous Returns | TAPVR | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital (present at birth) heart defect. […] Babies with total anomalous pulmonary venous return are not able to supply oxygen-rich (red) blood to the body after birth. […] Without an additional heart defect that allows mixing of oxygen-poor (blue) and oxygen-rich (red) blood, infants with TAPVR will have a mixture of oxygen-rich (red) and oxygen-poor (blue) blood circulating through the right heart and back to the lungs – a situation that is fatal. […] The obvious indication of total anomalous pulmonary venous return is a newborn who becomes cyanotic (blue coloring of the skin, lips, and nailbeds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. […] The following are the other most common total anomalous pulmonary venous return symptoms. However, each child may experience symptoms differently. TAPVR symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding.

• #40 Total anomalous pulmonary venous return (TAPVR) – Children’s Health Cardiology

  https://www.childrens.com/specialties-services/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) makes it hard for the heart to pump oxygen-rich blood to the rest of the body. […] TAPVR develops during the first four to six weeks of pregnancy because the child’s heart doesnt develop normally. In TAPVR, a child’s blood vessels (pulmonary veins) connect to the wrong side of the heart. When this happens, the oxygen in the lungs can’t be brought to the rest of the body efficiently. […] In some cases, signs of TAPVR show up during prenatal tests, such as a fetal ultrasound. Children can develop symptoms within the first weeks, months or year of their life. […] These symptoms include: Skin that appears ashen or blue from poor circulation (also called cyanosis), Rapid breathing or shortness of breath, Heart murmur, Weak pulse, Difficulty feeding, Rapid heartbeat.

• #41 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #42 Total anomalous pulmonary venous return (TAPVR) – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/total-anomalous-pulmonary-venous-return/cdc-20385613

  In total anomalous pulmonary venous return (TAPVR), the pulmonary veins incorrectly send blood to the heart’s upper right chamber. That chamber is called the right atrium. As a result, oxygen-rich blood mixes with oxygen-poor blood, as shown in purple. In a typical heart, shown on the left, oxygen-rich blood flows from the pulmonary veins to the upper left chamber, also called the left atrium. […] Total anomalous pulmonary venous return (TAPVR) is a rare heart condition that’s present at birth. That means it’s a congenital heart defect. […] Symptoms of total anomalous pulmonary venous return (TAPVR) in babies may include trouble breathing, poor feeding and a weak pulse. The baby’s skin may look gray or blue due to low oxygen levels. This is called cyanosis. Depending on skin color, these changes may be easier or harder to see. […] Symptoms of TAPVR may appear soon after birth. But some people don’t have symptoms until later in life.

• #43 Total Anomalous Pulmonary Venous Return (TAPVR) | Cedars-Sinai

  https://www.cedars-sinai.org/health-library/diseases-and-conditions—pediatrics/t/total-anomalous-pulmonary-venous-return.html

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur.

• #44 Content – Health Encyclopedia – University of Rochester Medical Center

  https://www.urmc.rochester.edu/encyclopedia/content?contenttypeid=90&contentid=P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Your baby may need to go into the intensive care unit (ICU) for treatment. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will still need to see a heart doctor for regular checkups for the rest of their life.

• #45 Pediatric Total Anomalous Pulmonary Venous Return (TAPVR) – Conditions and Treatments | Children’s National Hospital

  https://www.childrensnational.org/get-care/health-library/total-anomalous-pulmonary-venous-return-tapvr

  The obvious indication of TAPVR is a newborn who becomes cyanotic (blue coloring of the skin, lips and nail beds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. The degree of cyanosis is related to the degree of obstruction of the anomalous pulmonary veins and the size of the foramen ovale that allows the red and blue blood to mix. […] The following are the other most common symptoms of total anomalous pulmonary venous. However, each child may experience symptoms differently. Symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding. […] Another problem that occurs with TAPVR is that too much blood flows through the blood vessels in the lungs, since the pulmonary veins add extra blood back in to the circulation on the right side of the heart. The lungs become stressed by this extra blood flow and can eventually become damaged from it. […] Many infants who have had TAPVR surgical repair will grow and develop normally. However, after TAPVR repair, your infant will need to be followed periodically by a pediatric cardiologist who will make assessments to check for any heart-related problems.

• #46 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #47 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #48 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #49 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #50 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #51 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #52 Partners in Care | Total Anomalous Pulmonary Venous Return treatment…

  https://partnersincare.health/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect in which the veins that bring oxygen-rich blood to the heart return to an abnormal location. […] Symptoms of TAVPR vary based on where the veins connect and whether there is obstruction to the blood flow through the veins at the abnormal connection. If the veins are obstructed, the child may become very sick very quickly and can require emergency surgery. If the veins are not obstructed, the child may not require surgical intervention for weeks to months after being born. […] Symptoms of TAPVR may include: Difficulty breathing, Face or chest appear blue in color, Fast breathing, Poor feeding, Poor growth. […] Treatment of a TAPVR requires open-heart surgery. If the pulmonary venous pathway is obstructed, surgery may need to be performed as an emergency surgery shortly after birth. If the pathway is not obstructed, surgery may be able to be performed electively later during infancy.

• #53 Total Anomalous Pulmonary Venous Returns | TAPVR | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital (present at birth) heart defect. […] Babies with total anomalous pulmonary venous return are not able to supply oxygen-rich (red) blood to the body after birth. […] Without an additional heart defect that allows mixing of oxygen-poor (blue) and oxygen-rich (red) blood, infants with TAPVR will have a mixture of oxygen-rich (red) and oxygen-poor (blue) blood circulating through the right heart and back to the lungs – a situation that is fatal. […] The obvious indication of total anomalous pulmonary venous return is a newborn who becomes cyanotic (blue coloring of the skin, lips, and nailbeds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. […] The following are the other most common total anomalous pulmonary venous return symptoms. However, each child may experience symptoms differently. TAPVR symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding.

• #54 Understanding Total Anomalous Pulmonary Venous Return

  https://lagans.org.uk/total-anomalous-pulmonary-venus-return/

  Total Anomalous Pulmonary Venous Return is a rare heart defect that is present at birth and it occurs when pulmonary veins connect to the heart in an abnormal way. […] Children born with this condition will need surgery to repair the defect, as well routine checkups to stay as healthy as possible as they grow. […] Symptoms of Total Anomalous Pulmonary Venous Return will usually occur immediately after birth or soon after. Infants with TAPVR will often have bluish looking skin, called cyanosis, because their blood doesnt carry enough oxygen. […] Other signs and symptoms can include: Difficulty breathing and making grunting sounds, Retractions of the rib cage muscles, Weak pulse, Lack of growth or weight gain, Problems feeding, Extreme tiredness, Heart murmurs. […] All types of Total Anomalous Pulmonary Venous Return will need to be treated with surgery, but the timing of the surgery will depend on the type of TAPVR present.

• #55 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #56 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #57 Understanding Total Anomalous Pulmonary Venous Return

  https://lagans.org.uk/total-anomalous-pulmonary-venus-return/

  Total Anomalous Pulmonary Venous Return is a rare heart defect that is present at birth and it occurs when pulmonary veins connect to the heart in an abnormal way. […] Children born with this condition will need surgery to repair the defect, as well routine checkups to stay as healthy as possible as they grow. […] Symptoms of Total Anomalous Pulmonary Venous Return will usually occur immediately after birth or soon after. Infants with TAPVR will often have bluish looking skin, called cyanosis, because their blood doesnt carry enough oxygen. […] Other signs and symptoms can include: Difficulty breathing and making grunting sounds, Retractions of the rib cage muscles, Weak pulse, Lack of growth or weight gain, Problems feeding, Extreme tiredness, Heart murmurs. […] All types of Total Anomalous Pulmonary Venous Return will need to be treated with surgery, but the timing of the surgery will depend on the type of TAPVR present.

• #58 Total Anomalous Pulmonary Venous Return

  https://www.rwjbh.org/treatment-care/heart-and-vascular-care/diseases-conditions/congenital-heart-disease/total-anomalous-pulmonary-venous-return/

  Some people born with this condition have no signs or symptoms. However, as the condition worsens symptoms start to appear. Some of these symptoms may include: […] A bluish discoloration of the lips and skin caused by low oxygen (cyanosis). […] Rapid breathing or working harder while breathing, especially while eating. […] Unusual fatigue or lethargy. […] If not immediately addressed, life-threatening consequences can occur.

• #59 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #60 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is an issue where veins from your babys lungs connect to the right side of their heart instead of the left. Blood with and without oxygen mixes, which keeps their body from getting enough oxygen. This is a rare, life-threatening congenital heart issue that affects newborns. […] Some of the time, babies with total anomalous pulmonary venous return have trouble breathing soon after birth. Their skin may appear blue (or gray on darker skin). […] Symptoms of TAPVR usually appear very soon after birth. Babies have symptoms at birth if they have any narrowing where their lung veins connect to their hearts. But some babies dont have symptoms for several weeks. […] Symptoms may include: Cyanosis (bluish or grayish skin, nails and lips). Difficulty feeding. Fatigue and lethargy (lack of energy). Heart murmur. Shortness of breath (dyspnea) and trouble breathing. Lack of growth or weight gain.

• #61 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #62 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #63 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Total anomalous pulmonary venous return (TAPVR) occurs when the pulmonary veins bringing blood back from the lungs do not connect to the left atrium. Instead, they go to the heart by way of an abnormal (anomalous) connection. […] In a baby with TAPVR, oxygen-rich blood from the lungs returns to the right side of the heart. Here, oxygen-rich blood mixes with oxygen-poor blood. This causes the baby to get less oxygen than is needed to the body. […] Symptoms of TAPVR usually occur at birth or very soon afterwards. Infants with TAPVR can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. Infants with TAPVR or other conditions causing cyanosis can have symptoms such as: Problems breathing, Weak pulse, Ashen or bluish skin color, Poor feeding, Extreme sleepiness.

• #64 Total anomalous pulmonary venous return (TAPVR) – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/total-anomalous-pulmonary-venous-return/cdc-20385613

  In total anomalous pulmonary venous return (TAPVR), the pulmonary veins incorrectly send blood to the heart’s upper right chamber. That chamber is called the right atrium. As a result, oxygen-rich blood mixes with oxygen-poor blood, as shown in purple. In a typical heart, shown on the left, oxygen-rich blood flows from the pulmonary veins to the upper left chamber, also called the left atrium. […] Total anomalous pulmonary venous return (TAPVR) is a rare heart condition that’s present at birth. That means it’s a congenital heart defect. […] Symptoms of total anomalous pulmonary venous return (TAPVR) in babies may include trouble breathing, poor feeding and a weak pulse. The baby’s skin may look gray or blue due to low oxygen levels. This is called cyanosis. Depending on skin color, these changes may be easier or harder to see. […] Symptoms of TAPVR may appear soon after birth. But some people don’t have symptoms until later in life.

• #65 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #66 Partners in Care | Total Anomalous Pulmonary Venous Return treatment…

  https://partnersincare.health/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect in which the veins that bring oxygen-rich blood to the heart return to an abnormal location. […] Symptoms of TAVPR vary based on where the veins connect and whether there is obstruction to the blood flow through the veins at the abnormal connection. If the veins are obstructed, the child may become very sick very quickly and can require emergency surgery. If the veins are not obstructed, the child may not require surgical intervention for weeks to months after being born. […] Symptoms of TAPVR may include: Difficulty breathing, Face or chest appear blue in color, Fast breathing, Poor feeding, Poor growth. […] Treatment of a TAPVR requires open-heart surgery. If the pulmonary venous pathway is obstructed, surgery may need to be performed as an emergency surgery shortly after birth. If the pathway is not obstructed, surgery may be able to be performed electively later during infancy.

• #67 Total Anomalous Pulmonary Venous Return (TAPVR) | Cedars-Sinai

  https://www.cedars-sinai.org/health-library/diseases-and-conditions—pediatrics/t/total-anomalous-pulmonary-venous-return.html

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur.

• #68 Total Anomalous Pulmonary Venous Returns | TAPVR | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a congenital (present at birth) heart defect. […] Babies with total anomalous pulmonary venous return are not able to supply oxygen-rich (red) blood to the body after birth. […] Without an additional heart defect that allows mixing of oxygen-poor (blue) and oxygen-rich (red) blood, infants with TAPVR will have a mixture of oxygen-rich (red) and oxygen-poor (blue) blood circulating through the right heart and back to the lungs – a situation that is fatal. […] The obvious indication of total anomalous pulmonary venous return is a newborn who becomes cyanotic (blue coloring of the skin, lips, and nailbeds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. […] The following are the other most common total anomalous pulmonary venous return symptoms. However, each child may experience symptoms differently. TAPVR symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding.

• #69 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #70 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #71 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #72 Total anomalous pulmonary venous return Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #73 Pediatric Total Anomalous Pulmonary Venous Return (TAPVR) – Conditions and Treatments | Children’s National Hospital

  https://www.childrensnational.org/get-care/health-library/total-anomalous-pulmonary-venous-return-tapvr

  The obvious indication of TAPVR is a newborn who becomes cyanotic (blue coloring of the skin, lips and nail beds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. The degree of cyanosis is related to the degree of obstruction of the anomalous pulmonary veins and the size of the foramen ovale that allows the red and blue blood to mix. […] The following are the other most common symptoms of total anomalous pulmonary venous. However, each child may experience symptoms differently. Symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding. […] Another problem that occurs with TAPVR is that too much blood flows through the blood vessels in the lungs, since the pulmonary veins add extra blood back in to the circulation on the right side of the heart. The lungs become stressed by this extra blood flow and can eventually become damaged from it. […] Many infants who have had TAPVR surgical repair will grow and develop normally. However, after TAPVR repair, your infant will need to be followed periodically by a pediatric cardiologist who will make assessments to check for any heart-related problems.

• #74 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  A baby with TAPVR can have heart failure and pulmonary hypertension. Even after the initial repair, TAPVR can sometimes lead to abnormal heart rhythms or blockages in your childs pulmonary veins. […] Nearly every baby with total anomalous pulmonary venous return needs surgery to survive. Healthcare providers treat TAPVR with open-heart surgery. Most often, providers perform this surgery as soon as they can after diagnosing the condition. […] Without surgery, some forms of total anomalous pulmonary venous return are typically fatal a few weeks after birth. With early diagnosis and surgical treatment, the outlook for babies with TAPVR is very good. The survival rate after surgery is around 97%. […] Your child will need regular visits with their cardiologist as they grow into adulthood. Lifelong follow-up visits can help cardiologists find problems like an irregular heartbeat or blockages (obstructions) in their blood vessels. An obstruction requires another surgery and may be hard to treat.

• #75 Total Anomalous Pulmonary Venous Return (TAPVR) | University Hospitals

  https://www.uhhospitals.org/rainbow/services/congenital-heart/conditions-and-treatments/article/Diseases-and-Conditions—Pediatrics/total-anomalous-pulmonary-venous-return

  All children with a TAPVR will need to have surgery to fix it. Your baby will need to go into the intensive care unit (ICU) for treatment. […] The complications of TAPVR include: Enlarged heart, Lung problems, including respiratory failure and high blood pressure in the lungs, Abnormal heart rhythms, Shock, Heart failure, Slowed growth and development, Enlarged liver, Need for another surgery, Infection, Death. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will still need to see a heart doctor for regular checkups for the rest of their life.

• #76 Total Anomalous Pulmonary Venous Return (TAPVR) | University Hospitals

  https://www.uhhospitals.org/rainbow/services/congenital-heart/conditions-and-treatments/article/Diseases-and-Conditions—Pediatrics/total-anomalous-pulmonary-venous-return

  All children with a TAPVR will need to have surgery to fix it. Your baby will need to go into the intensive care unit (ICU) for treatment. […] The complications of TAPVR include: Enlarged heart, Lung problems, including respiratory failure and high blood pressure in the lungs, Abnormal heart rhythms, Shock, Heart failure, Slowed growth and development, Enlarged liver, Need for another surgery, Infection, Death. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will still need to see a heart doctor for regular checkups for the rest of their life.

• #77 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://www.isuog.org/clinical-resources/patient-information-series/patient-information-pregnancy-conditions/heart/total-anomalous-pulmonary-venous-return-tapvr.html

  TAPVR accounts for 1% of all children with congenital heart defects. […] In TAPVR, oxygen-rich blood mistakenly enters other structures, usually the right atrium where it mixes with less oxygen-rich blood coming from the rest of the body. […] Children with narrowing (stenosis) of the pulmonary veins in addition, usually have more severe symptoms and can have a duskiness to their skin colour called cyanosis. When this is present, earlier surgical correction is required. […] After birth, your baby will be watched carefully for any signs of severe disease. An echocardiogram will be performed to verify the diagnosis and establish the type of TAPVR and rule out other structural changes in the heart such as the presence and degree of obstruction in the venous system. […] The baby will be watched for complications such as pneumonia and acute heart failure. Surgical intervention is required to correct this condition, the timing of which will be decided by the pediatric cardiologist and cardiovascular surgeon, after newborn examination and investigations are completed. TAPVR is a serious heart anomaly. Without corrective surgery, many babies will die in the first year of life.

• #78 Partial and Total Anomalous Pulmonary Venous Connection – StatPearls – NCBI Bookshelf

  https://www.ncbi.nlm.nih.gov/books/NBK560707/

  Patients with obstructed TAPVC usually present with severe respiratory distress and cyanosis in the newborn period. […] In untreated patients, TAPVC is almost always fatal within the first few weeks of life. The long term survival in patients has increased with the improvement in medical management and surgical techniques.

• #79 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #80 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #81 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #82 Total anomalous pulmonary venous return: MedlinePlus Medical EncyclopediaLock

  https://medlineplus.gov/ency/article/001115.htm

  Total anomalous pulmonary venous return (TAPVR) is a heart disease in which the 4 veins that take blood from the lungs to the heart do not attach normally to the left atrium (left upper chamber of the heart). Instead, they attach to another blood vessel or the wrong part of the heart. It is present at birth (congenital heart disease). […] The infant may appear very sick and may have the following symptoms: Bluish color to the skin (cyanosis) due to low oxygen level in the blood, Frequent respiratory infections, Lethargy, Poor feeding, Poor growth, Rapid breathing. […] Note: Sometimes, no symptoms may be present in infancy or early childhood. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival.

• #83 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #84 Total Anomalous Pulmonary Venous Return Symptoms, Doctors, Treatments, Advances & More | MediFind

  https://www.medifind.com/conditions/total-anomalous-pulmonary-venous-return/4755

  This condition may be apparent at the time of birth. However, symptoms may not be present until later. Contact your health care provider if you notice symptoms of TAPVR. Prompt attention is required. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery.

• #85 Pediatric Total Anomalous Pulmonary Venous Return (TAPVR) – Conditions and Treatments | Children’s National Hospital

  https://www.childrensnational.org/get-care/health-library/total-anomalous-pulmonary-venous-return-tapvr

  The obvious indication of TAPVR is a newborn who becomes cyanotic (blue coloring of the skin, lips and nail beds) in the first days of life after the maternal source of oxygen (from the placenta) is removed. The degree of cyanosis is related to the degree of obstruction of the anomalous pulmonary veins and the size of the foramen ovale that allows the red and blue blood to mix. […] The following are the other most common symptoms of total anomalous pulmonary venous. However, each child may experience symptoms differently. Symptoms may include: Rapid breathing, Labored breathing, Rapid heart rate, Cool, clammy skin, Lethargy, Poor feeding. […] Another problem that occurs with TAPVR is that too much blood flows through the blood vessels in the lungs, since the pulmonary veins add extra blood back in to the circulation on the right side of the heart. The lungs become stressed by this extra blood flow and can eventually become damaged from it. […] Many infants who have had TAPVR surgical repair will grow and develop normally. However, after TAPVR repair, your infant will need to be followed periodically by a pediatric cardiologist who will make assessments to check for any heart-related problems.

• #86 Total Anomalous Pulmonary Venous Return (TAPVR) | Nationwide Children’s

  https://www.nationwidechildrens.org/conditions/total-anomalous-pulmonary-venous-return

  Total anomalous pulmonary venous return is a heart problem where veins connect to the wrong place. It needs surgery to fix. […] Total anomalous pulmonary venous return (TAPVR) is a condition where the blood vessels in the lungs, called the pulmonary veins, are not attached to the heart in the right place. These veins carry blood with oxygen to the heart, then out to the body. Normally, these veins are connected to the upper left chamber of the heart, called the atrium. In TAPVR, theyre connected to a different vein. Because of this, the body cant get enough oxygen. […] Babies with TAPVR usually have a hole between the right and left atriums. This is called an atrial septal defect (ASD). This lets blood with some oxygen get to the left side of the heart. This blood is then pumped out to the rest of the body.

• #87 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #88 Content – Health Encyclopedia – University of Rochester Medical Center

  https://www.urmc.rochester.edu/encyclopedia/content?contenttypeid=90&contentid=P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Your baby may need to go into the intensive care unit (ICU) for treatment. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will still need to see a heart doctor for regular checkups for the rest of their life.

• #89 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #90 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #91 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #92 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #93 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #94 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #95 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #96 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #97 Total Anomalous Pulmonary Venous Return (TAPVR) – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/total-anomalous-pulmonary-venous-return-tapvr

  In total anomalous pulmonary venous return, the pulmonary veins drain to a confluence adjacent to the posterior wall of the left atrium but do not connect to the left atrium. […] Patients may be only mildly symptomatic or have significant heart failure symptoms. Severe obstruction of the pulmonary venous return may occur, resulting in severe neonatal cyanosis, pulmonary edema, and pulmonary hypertension. […] The infradiaphragmatic drainage type is invariably severely obstructed, leading to dramatic pulmonary edema and cyanosis unresponsive to supplemental oxygen that manifest shortly after birth. The other 2 types do not typically involve obstruction and lead to mild to moderate signs of heart failure and mild cyanosis in the first month of life. […] Neonates with obstructed pulmonary venous return present with respiratory distress, pulmonary edema, and marked cyanosis. […] If pulmonary venous return is not obstructed, mild symptoms of heart failure may be present. Some infants with unobstructed supracardiac or cardiac total anomalous pulmonary venous return may be asymptomatic.

• #98 Total Anomalous Pulmonary Venous Return | Thoracic Key

  https://thoracickey.com/total-anomalous-pulmonary-venous-return/

  Total anomalous pulmonary venous return (TAPVR) is a rare lesion with the pulmonary veins commonly connecting to a venous confluence that ultimately drains to the desaturated atrial chamber. […] Patients will most often present with a large left-to-right shunt resulting in pulmonary overcirculation and heart failure. Less frequently, the pulmonary venous connection is obstructed, leading to cardiopulmonary collapse shortly following birth. […] In a comprehensive, population-based study from several European countries the most common signs and symptoms at the time of presentation in children with TAPVR were cyanosis (43%), respiratory distress (31%), failure to thrive (11%), circulatory collapse (4.5%), a murmur (0.5%), or supraventricular tachycardia (0.5%). […] For children with pulmonary venous obstruction (PVO), rapid progression to metabolic acidosis, cardiac failure, and death may occur shortly following birth.

• #99 Anomalous pulmonary venous connection – Wikipedia

  https://en.wikipedia.org/wiki/Anomalous_pulmonary_venous_connection

  TAPVC with obstruction will clinically present with cyanosis, tachypnea, dyspnea, and hypoxemia. Chest x-ray may show a ground-glass appearance due to pulmonary edema resulting from increased pressure in the obstructed pulmonary veins. […] Cases of TAPVC with obstruction are considered a surgical emergency. […] In TAPVC without obstruction, surgical redirection can be performed within the first month of life. The operation is performed under general anesthesia. The four pulmonary veins are reconnected to the left atrium, and any associated heart defects such as atrial septal defect, ventricular septal defect, patent foramen ovale, and/or patent ductus arteriosus are surgically closed. With obstruction, surgery should be undertaken urgently.

• #100 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #101 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #102 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #103 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #104 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #105 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #106 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Earlier detection and correction of TAPVR improves patient outcome. However, it is difficult to make a differential diagnosis between TAPVR and other neonatal respiratory diseases, such as respiratory distress syndrome, in newborns because initial symptoms or signs may be non-specific and cardiac murmur can be inaudible in TAPVR. Therefore, a high degree of suspicion is essential for an early diagnosis of TAPVR. In the cases presented herein, TAPVR was recognized in the younger brother at 1 month of age. Upon his hospital admission, his symptoms of congestive heart failure and pulmonary hypertension had already progressed. As in this case, early manifestations in TAPVR were nonspecific; thus, diagnosis of this critical congenital heart disease can be delayed. Echocardiography is the diagnostic mode of choice; thus, if the younger brother had received routine echocardiography, TAPVR could have been diagnosed and operated on earlier.

• #107 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Earlier detection and correction of TAPVR improves patient outcome. However, it is difficult to make a differential diagnosis between TAPVR and other neonatal respiratory diseases, such as respiratory distress syndrome, in newborns because initial symptoms or signs may be non-specific and cardiac murmur can be inaudible in TAPVR. Therefore, a high degree of suspicion is essential for an early diagnosis of TAPVR. In the cases presented herein, TAPVR was recognized in the younger brother at 1 month of age. Upon his hospital admission, his symptoms of congestive heart failure and pulmonary hypertension had already progressed. As in this case, early manifestations in TAPVR were nonspecific; thus, diagnosis of this critical congenital heart disease can be delayed. […] Screening of all siblings with TAPVR is a burden to patients due to psychological stress or financial problems on the parents; thus, not all siblings will present for screening. However, these consequences are outweighed by the benefit of diagnosing this critical disease so the patient can be taken for surgery before severe congestive heart failure develops.

• #108 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #109 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Total anomalous pulmonary venous return (TAPVR) is a rare and critical congenital vascular anomaly that requires an early operation. However, initial symptoms of TAPVR may be non-specific, and cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, a high degree of suspicion and an early diagnosis of TAPVR are important. […] However, initial symptoms of TAPVR may be non-specific and include dyspnea, poor oral feeding, and cardiorespiratory failure. Moreover, the cardiovascular findings may be minimal. The heart may not be enlarged and there is often no cardiac murmur. Without cardiac murmur, these symptoms are similar to those of respiratory distress syndrome in newborns. Therefore, misdiagnosis and a delayed operation can increase mortality and morbidity in infants with TAPVR.

• #110 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #111 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  A baby with TAPVR can have heart failure and pulmonary hypertension. Even after the initial repair, TAPVR can sometimes lead to abnormal heart rhythms or blockages in your childs pulmonary veins. […] Nearly every baby with total anomalous pulmonary venous return needs surgery to survive. Healthcare providers treat TAPVR with open-heart surgery. Most often, providers perform this surgery as soon as they can after diagnosing the condition. […] Without surgery, some forms of total anomalous pulmonary venous return are typically fatal a few weeks after birth. With early diagnosis and surgical treatment, the outlook for babies with TAPVR is very good. The survival rate after surgery is around 97%. […] Your child will need regular visits with their cardiologist as they grow into adulthood. Lifelong follow-up visits can help cardiologists find problems like an irregular heartbeat or blockages (obstructions) in their blood vessels. An obstruction requires another surgery and may be hard to treat.

• #112 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #113 Total Anomalous Pulmonary Venous Return (TAPVR) | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/total-anomalous-pulmonary-venous-return

  Most babies born with total anomalous pulmonary venous return (TAPVR) are very ill soon after birth. Symptoms may include: A bluish tint to the skin and lips […] Trouble breathing […] Rapid breathing […] Poor feeding or poor growth. If your child has any of these symptoms, your pediatrician may refer you to a pediatric cardiologist for testing. Children with TAPVR will need surgery in infancy to repair the problem. Newborns with severe TAPVR will need emergency surgery shortly after birth. They often need to be admitted to the cardiac intensive care unit (CICU) and require intensive support with medications and a ventilator (breathing machine). Some babies with severe TAPVR may need a specialized life support system called ECMO (extracorporeal membrane oxygenation), an advanced technology that functions as a replacement for a critically ill child’s heart and lungs. Babies with less severe TAPVR usually have surgery in the days or weeks after they’re diagnosed. Thanks to updates in surgical techniques for repairing TAPVR, the long-term outlook is continually improving. Children who have had a repair for TAPVR will require lifelong checkups with a cardiologist to make sure their veins remain open. If the veins become narrowed, they may need catheterizations or surgeries to repair these veins.

• #114 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #115 Understanding Total Anomalous Pulmonary Venous Return

  https://lagans.org.uk/total-anomalous-pulmonary-venus-return/

  Newborns who have an obstructed TAPVR will need surgery immediately after birth. […] Infants with an unobstructed TAPVR will typically have surgery days to weeks after the diagnosis is made. […] There are a few possible complications of Total Anomalous Pulmonary Venous Return if the condition is left untreated or not managed appropriately: Enlarged heart, Lung problems, Abnormal heart rhythms, known as arrhythmia, Heart failure, Slowed growth and development, Enlarged liver, Infection, Death. […] The outcome for surgical repair of Total Anomalous Pulmonary Venous Return is extremely positive, with many infants growing and developing as normal after all surgery and aftercare is completed. […] Although not impossible, it is also rare for children to develop complications related to TAPVR late after surgery. However, regular follow-up appointments with your childs cardiologist are essential for spotting these problems early on.

• #116 Total Anomalous Pulmonary Venous Return (TAPVR) – Cardiothoracic Surgery

  https://lsom.uthscsa.edu/ct-surgery/patient-care/congenital-heart/conditions-we-treat/total-anomalous-pulmonary-venous-return-tapvr/

  In TAPVR the entire pulmonary venous circulation drains to the RA, either directly or by a systemic vein or sinus connecting with the RA via the SVC, IVC, or coronary sinus. An ASD is necessary to deliver oxygenated blood to the left heart. TAPVR is classified as supracardiac, cardiac, or infracardiac. In cases without obstruction there is a large left-to-right shunt and patients present with heart failure months after birth up to early childhood. There may be a gallop or faint systolic murmur secondary to increased flow across the tricuspid valve, and a prominent fixed S2. Patients with non obstructed TAPVR are repaired electively when diagnosed, usually when symptoms develop around 6 months of age. When there is pulmonary venous obstruction, infants present in extremis within hours to days of birth; they are profoundly cyanotic and in severe congestive heart failure. Diagnosis and mapping of the anomalous connections is possible by echocardiography. Obstructed TAPVR is a surgical emergency. […] 5-15% of patients develop recurrent pulmonary venous obstruction within the first year post-op.

• #117 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #118 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  A baby with TAPVR can have heart failure and pulmonary hypertension. Even after the initial repair, TAPVR can sometimes lead to abnormal heart rhythms or blockages in your childs pulmonary veins. […] Nearly every baby with total anomalous pulmonary venous return needs surgery to survive. Healthcare providers treat TAPVR with open-heart surgery. Most often, providers perform this surgery as soon as they can after diagnosing the condition. […] Without surgery, some forms of total anomalous pulmonary venous return are typically fatal a few weeks after birth. With early diagnosis and surgical treatment, the outlook for babies with TAPVR is very good. The survival rate after surgery is around 97%. […] Your child will need regular visits with their cardiologist as they grow into adulthood. Lifelong follow-up visits can help cardiologists find problems like an irregular heartbeat or blockages (obstructions) in their blood vessels. An obstruction requires another surgery and may be hard to treat.

• #119 Total Anomalous Pulmonary Venous Return (TAPVR) – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=total-anomalous-pulmonary-venous-return-tapvr-90-P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to his or her body. Other symptoms can include fast or troubled breathing, fast heart rate, cool, clammy skin, tiredness and little movement, poor feeding, poor pulses, enlarged liver, and heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Your child will need to see a heart doctor for regular checkups for the rest of their life. Many children with TAPVR will grow and develop normally after they have surgery.

• #120 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  A baby with TAPVR can have heart failure and pulmonary hypertension. Even after the initial repair, TAPVR can sometimes lead to abnormal heart rhythms or blockages in your childs pulmonary veins. […] Nearly every baby with total anomalous pulmonary venous return needs surgery to survive. Healthcare providers treat TAPVR with open-heart surgery. Most often, providers perform this surgery as soon as they can after diagnosing the condition. […] Without surgery, some forms of total anomalous pulmonary venous return are typically fatal a few weeks after birth. With early diagnosis and surgical treatment, the outlook for babies with TAPVR is very good. The survival rate after surgery is around 97%. […] Your child will need regular visits with their cardiologist as they grow into adulthood. Lifelong follow-up visits can help cardiologists find problems like an irregular heartbeat or blockages (obstructions) in their blood vessels. An obstruction requires another surgery and may be hard to treat.

• #121 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #122 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #123 About Total Anomalous Pulmonary Venous Return | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tapvr.html

  Babies with TAPVR will need surgery to repair the defect. The age at which the surgery is done depends on: How sick the child is, The specific structure of the abnormal connections. […] Surgical repairs for TAPVR are not a cure. People living with TAPVR may have lifelong complications. Routine checkups with a heart doctor are needed to monitor progress, avoid complications, check for other health conditions that might develop over time.

• #124 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://healthlibrary.reading.towerhealth.org/HomeHealthyHolidays/90,P01820

  All children with a TAPVR will need to have surgery to fix it. Your baby may need to go into the intensive care unit (ICU) for treatment. […] Many children with TAPVR will grow and develop normally after they have surgery. Your child will need to see a heart doctor for regular checkups for the rest of their life.

• #125 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://my.clevelandclinic.org/health/diseases/23069-total-anomalous-pulmonary-venous-return

  A baby with TAPVR can have heart failure and pulmonary hypertension. Even after the initial repair, TAPVR can sometimes lead to abnormal heart rhythms or blockages in your childs pulmonary veins. […] Nearly every baby with total anomalous pulmonary venous return needs surgery to survive. Healthcare providers treat TAPVR with open-heart surgery. Most often, providers perform this surgery as soon as they can after diagnosing the condition. […] Without surgery, some forms of total anomalous pulmonary venous return are typically fatal a few weeks after birth. With early diagnosis and surgical treatment, the outlook for babies with TAPVR is very good. The survival rate after surgery is around 97%. […] Your child will need regular visits with their cardiologist as they grow into adulthood. Lifelong follow-up visits can help cardiologists find problems like an irregular heartbeat or blockages (obstructions) in their blood vessels. An obstruction requires another surgery and may be hard to treat.

• #126 Total Anomalous Pulmonary Venous Return (TAPVR) | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/total-anomalous-pulmonary-venous-return-tapvr

  Total anomalous pulmonary venous return symptoms include: […] The severity of symptoms is determined by the presence of obstruction (or narrowing) of the pulmonary veins. […] In some cases, newborns with TAPVR have difficulty breathing and quickly become very ill. This occurs when the pulmonary veins are too narrow or are obstructed at some point, and blood cant flow from the lungs as quickly as it should. This is called TAPVR with pulmonary obstruction. […] In other cases, TAPVR is diagnosed in the first few months of life, after a child demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to skin). […] Children who were critically ill as newborns may have a longer road to recovery. In most cases, however, children wont experience long-term effects. They also wont have to remain on any medicines or limit sports. […] Rarely, the pulmonary veins become obstructed later in life and additional surgery or a catheterization procedure is required. A small number of children may also experience arrhythmia (abnormal heart rhythm), which may be treated with medicines, radiofrequency ablation or a pacemaker.

• #127 Total Anomalous Pulmonary Venous Return Symptoms, Doctors, Treatments, Advances & More | MediFind

  https://www.medifind.com/conditions/total-anomalous-pulmonary-venous-return/4755

  This condition may be apparent at the time of birth. However, symptoms may not be present until later. Contact your health care provider if you notice symptoms of TAPVR. Prompt attention is required. […] How severe this condition is depends on whether the pulmonary veins are blocked or obstructed as they drain. Obstructed TAPVR causes symptoms early in life and can be deadly very quickly if it is not found and corrected with surgery.

• #128 HIE Multimedia – Total anomalous pulmonary venous return

  https://adamcertificationdemo.adam.com/content.aspx?productid=117&isarticlelink=false&pid=1&gid=001115

  Note: Sometimes, no symptoms may be present in infancy or early childhood. […] If this condition is not treated, the heart will get larger, leading to heart failure. Repairing the defect early provides excellent results if there is no blockage of the pulmonary veins at the new connection into the heart. Infants who have obstructed veins have worsened survival. […] This condition may be apparent at the time of birth. However, symptoms may not be present until later. […] Contact your health care provider if you notice symptoms of TAPVR. Prompt attention is required.

• #129 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://healthlibrary.umcno.org/wellness/BloodPressure/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. Other symptoms can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Many children with TAPVR will grow and develop normally after they have surgery. Your child will need to see a heart doctor for regular checkups for the rest of their life. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] In TAPVR, the 4 blood vessels that carry oxygen-rich blood to the heart from the lungs aren’t connected correctly. This condition prevents oxygen-rich blood from being pumped to the body. Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body.

• #130 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://library.ouhealth.com/Wellness/Stress/Tools/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body. […] All children with TAPVR will need surgery. This is done to restore normal blood flow through the heart. […] Many children with TAPVR will grow and develop normally after they have surgery.

• #131 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://healthlibrary.umcno.org/wellness/BloodPressure/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. Other symptoms can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Many children with TAPVR will grow and develop normally after they have surgery. Your child will need to see a heart doctor for regular checkups for the rest of their life. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] In TAPVR, the 4 blood vessels that carry oxygen-rich blood to the heart from the lungs aren’t connected correctly. This condition prevents oxygen-rich blood from being pumped to the body. Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body.

• #132 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://library.ouhealth.com/Wellness/Stress/Tools/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body. […] All children with TAPVR will need surgery. This is done to restore normal blood flow through the heart. […] Many children with TAPVR will grow and develop normally after they have surgery.

• #133 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://healthlibrary.umcno.org/wellness/BloodPressure/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] The symptoms of TAPVR may seem like symptoms of other health conditions. Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. Other symptoms can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] All children with a TAPVR will need to have surgery to fix it. Many children with TAPVR will grow and develop normally after they have surgery. Your child will need to see a heart doctor for regular checkups for the rest of their life. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] In TAPVR, the 4 blood vessels that carry oxygen-rich blood to the heart from the lungs aren’t connected correctly. This condition prevents oxygen-rich blood from being pumped to the body. Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body.

• #134 Total Anomalous Pulmonary Venous Return (TAPVR)

  https://library.ouhealth.com/Wellness/Stress/Tools/90,P01820

  Total anomalous pulmonary venous return (TAPVR) is a congenital heart defect. This condition causes oxygen-rich blood from the lungs to mix with oxygen-poor (blue) blood from the body. Your child can’t live with TAPVR long-term. They need oxygen-rich blood all over the body. […] Newborns with TAPVR will have blue coloring of their skin, lips, and nailbeds (cyanosis). This happens in the first hours or days of their life. How severe your child’s condition is depends on how much blood is able to get to their body. […] Other symptoms can be a bit different for each child. They can include: Fast or troubled breathing, Fast heart rate, Cool, clammy skin, Tiredness and little movement, Poor feeding, Poor pulses, Enlarged liver, Heart murmur. […] Call your child’s healthcare provider if: Your child’s skin, lips, or fingernails become blue, Your child has trouble breathing or feeding. […] Your child can’t live with TAPVR long-term because people need oxygen-rich blood all over their body. […] All children with TAPVR will need surgery. This is done to restore normal blood flow through the heart. […] Many children with TAPVR will grow and develop normally after they have surgery.

• #135 Total Anomalous Pulmonary Venous Return (TAPVR) | Concise Medical Knowledge

  https://www.lecturio.com/concepts/total-anomalous-pulmonary-venous-return-tapvr/

  Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart defect wherein the pulmonary veins drain into anatomical sites other than the left atrium. Patients are usually cyanotic from birth and present with respiratory and heart failure right after birth. […] On examination there is a fixed, wide split-second heart sound, and a chest X-ray might reveal the snowman sign. […] The degree of obstruction of pulmonary veins determines the age of presentation: Obstructed: At birth, Cyanosis, Signs of shock, Difficult to arouse, Severe shortness of breath. […] Unobstructed: 30 + days of age, Subtle cyanosis, Poor feeding, Labored breathing. […] If untreated, neonate usually dies within 1st month of life. Surgical repair has very low mortality rate and excellent long-term outcome.

• #136 Total Anomalous Pulmonary Venous Return in Siblings

  https://pmc.ncbi.nlm.nih.gov/articles/PMC4286644/

  Earlier detection and correction of TAPVR improves patient outcome. However, it is difficult to make a differential diagnosis between TAPVR and other neonatal respiratory diseases, such as respiratory distress syndrome, in newborns because initial symptoms or signs may be non-specific and cardiac murmur can be inaudible in TAPVR. Therefore, a high degree of suspicion is essential for an early diagnosis of TAPVR. In the cases presented herein, TAPVR was recognized in the younger brother at 1 month of age. Upon his hospital admission, his symptoms of congestive heart failure and pulmonary hypertension had already progressed. As in this case, early manifestations in TAPVR were nonspecific; thus, diagnosis of this critical congenital heart disease can be delayed. Echocardiography is the diagnostic mode of choice; thus, if the younger brother had received routine echocardiography, TAPVR could have been diagnosed and operated on earlier.

• #137 :: JCVI :: Journal of Cardiovascular Imaging

  https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.213

  Earlier detection and correction of TAPVR improves patient outcome. However, it is difficult to make a differential diagnosis between TAPVR and other neonatal respiratory diseases, such as respiratory distress syndrome, in newborns because initial symptoms or signs may be non-specific and cardiac murmur can be inaudible in TAPVR. Therefore, a high degree of suspicion is essential for an early diagnosis of TAPVR. In the cases presented herein, TAPVR was recognized in the younger brother at 1 month of age. Upon his hospital admission, his symptoms of congestive heart failure and pulmonary hypertension had already progressed. As in this case, early manifestations in TAPVR were nonspecific; thus, diagnosis of this critical congenital heart disease can be delayed. […] Screening of all siblings with TAPVR is a burden to patients due to psychological stress or financial problems on the parents; thus, not all siblings will present for screening. However, these consequences are outweighed by the benefit of diagnosing this critical disease so the patient can be taken for surgery before severe congestive heart failure develops.

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