Materiały źródłowe

• #1 Med-Surg Nursing: Systemic Sclerosis (Scleroderma) – LevelUpRN

  https://leveluprn.com/blogs/medical-surgical-nursing/immune-system-6-systemic-sclerosis-scleroderma?srsltid=AfmBOoqe9fMaSE5pKw0W1DIW8Eqw51WDGWiuc3-QjIoQ5EV-ChhpgTVi

  Scleroderma is an autoimmune disorder marked by chronic inflammation of the body’s connective tissue, resulting in damage and occlusion to the blood vessels (vasculitis). Scleroderma also causes overproduction of collagen, which causes tissues to become inflamed, fibrotic and sclerotic (hard). […] There is no cure for scleroderma, so treatment is usually supportive. Immunosuppressants like prednisone or methotrexate can be given to a patient with scleroderma to calm the immune response and prevent escalation of symptoms. The patient can also be given ACE inhibitors like captopril. […] Patients with scleroderma should be encouraged to moisturize their skin as this can prevent it from drying out and becoming more hardened. They should take frequent rest periods. They should avoid stress and cold. To avoid cold, they should wear socks and really focus on keeping themselves warm, because if they get cold, the Raynaud’s syndrome side effect will worsen.

• #2 Scleroderma – Diagnosis and treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/scleroderma/diagnosis-treatment/drc-20351957

  Because scleroderma can take so many forms and affect so many different areas of the body, it can be difficult to diagnose. […] There is no treatment that can cure or stop the overproduction of collagen that happens in scleroderma. But a variety of treatments can help control symptoms and prevent complications. […] Because scleroderma can affect so many different parts of the body, the choice of medicine varies depending on the symptoms. […] Physical or occupational therapists can help you improve your strength and mobility and maintain independence with daily tasks. Hand therapy may help prevent hand stiffness, also called contractures. […] You can take a number of steps to help manage your symptoms of scleroderma: Stay active. Exercise keeps your body flexible, improves circulation and eases stiffness.

• #3 Scleroderma: Causes, Symptoms and Treatments | Arthritis Foundation

  https://www.arthritis.org/diseases/scleroderma

  Scleroderma causes hardening and tightening of the skin but may also affect other body parts. […] There is no cure for scleroderma, but treatment can help manage symptoms. […] Depending on which body parts are affected, several specialists may be involved in care, including a rheumatologist (a doctor who specializes in musculoskeletal diseases), a dermatologist (skin doctor), and those who treat specific organs. […] Physical therapists can help keep skin and joints flexible by teaching strengthening and range-of-motion exercises. […] Choose gentle cleansers with added moisturizers. […] Exercise regularly. Physical activity keeps skin and joints flexible, improves circulation and relieves joint stiffness. […] Manage emotional health. Changes in physical appearance coupled with managing a chronic illness can create stress and lead to depression.

• #4 Nursing Care Plan for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-scleroderma

  Nursing Care Plan (NCP) for Scleroderma […] By the end of this Nursing Care Plan Lesson for Scleroderma, students should be able to: Provide a deep understanding of the conditions pathophysiology, etiology, and a comprehensive approach to care that includes assessment, diagnosis, interventions, and evaluation. […] Scleroderma, or systemic sclerosis, is a chronic autoimmune disease characterized by fibrosis (thickening and hardening) of the skin and sometimes other organs. It involves overproduction of collagen, leading to skin tightening and thickening and potentially affecting internal organs like the heart, lungs, kidneys, and gastrointestinal tract. Scleroderma can be localized (affecting only the skin) or systemic. […] Desired Outcomes for Scleroderma: Patient demonstrates an understanding of the disease process and management strategies. […] Symptom management: Reduction in skin tightness, relief from pain, and improvement in mobility. […] Prevention or management of complications related to internal organ involvement. […] Maintaining optimal nutritional status and weight.

• #5 Scleroderma

  https://www.nhs.uk/conditions/scleroderma/

  The aim of treatment is to relieve symptoms, prevent the condition getting worse, detect and treat any complications (such as pulmonary hypertension) and help you maintain the use of affected parts of the body. […] Common treatments include: medication to improve circulation, medicines that reduce the activity of the immune system and slow the progression of the condition, steroids to relieve joint and muscle problems, moisturising affected areas of skin to help keep it supple and relieve itchiness, various medicines to control other symptoms (such as pain, heartburn and high blood pressure). […] You will also need regular blood pressure checks and other tests to check for any problems with your organs. […] If your symptoms are severe, surgery may be needed. For example, hard lumps under the skin may need to be removed, and tightened muscles may need to be loosened.

• #6 Nursing Care Plan For Systemic Sclerosis – Made For Medical

  https://www.madeformedical.com/nursing-care-plan-for-systemic-sclerosis/

  Systemic sclerosis, also known as scleroderma, is a rare and chronic autoimmune connective tissue disorder that affects multiple organs and systems in the body. […] As nurses, we play a crucial role in developing a comprehensive nursing care plan that focuses on addressing the physical, emotional, and psychosocial needs of individuals diagnosed with systemic sclerosis. […] Hence, it becomes imperative to tailor a holistic care plan that encompasses symptom management, patient education, psychosocial support, and close monitoring of disease progression. […] By adopting a patient-centered approach and working collaboratively with the interdisciplinary healthcare team, nurses can effectively manage symptoms, prevent complications, and enhance the overall quality of life for those living with systemic sclerosis.

• #7 Nursing Care Plan For Systemic Sclerosis – Made For Medical

  https://www.madeformedical.com/nursing-care-plan-for-systemic-sclerosis/

  By conducting a comprehensive nursing assessment for systemic sclerosis, healthcare providers can develop an individualized care plan that addresses the unique needs and challenges faced by each patient. […] Regular assessments and ongoing monitoring are essential to ensure timely intervention, promote symptom management, and improve the overall quality of life for individuals living with systemic sclerosis. […] These nursing diagnosis provide a foundation for developing individualized care plans for patients diagnosed with systemic sclerosis. […] The nursing interventions associated with each diagnosis aim to address the specific needs of the patient, alleviate symptoms, and enhance overall quality of life. […] By closely monitoring the patients condition and collaborating with the interdisciplinary healthcare team, nurses play a vital role in optimizing care and supporting individuals living with systemic sclerosis.

• #8 Nursing Care Plan for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-scleroderma

  Subjective Data for Scleroderma: Reports of skin changes, such as tightening or hardening. […] Pain or stiffness in the joints. […] Fatigue. […] Gastrointestinal symptoms like acid reflux or difficulty swallowing. […] Objective Data for Scleroderma: Physical examination showing skin thickening, shiny areas, and loss of skin folds. […] Evidence of Raynauds phenomenon (fingers or toes turning white or blue in response to cold or stress). […] Pulmonary function tests indicating lung involvement. […] Echocardiogram or renal function tests to assess heart and kidney involvement. […] Assessment for Scleroderma: Skin Assessment: Evaluate the extent and severity of skin changes. […] Joint and Muscle Assessment: Assess for pain, stiffness, and mobility limitations. […] Respiratory Assessment: Monitor for signs of pulmonary involvement, such as shortness of breath or persistent cough. […] Gastrointestinal Assessment: Assess for symptoms of gastroesophageal reflux disease (GERD) and other GI complications.

• #9 Nursing Care Plan for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-scleroderma

  Nursing Diagnosis for Scleroderma: Impaired Skin Integrity related to skin thickening and tightness. […] Chronic Pain related to joint and muscle involvement. […] Impaired Physical Mobility related to skin and musculoskeletal changes. […] Risk for Malnutrition related to gastrointestinal involvement. […] Nursing Interventions and Rationales for Scleroderma: Skin Care and Monitoring: Intervention: Regularly inspect the skin for any changes, such as thickening, swelling, or ulcers. Encourage the patient to maintain skin moisture with mild, hypoallergenic lotions. […] Rationale: Patients with scleroderma often have skin changes. Regular monitoring helps in early identification of complications like skin ulcers. Keeping the skin moisturized helps in managing dryness and preventing cracking, which can lead to infections. […] Pain Management: Intervention: Assess the patients pain level frequently and provide appropriate pain relief measures, which may include medications and non-pharmacological methods like warm compresses. […] Rationale: Pain management is crucial as scleroderma can cause discomfort due to skin tightness and joint involvement. Effective pain control enhances the patients quality of life and allows them to participate more fully in daily activities. […] Nutritional Support: Intervention: Assess nutritional status and provide guidance on a healthy diet. Encourage small, frequent meals and the inclusion of soft foods if the patient has difficulty swallowing. […] Rationale: Scleroderma can affect the digestive system, making swallowing difficult. Proper nutrition is essential for maintaining strength and overall health. Small, frequent meals and soft foods can make eating easier and more comfortable. […] Promotion of Physical Activity: Intervention: Encourage regular, gentle exercises like walking or swimming, and refer to physical therapy if needed. […] Rationale: Exercise helps maintain joint flexibility and overall physical health. It also aids in managing symptoms like fatigue and can improve mental health. […] Emotional Support and Education: Intervention: Provide emotional support and education about the disease. Encourage participation in support groups or counseling if the patient is experiencing emotional distress. […] Rationale: Living with a chronic condition like scleroderma can be challenging emotionally. Providing education about the disease helps the patient understand their condition and manage it effectively. Emotional support and counseling can help in coping with the stress and emotional aspects of the disease. […] Prevention of Complications: Intervention: Monitor for signs of complications such as high blood pressure, breathing difficulties, or gastrointestinal problems. […] Rationale: Scleroderma can affect various organs. Regular monitoring helps in early detection and management of complications, reducing the risk of severe outcomes. […] Temperature Regulation: Intervention: Advise the patient to dress warmly and avoid exposure to cold temperatures. Provide guidance on managing Raynauds phenomenon if present. […] Rationale: Patients with scleroderma often experience sensitivity to cold, and many have Raynauds phenomenon, where small blood vessels in the fingers and toes constrict excessively in response to cold. Keeping warm helps prevent these episodes and maintains comfort. […] Medication Management: Intervention: Assist in managing medications prescribed for scleroderma and monitor for side effects. […] Rationale: Medications can be a crucial part of managing scleroderma, including managing symptoms and slowing disease progression. Proper medication management ensures effectiveness and minimizes potential side effects.

• #10 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  Nursing care for patients with scleroderma is crucial in managing symptoms, preventing complications, and improving quality of life. […] The following are common nursing care planning goals and expected outcomes for scleroderma: […] The patient will report improved management of Raynauds phenomenon symptoms […] The patient will demonstrate increased joint mobility and reduced pain […] The patient will maintain adequate nutrition and report improved swallowing ability […] The patient will exhibit improved skin integrity and reduced risk of digital ulcers […] The patient will report the enhanced ability to perform activities of daily living […] The patient will demonstrate effective coping strategies for managing chronic illness. […] Perform daily skin assessments, focusing on areas prone to breakdown. Rationale: Early detection of skin changes allows for prompt intervention and prevention of complications.

• #11 Nursing Care Plan For Systemic Sclerosis – Made For Medical

  https://www.madeformedical.com/nursing-care-plan-for-systemic-sclerosis/

  These nursing interventions aim to address the physical, emotional, and psychosocial needs of individuals with systemic sclerosis. […] By implementing these interventions, nurses can contribute to improved patient outcomes, enhanced quality of life, and better management of systemic sclerosis. […] The nursing care plan for systemic sclerosis plays a pivotal role in providing comprehensive and individualized care to patients living with this complex autoimmune disorder. […] By incorporating evidence-based interventions and a patient-centered approach, nurses can effectively manage the diverse manifestations of systemic sclerosis and improve the overall quality of life for those affected. […] Through regular assessments and close monitoring, nurses can promptly identify changes in the patients condition, enabling early intervention and prevention of complications.

• #12 Self-care: 10 ways to relieve discomfort from scleroderma

  https://www.aad.org/public/diseases/a-z/scleroderma-self-care

  If you have skin problems, see a dermatologist who has experience treating scleroderma. Treatment for your skin can help reduce signs and symptoms, helping you to feel more comfortable. […] Make time to treat your skin. Having scleroderma can feel overwhelming. If you are also treating other symptoms, it can feel less important to treat the skin. Treating the skin is important. Started early, treatment can help you maintain your ability to move when hardening skin develops over a joint like a finger, knee, or jaw. […] Keep warm any area with thickened skin and sores. When the skin thickens and sores develop, it leads to poor circulation in that area. Keeping this area warm can increase blood flow, which can help with healing. […] Protect your skin from getting injured. Calcium deposits can develop if you injure your skin. These can be painful. They feel like firm bumps underneath the skin. If you get calcium deposits, its important to protect the skin that has calcium deposits from getting bumped or injured. This could cause a calcium deposit to break through the skin, which could be very painful and cause an infection.

• #13 Self-care: 10 ways to relieve discomfort from scleroderma

  https://www.aad.org/public/diseases/a-z/scleroderma-self-care

  Gently clean affected skin. Skin with scleroderma is dry and fragile. When washing, you want to be gentle. Use a mild fragrance-free cleanser, applying it gently with your fingertips. Rinse the cleanser away with warm water. […] Moisturize dry skin. Scleroderma can make the skin very dry. Dry skin is more easily injured. Infection and sores can develop. To reduce dry skin, dermatologists recommend that you apply a fragrance-free moisturizer every time after showering, taking a bath, and washing your hands. A thick cream or ointment works better than a lotion. […] Use a humidifier when the air feels dry. This can reduce dry skin. […] If you smoke, stop. Smoking wreaks havoc on the skin. It also worsens other symptoms of scleroderma like Raynaud phenomenon (extreme sensitivity to cold and stress).

• #14 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  Implement a gentle skincare routine using lukewarm water and mild, fragrance-free moisturizers. Rationale: Proper skin care helps maintain skin integrity and prevents further drying and cracking. […] Teach and encourage range of motion exercises for affected joints. Rationale: Regular movement helps maintain skin flexibility and prevents contractures. […] Apply protective dressings to existing ulcers and pressure points. Rationale: Appropriate wound care promotes healing and prevents infection. […] Educate the patient on the importance of avoiding extreme temperatures and protecting the skin from trauma. Rationale: Temperature extremes and minor injuries can exacerbate Raynauds phenomenon and lead to ulcer formation. […] The patient will demonstrate improved skin integrity within two weeks.

• #15 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  Provide small, frequent meals and soft or pureed foods as tolerated. Rationale: Smaller meals are easier to swallow and digest for patients with GI involvement. […] The patient will demonstrate weight stability or gain within one month. […] The patient will report improved ability to swallow and reduced GERD symptoms within two weeks. […] The patient will verbalize understanding of dietary modifications by the end of the education session. […] Assess pain characteristics, intensity, and impact on daily activities using a standardized pain scale. Rationale: Comprehensive pain assessment guides appropriate management strategies. […] Administer prescribed pain medications as ordered and evaluate their effectiveness. Rationale: Proper pain management improves quality of life and functional ability.

• #16 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  Apply warm compresses to affected joints and teach proper technique for home use. Rationale: Heat therapy can help reduce joint stiffness and improve circulation. […] Teach and encourage regular gentle exercises and stretching routines. Rationale: Physical activity helps maintain joint flexibility and reduces pain. […] The patient will report decreased pain intensity (by at least 2 points on the pain scale) within two weeks. […] The patient will demonstrate increased joint mobility within one month. […] The patient will utilize at least two non-pharmacological pain management techniques by the end of the education session. […] The patient will verbalize an improved understanding of scleroderma and its management within one week. […] The patient will demonstrate the use of at least two coping strategies within two weeks. […] The patient will express feelings of increased control over their condition within one month.

• #17 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  The patient will demonstrate improved breathing patterns within one week. […] The patient will maintain oxygen saturation 92% on room air within two weeks. […] The patient will verbalize understanding of breathing techniques by the end of the education session. […] Assess nutritional status, including weight, dietary intake, and laboratory values. Rationale: Comprehensive nutritional assessment helps identify specific deficiencies and guide interventions. […] Collaborate with a dietitian to develop a tailored meal plan. Rationale: A specialized diet can address nutritional needs while accommodating swallowing difficulties. […] Teach and encourage proper positioning during and after meals (upright for at least 30 minutes). Rationale: Proper positioning helps reduce reflux and improves swallowing.

• #18 Best self-care options for living with scleroderma | Southwest Florida Rheumatology

  https://www.swflrheum.com/living-with-scleroderma-best-scleroderma-self-care-options/

  Scleroderma is a rheumatic, autoimmune disease that affects the body’s connective tissue, mainly the skin and joints. The condition’s name itself means „hard skin.” […] A person living with scleroderma should seek treatment to help relieve the symptoms of this chronic condition. […] Patients can also engage in some self-care for treating scleroderma. […] Doctors can treat scleroderma and help patients manage their symptoms. While there is no cure for this autoimmune disease and the causes are unknown, patients have self-care options that can limit the long-term damage caused by scleroderma. […] For itchiness, a common symptom of this condition, using over-the-counter lotions free from fragrance is best. […] Patients with scleroderma should incorporate exercise and physical therapy into their routine to maintain mobility in their joints and to retain muscle strength. Exercise will also improve blood flow.

• #19 Scleroderma – Diagnosis and treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/scleroderma/diagnosis-treatment/drc-20351957

  As is true with other chronic diseases, living with scleroderma can cause you to feel anxious or worried. […] Keep in mind that your physical health can have a direct impact on your mental health. […] Joining a support group, where you can share experiences and feelings with other people, is often a good approach. […] You’ll probably first bring your symptoms to the attention of your family healthcare professional. […] Because scleroderma can affect many organ systems, you may need to see a variety of medical specialists.

• #20 Scleroderma – HealthyWomen

  https://www.healthywomen.org/condition/scleroderma

  Reducing stress is critical, and some experts suggest biofeedback training. It could help reduce pain and promote relaxation. […] Joining a scleroderma support group can also help with the emotional aspects of the disease, and you will be able to exchange information with others who have the same problems.

• #21

  https://myhealth.alberta.ca/Health/aftercareinformation/pages/conditions.aspx?hwid=zc1649

  Scleroderma cannot be cured, but in some cases the condition may improve over time. […] Follow-up care is a key part of your treatment and safety. […] You will probably need medicines to treat symptoms and to prevent long-term problems. […] Take your medicines exactly as prescribed. […] Check your blood pressure every day. […] Get regular exercise. This can help you stay strong and flexible. […] Talk to your doctor if you have sexual problems such as erectile dysfunction or pain with intercourse. […] Get help if you need it. Discuss your concerns with your doctor, counsellor, or other health professional. […] Call your doctor or nurse advice line now or seek immediate medical care if: You have new or worse trouble breathing. […] Watch closely for changes in your health, and be sure to contact your doctor or nurse advice line if: You have new or worse symptoms that worry you.

• #22 Scleroderma: Care Instructions | Kaiser Permanente

  https://healthy.kaiserpermanente.org/health-wellness/health-encyclopedia/he.scleroderma-care-instructions.zc1649

  Scleroderma is an autoimmune disease that affects the skin and blood vessels. It can also affect organs such as the kidneys, heart, esophagus, and lungs. […] Scleroderma cannot be cured, but in some cases the condition may improve over time. […] Follow-up care is a key part of your treatment and safety. Be sure to make and go to all appointments, and call your doctor if you are having problems. […] Take your medicines exactly as prescribed. Call your doctor if you have any problems with your medicine. […] Check your blood pressure every day. Call your doctor if it is higher than normal. […] Get regular exercise. This can help you stay strong and flexible. […] Call your doctor now or seek immediate medical care if: You have new or worse trouble breathing. […] Watch closely for changes in your health, and be sure to contact your doctor if: You have new or worse symptoms that worry you.

• #23 Scleroderma | Scleroderma Symptoms | MedlinePlus

  https://medlineplus.gov/scleroderma.html

  Scleroderma means „hard skin.” It’s the name of an autoimmune disease that causes inflammation and thickening in the skin and other areas of the body. This inflammation causes you to have areas of tight, hard skin. Scleroderma may affect just one area of your body, or it can affect many systems in your body. […] There is no cure for scleroderma, but treatments can help control your symptoms and limit damage. The treatments may include: […] Physical or occupational therapy to help with pain, improve muscle strength, and teach you ways to help with daily living. […] You may need to see specialists to help treat your disease. Many people with scleroderma will see a rheumatologist. This is a doctor who specializes in rheumatic diseases such as arthritis and other inflammatory or autoimmune disorders. Dermatologists, who specialize in conditions of the skin, hair, and nails, may also play an important role in treating the disease. […] You can also help manage some of your symptoms, for example by: Dressing warm and avoiding cold or wet environments.

• #24 Scleroderma: Diagnosis, Treatment, and Steps to Take

  https://www.niams.nih.gov/health-topics/scleroderma/diagnosis-treatment-and-steps-to-take

  Your treatment depends on the type of scleroderma you have, your symptoms, and which tissues and organs are affected. Treatment can help control the symptoms and limit damage. […] Many people benefit from physical or occupational therapy to: […] Regular dental care is important because scleroderma can make your mouth dry and damage connective tissues in your mouth, speeding up tooth decay and causing your teeth to become loose. […] To help minimize lung complications, work closely with your doctor. […] Because scleroderma can affect many different organs and organ systems, you may have several different doctors providing your care. […] Depending on the type of scleroderma you have and your symptoms, living with the disease may be hard. To help, try to take an active part in treating your scleroderma.

• #25 Scleroderma Program

  https://www.massgeneral.org/medicine/rheumatology/treatments-and-services/scleroderma

  Treatments may include: Immunosuppressive medications to control the body’s immune response, Medications that treat specific symptoms of scleroderma, such as pulmonary hypertension, lung disease, heartburn or Raynaud’s phenomenon, Occupational and Physical therapy to promote joint mobility and muscle strength. […] Most of our patients receive lifelong care at MGH. […] At MGH, we take a multi-disciplinary approach to managing a multi-system disease like scleroderma. […] Our experts are advancing the field of scleroderma through innovative studies. […] We perform a wide array of research, including clinical trials, observational and translational studies to better understand and manage scleroderma. […] Our fellowship program, affiliated with Harvard Medical School, offers physicians experience in the clinical aspects of scleroderma.

• #26 Scleroderma and Systemic Sclerosis (SSc): An Overview – HSS.edu

  https://www.hss.edu/conditions_scleroderma-and-systemic-sclerosis-overview.asp

  Scleroderma is a group of conditions affecting approximately 300,000 people in the United States. […] SSc affects approximately 100,000 people, or about one third of individuals with scleroderma in the United States. It is a chronic condition that should be treated and monitored by a rheumatologist, and frequently needs the input from physicians in other medical specialties. […] The care of individuals with scleroderma frequently requires a team approach. Depending on your symptoms, you will likely also need to be referred to other specialists including pulmonologists, cardiologists, gastroenterologists, nephrologists, or dermatologists. The treatment depends on the organ system involvement. […] Although there is no cure for SSc, there are many treatments which can improve the various symptoms of the disease.

• #27 Scleroderma and Systemic Sclerosis (SSc): An Overview – HSS.edu

  https://www.hss.edu/conditions_scleroderma-and-systemic-sclerosis-overview.asp

  Rehabilitation/Physical and occupational therapy (PT/OT): This is essential to overall health and maintenance function. The PT focus is on the larger muscle groups and the OT focus is on the fine motor skills especially the hands. There is an important role for PT and OT in the treatment of skin disease, arthritis, and muscle disease.

• #28 Scleroderma: Symptoms, Causes & Treatment Options

  https://my.clevelandclinic.org/health/diseases/scleroderma

  Scleroderma can be a very frustrating condition to live with. Because experts aren’t sure what causes it and there’s no one treatment that works for everyone, it might take time to find treatments that manage your symptoms well. Your healthcare provider will help you at every step of the process. […] Cleveland Clinic takes a team approach to scleroderma treatment. We’ll help you slow its progression and manage your symptoms.

• #29 Get Scleroderma Treatment | Cleveland Clinic

  https://my.clevelandclinic.org/services/scleroderma-treatment

  So, when you hear you may have scleroderma, youll want to find healthcare providers with lots of experience treating it. At Cleveland Clinic, our scleroderma experts are here to help you manage your symptoms, reduce flare-ups and damage and live more comfortably. […] Your provider may recommend a combination of therapies to manage scleroderma symptoms. Medications, physical therapy and lifestyle changes may reduce pain and help you move more comfortably. Well guide you through each step. […] Our team-based approach to care means youll have providers from different specialties working together to plan and manage your treatment. […] Once we get your test results back, your provider will go over them with you. And then theyll work with you to build a highly personalized treatment plan. This plan will focus on the type of scleroderma you have, your symptoms and your recovery goals.

• #30 Scleroderma and Raynaud’s Disease | UMass Memorial Health

  https://www.ummhealth.org/services-treatments/rheumatology/scleroderma-and-raynauds-disease

  UMass Memorial Health rheumatologists take care to accurately diagnose these conditions. We also make sure you understand the details of the condition you have, so you can make informed decisions about your care and treatment. […] Early diagnosis is important. At UMass Memorial, you receive a careful physical exam and appropriate diagnostic tests to confirm your diagnosis. Our team educates you about the conditions and discusses the most appropriate, up-to-date therapies available for treatment. […] Scleroderma may affect different body systems, like the lungs, kidneys, or intestinal tract, so your care team includes other specialists when needed. […] Our rheumatologists regularly discuss your treatment progress with your primary care provider (PCP) and other specialists. This ongoing communication allows your health care team to work together to help you feel your best.

• #31 Scleroderma Program > Departments > Yale Medicine

  https://www.yalemedicine.org/departments/scleroderma-program

  The goal is improved quality of life for our patients. […] We strive to ease the burden on patients and their families. […] Support staff help patients gather outside medical records and coordinate appointments with different specialists at Yale so that patients can get all their relevant medical care in one place. […] Doctors readily communicate about the plan of care through the electronic health record. […] We also actively participate in clinical research, to bring the most innovative treatments for the disease to our patients. […] Yale has been designated as a Scleroderma Center by the Scleroderma Foundation.

• #32 Get Scleroderma Treatment | Cleveland Clinic

  https://my.clevelandclinic.org/services/scleroderma-treatment

  Sometimes, you can manage mild scleroderma with lifestyle changes. We may recommend: Changing what and how you eat, Exercise, Joint and skin care, Proper dental care, Stress management, Physical therapy. […] Several medications can help manage severe symptoms, especially if scleroderma affects many of your organs. We may prescribe: Antacids, proton pump inhibitors (also called PPIs, like Prevacid, Protonix or Nexium) or H2 receptor blockers (Pepcid) to treat heartburn and GERD, Immunosuppresive drugs, such as mycophenolate mofetil (CellCept) or cyclophosphamide (Cytoxan) for lung scarring (pulmonary fibrosis) resulting from interstitial lung disease, Various medications for pulmonary hypertension, Nonsteroidal anti-inflammatory drugs (NSAIDs) and corticosteroids to relieve joint pain, Topical gels or creams to help moisturize dry, hard skin or treat skin sores, Various medications to treat Raynauds phenomenon and its symptoms, Drugs to manage and treat scleroderma-related kidney disease. […] A scleroderma diagnosis is serious, but treatable. Cleveland Clinics expert healthcare providers can help you find the best ways using the latest treatments to manage your symptoms, so you can live an active, healthy and productive life.

• #33 Scleroderma

  https://www.nhs.uk/conditions/scleroderma/

  There are many therapies and lifestyle changes that can help reduce the impact of scleroderma on your life. […] Regular physiotherapy and stretching exercises may help keep your muscles supple and loosen tight skin. […] An occupational therapist can help you adapt to any movement difficulties by suggesting changes to your home and advising you on equipment to make daily life easier. […] It’s important to eat healthily, exercise regularly and stop smoking (if you smoke) to keep blood pressure under control and improve your circulation.

• #34 Scleroderma: Nursing Diagnosis & Interventions | Nurse.com

  https://www.nurse.com/clinical-guides/scleroderma/?srsltid=AfmBOoq8jcaPb0Ty7CANyMPYZgnYQcluxFOibKRHX7OPhrB_wzRowTON

  Scleroderma is not curable, and any damage caused to body organs is irreversible. Early identification of multisystem involvement is imperative to prevent permanent damage. […] Management and treatments options are aimed towards symptom management and vary depending on the disease process specific to the individual. Management may involve pharmacological interventions, including (ACR, 2020): […] Appropriate interventions will be determined by the site and severity of the individuals scleroderma but may include the following: […] The individual will report and laboratory tests will confirm: […] Disease process: Various topics needed for adequate management include: […] Medication compliance: Importance of taking medication as prescribed to manage symptoms and irreversible changes.

• #35 Scleroderma Follow-up: Further Inpatient Care, Patient Education

  https://emedicine.medscape.com/article/331864-followup

  Patients with systemic sclerosis may need to be treated by other subspecialists, depending on the involvement of specific organ systems (eg, cardiologist, pulmonologist, gastroenterologist, nephrologist, endocrinologist, vascular surgeon, wound care specialist, hand surgeon). […] Patients should be counseled to keep regular follow up appointments with their rheumatologist. Patients should be vigilant to look for decreases in their exercise tolerance as cardiopulmonary disease is the largest cause of mortality in scleroderma. Patients should also be vigilant to watch their Raynaud’s phenomenon closely, avoid cigarette smoke, conservatively warm their hands in cool weather/environments, and look for any developing digital tip ulcerations. Consider providing patients with diffuse systemic sclerosis a blood pressure cuff so they can monitor their blood pressure weekly (to screen for scleroderma renal crisis).

• #36

  https://www.singhealth.com.sg/patient-care/conditions-treatments/scleroderma-systemic-sclerosis

  Scleroderma (Systemic Sclerosis) – Symptoms Treatments | SingHealth […] Even though there is no known cure for this condition yet, it is paramount to alleviating the various symptoms of the condition to limit damage to the internal organs with medication. Regular moderate exercise is important to improve joint flexibility and cardiovascular health. Consult your doctor or physiotherapist about the type of exercise you can do. Pain relief for stiff and swollen joints is usually possible with non-steroidal anti-inflammatory drugs. Areas of dry and irritated skin can be helped by a regular moisturiser. Antihistamines may help with intense itching of the skin. For Raynauds phenomenon, it is important to keep warm and to stop smoking. Medication to improve blood may be prescribed, while antibiotics can protect skin ulcers from getting infected. Proper wound care to promote ulcer healing can help to slow down the progression in scleroderma. For oesophageal involvement, H2 blockers, proton pump inhibitors or prokinetics may be prescribed. Simple measures such as avoiding acidic foods, eating smaller and more frequent meals, elevating the head of the bed and avoiding lying down for at least 3 hours after a meal can help to decrease symptoms of acid reflux. When a patient is diagnosed with diffuse scleroderma, medication may be prescribed to decrease the activity of the immune system. When internal organs are affected by the condition, other specific treatments may be needed.

• #37 Scleroderma | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/scleroderma

  Scleroderma is a chronic autoimmune condition that leads to scarring of the skin, joints, and other internal organs. […] Scleroderma can lead to scarring of the skin, joints, and other internal organs, but it’s important to remember that each child may experience scleroderma differently. […] Since there is no treatment for scleroderma itself, treatment is targeted to alleviate your child’s symptoms. Components of your child’s treatment may include: Nonsteroidal, anti-inflammatory medications (NSAIDs) or corticosteroids to relieve pain, Penicillamine to slow the skin thickening process and delay damage to internal organs, Immunosuppressive medications, such as methotrexate, Treating specific symptoms, such as heartburn and Raynaud’s phenomenon, Physical therapy and exercise to maintain your child’s muscle strength.

• #38 Scleroderma Care – Los Angeles, CA | UCLA Health

  https://www.uclahealth.org/medical-services/rheumatology/scleroderma

  Our multispecialty team of scleroderma experts provides comprehensive, personalized care. We work together to create well-rounded treatment plans that help you achieve your best health. […] Specialists in the UCLA Health Scleroderma Program provide state-of-the-art diagnosis and treatment for scleroderma, a rare disease that causes inflammation and scarring in the skin or internal organs. […] This recognition underscores our commitment to comprehensive, high-quality scleroderma care. […] A team of specialists works together to care for you. Your treatment may include care from a rheumatologist, pulmonologist, gastroenterologist, radiologist, cardiologist or hematologist, depending on your needs. […] Our specialists aim to understand all the factors that affect your overall wellness. With this knowledge, we can make recommendations for lifestyle changes to improve your health.

• #39 Scleroderma Care – Los Angeles, CA | UCLA Health

  https://www.uclahealth.org/medical-services/rheumatology/scleroderma

  We offer meditation, yoga and other integrative services as needed. […] We hold support groups for patients living with scleroderma, so you can connect with others going through similar experiences. […] Our multispecialty team offers the full range of scleroderma tests and treatment options. We comprehensively evaluate your symptoms and needs and find an effective treatment plan for you. […] The goal of scleroderma treatment is to slow down and, in some cases, reverse progression of the disease. […] Tailored nutrition guidance may help improve your health and quality of life. […] Many people with scleroderma take medications to reduce inflammation and scarring or suppress the immune system. […] Our scleroderma specialists are renowned experts in scleroderma diagnosis and treatment. […] We also make recommendations for lifestyle changes to help you live a healthier life. […] Our scleroderma specialists are dedicated to high-quality, research-based care.

• #40 Nursing Care Plan for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-scleroderma

  In summary, the nursing interventions for scleroderma focus on managing symptoms, preventing complications, and providing support and education. Each intervention is tailored to address the specific challenges and needs that a patient with scleroderma might face, ensuring a comprehensive and empathetic approach to their care. […] Evaluation for Scleroderma: Skin Condition: Monitor changes in skin condition and patients ability to perform skin care. […] Pain Level: Regular assessment of pain levels and effectiveness of pain management strategies. […] Mobility Status: Evaluate improvements or changes in mobility and joint function. […] Nutritional Status: Monitor weight, dietary intake, and signs of adequate nutrition.

• #41 Scleroderma Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/scleroderma-nursing-diagnosis/

  The patient will report the decreased incidence of Raynauds attacks within one month. […] The patient will exhibit proper skincare techniques by the end of the education session. […] Assess respiratory rate, depth, and effort every 4 hours. Rationale: Regular monitoring helps detect early signs of respiratory deterioration. […] Position the patient in a semi-Fowlers or high Fowlers position. Rationale: Upright positioning promotes optimal lung expansion and eases breathing effort. […] Teach and practice pursed-lip breathing and diaphragmatic breathing techniques. Rationale: These techniques help improve oxygenation and reduce the work of breathing. […] Administer oxygen therapy as prescribed and monitor oxygen saturation. Rationale: Supplemental oxygen helps maintain adequate tissue oxygenation.

• #42 03.07 Nursing Care and Pathophysiology for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/03-07-nursing-care-and-pathophysiology-for-scleroderma?parentId=449153

  We will assess this patients skin for morphea or linear scleroderma. […] We want to assess their respiratory status, especially if they have that pulmonary fibrosis. […] The doctor may order a lab draw for BUN and creatinine to assess kidney status. […] Elevated BUN and creatinine levels signal that the kidneys are damaged and not filtering the muscle and protein breakdown byproducts out of the body. […] Listen to the heart rate and rhythm. Is there blood pressure elevated? […] We may administer medications that the doctor orders like steroids to help decrease inflammation from the autoimmune attacks. […] Immune system suppressors like methotrexate might be used to slow the T cell attack on the healthy cells. […] Pain relief may be needed, especially for the patient that gets the collagen buildup in the vaginal opening.

• #43 03.07 Nursing Care and Pathophysiology for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/03-07-nursing-care-and-pathophysiology-for-scleroderma?parentId=449153

  Surgery may be necessary if the disease progresses to be severe, like amputation or an organ transplant. […] The doctor may recommend special skin care like steroid cream to help decrease inflammation. […] Protection of cold will help to decrease the effects of the Raynauds on the fingers and toes where there is decreased blood flow. […] Our priority nursing concepts for the patient with scleroderma are immunity, tissue/skin integrity, and gas exchange. […] The disease may be managed with stress management, blood pressure meds, autoimmune medications, and steroid creams for the skin.

• #44 03.07 Nursing Care and Pathophysiology for Scleroderma | Free NURSING.com Courses

  https://nursing.com/lesson/03-07-nursing-care-and-pathophysiology-for-scleroderma?parentId=449153

  Scleroderma is caused by an autoimmune disorder where there is injury to the vascular injury and an increase in the amount of protein in the skin. This causes hardening and tightening of the skin. […] Scleroderma is an autoimmune disease that is thought to be triggered by some sort of stressor and results in T cell attack on normal cells. Collagen is overproduced in all tissues causing hardening and tightening of the tissues of the body. […] The skin is the most obviously affected as you will notice the shiny skin patches. […] The blood vessels are thickened and tightened causing high blood pressure. […] The GI tract is affected, especially the esophagus causing reflux of acid. […] The kidneys end up with decreased blood flow due to the affected vessels which will result in sclerodermic renal crisis and eventually renal failure.

• #45 Systemic Sclerosis/Scleroderma: A Treatable Multisystem Disease | AAFP

  https://www.aafp.org/pubs/afp/issues/2008/1015/p961.html

  Treating active interstitial lung disease with oral cyclophosphamide (Cytoxan) for one year modestly improves lung function, dyspnea, skin thickening, and health-related quality of life in patients with systemic sclerosis. […] Initiation and continuation of angiotensin-converting enzyme inhibitors are recommended in patients with scleroderma renal crisis, even in the presence of elevated creatinine levels. […] Because of the heterogeneity of systemic sclerosis and potential treatment toxicity, therapy must be individualized to each patient’s clinical presentation and needs. […] There has been significant improvement in treatments for organ-specific complications, especially Raynaud phenomenon, scleroderma renal crisis, and gastrointestinal and pulmonary complications. […] All patients with systemic sclerosis should be advised to check their blood pressure at home on a regular basis. Any persistent elevations should prompt a medical evaluation and treatment with ACE inhibitors if scleroderma renal crisis is suspected.

• #46 Scleroderma – HealthyWomen

  https://www.healthywomen.org/condition/scleroderma

  A scleroderma treatment plan almost always incorporates therapy for Raynaud’s phenomenon, which afflicts about 90 percent of those with scleroderma. […] If you have been diagnosed with scleroderma, consult your physician before planning to have a baby. […] If lifestyle and dietary changes aren’t enough to avoid severe gastrointestinal symptoms and over-the-counter antacids don’t work, you and your physician may want to consider H2 blockers such as ranitidine (Zantac), cimetidine (Tagamet) or famotidine (Pepcid AC), which reduce the amount of acid produced by the stomach. […] Regular exercise or stretching can maintain joint flexibility and help keep your skin pliable. Other strategies include frequent massage of the skin and avoidance of detergent soaps, which dry the skin. Frequent use of bath oils and moisturizing lotions or ointments can help soften the skin, and a cold-water room humidifier can keep your skin moist.

• #47 New directions for patient-centred care in scleroderma: the Scleroderma Patient-centred Intervention Network (SPIN)

  https://pmc.ncbi.nlm.nih.gov/articles/PMC3925434/

  Systemic sclerosis (SSc), or scleroderma, is a chronic multisystem autoimmune disorder characterised by thickening and fibrosis of the skin and by the involvement of internal organs such as the lungs, kidneys, gastrointestinal tract, and heart. […] The goal of SPIN, as described in this article, is to develop, test, and disseminate a set of accessible interventions designed to complement standard care in order to improve HRQoL outcomes in SSc. […] The core mission of SPIN is to develop and evaluate effective, feasible, easily accessible, cost-efficient non-pharmacological interventions for patients with SSc. […] SPIN members prioritised areas that have been identified by patients as having a high impact on HRQoL and where there is enough basic research to confidently develop and test an intervention in SSc.

• #48 New directions for patient-centred care in scleroderma: the Scleroderma Patient-centred Intervention Network (SPIN)

  https://pmc.ncbi.nlm.nih.gov/articles/PMC3925434/

  Thus, current SPIN priorities include the development and testing of interventions to improve hand function, reduce symptoms of psychological distress, address body image concerns related to significant disfigurement, as well as to implement a general programme for self-management geared to the needs of SSc patients. […] The first priority of SPIN will be to develop a set of supportive care interventions. […] SPIN has prioritised a plan to develop and test a brief DVD/downloadable instructional video to educate physical/occupational therapists on exercises unique to SSc to improve hand function for patients. […] A telephone-or internet-based support intervention would reduce barriers to attendance, such as difficulty travelling due to disability from SSc and would be available to patients who live far from urban centres.

• #49 Scleroderma Program | University of Michigan Health

  https://www.uofmhealth.org/conditions-treatments/rheumatology/scleroderma-program

  The Michigan Medicine Scleroderma Program is a multidisciplinary group of care givers, scientists and clinical researchers dedicated to advancing knowledge about scleroderma and related conditions. Our mission is to provide local, national and international leadership in advancing the treatment of scleroderma and related conditions, through excellence in clinical care, teaching and research. The overarching goal of the Program is to develop effective therapies for the disease and its complications. […] The goals of the Scleroderma Program are to develop effective therapies for scleroderma and its complications and to research the causes and mechanisms of disease. It is only through enhanced understanding of disease process that a cure will be possible. […] The Self-Manage Scleroderma Program is an online self-management program designed to help you learn about scleroderma, manage your symptoms, and learn strategies to help you advocate for yourself. The program consists of learning modules about numerous topics including self-advocacy, coping, exercise, fatigue and energy conservation, mouth and teeth care, and pain management, along with printable resources to support your learning and help you apply what you have learned.

• #50 New directions for patient-centred care in scleroderma: the Scleroderma Patient-centred Intervention Network (SPIN)

  https://pmc.ncbi.nlm.nih.gov/articles/PMC3925434/

  The content and strategies incorporated in the social skills training workshops will serve as the foundation for the development of a workshop-based intervention that we plan to adapt for easy delivery to SSc patients with significant body image concerns, via either telephone or internet. […] Patients with SSc indicated that they would be more likely to find the programme beneficial if topics were geared towards managing the unique demands of living with SSc. […] One of the primary reasons that SPIN has been created is to provide a network of experts to fill the gap in SSc psychosocial and allied health research and clinical practice, by developing and testing patient-centred interventions with the goal of broad dissemination of evidence-based interventions for use by a spectrum of people with the disease as well as providers that care for these patients.

• #51

  https://www.nursingcenter.com/journalarticle?Article_ID=3299137&Journal_ID=403341&Issue_ID=3299128

  Systemic scleroderma (systemic sclerosis) is a rare, autoimmune, collagen-vascular disease of unknown etiology that affects the connective tissues of the skin, internal organs, as well as the small blood vessels. […] Because systemic scleroderma is not common, many orthopaedic nurses may be unfamiliar with how to best provide care. […] This article provides information about the complexity of the different types of this disease and the basic nursing care of the patient with the most common subclass of systemic scleroderma, limited cutaneous systemic scleroderma.

• #52 Nursing Care Plan For Systemic Sclerosis – Made For Medical

  https://www.madeformedical.com/nursing-care-plan-for-systemic-sclerosis/

  The emphasis on skin care, respiratory support, and swallowing assistance is crucial in managing the unique challenges presented by this condition. […] Through compassionate care, evidence-based practices, and continuous evaluation, nurses can make a significant impact in supporting individuals living with systemic sclerosis on their journey towards better health and improved quality of life.

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