Materiały źródłowe

• #1 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Utilize this comprehensive nursing care plan and management guide to provide effective care for patients with cystic fibrosis. Gain valuable insights on nursing assessment, interventions, goals, and nursing diagnosis specifically tailored for cystic fibrosis in this guide. […] Nursing management is essential in the interdisciplinary care of adults with cystic fibrosis (CF). Nurses help patients manage pulmonary symptoms, prevent complications, and promote secretion removal through strategies like chest physiotherapy and breathing exercises. Patients are educated on reducing respiratory infection risks and recognizing early signs of infection. Adequate fluid and dietary intake are emphasized for secretion removal and nutrition. As CF is a lifelong disorder, patients adapt daily activities as the disease progresses. Palliative care and end-of-life discussions should be addressed when necessary, providing support to patients and families facing a shortened lifespan and uncertainty.

• #2 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Cystic fibrosis (CF) is a rare, genetic, and progressive disease that primarily affects the pulmonary and digestive system but may involve multiple organ systems. Cystic fibrosis is often diagnosed as a newborn. There is no cure for CF, and patients may have a limited lifespan. […] Nurses may treat children with respiratory infections or care for adults who undergo lung or liver transplants and must understand the complex and delicate disease process of CF. […] The first step of nursing care is the nursing assessment, during which the nurse will gather physical, psychosocial, emotional, and diagnostic data. In this section, we will cover subjective and objective data related to cystic fibrosis. […] Nursing interventions and care are essential for the patients recovery. In the following section, you will learn more about possible nursing interventions for a patient with cystic fibrosis.

• #3 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Cystic fibrosis (CF) is a hereditary and progressive genetic disorder that primarily affects the respiratory and digestive systems. This life-limiting condition results from a faulty gene that affects the production of a protein responsible for regulating salt and water movement in the body’s cells. As a result, individuals with CF experience thick and sticky mucus buildup in the lungs, pancreas, and other organs, leading to recurrent respiratory infections, digestive problems, and other complications. […] Management of a child with cystic fibrosis should be holistic and meticulous. […] The major goals for the child include: relieving immediate respiratory distress, maintaining adequate oxygenation, remaining free from infection, improving nutritional status, and relieving anxiety. […] Implementation of the following goals include these interventions: improve airway clearance, improve breathing, prevent infection, maintain adequate nutrition, reduce the child’s anxiety, and provide family support.

• #4 Cystic Fibrosis Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/cystic-fibrosis-nursing-diagnosis/

  Cystic Fibrosis (CF) is a complex genetic disorder that primarily affects the respiratory and digestive systems. As a progressive condition, it requires comprehensive nursing care and ongoing management. This article provides detailed nursing diagnoses, interventions, and care plans for patients with cystic fibrosis. […] Nurses should be familiar with these key symptoms: […] Respiratory Assessment: […] Monitor respiratory rate, depth, and pattern Rationale: Enables early detection of respiratory deterioration […] Perform chest physiotherapy Rationale: Helps mobilize secretions and improve airway clearance […] Teach pursed-lip breathing Rationale: Improves ventilation and reduces work of breathing […] Position patient for optimal breathing Rationale: Promotes lung expansion and easier breathing

• #5 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Nursing care plans help prioritize assessments and interventions for both short and long-term goals of care. […] The buildup of mucus also prevents the release of digestive enzymes from the pancreas causing malnutrition. […] Nursing Diagnosis: Imbalanced Nutrition […] Nursing Diagnosis: Impaired Gas Exchange […] Nursing Diagnosis: Impaired Spontaneous Ventilation […] Nursing Diagnosis: Ineffective Airway Clearance […] Nursing Diagnosis: Risk for Infection […] Administer medications as ordered. These are the following medications given to patients with CF: Pancreatic enzyme supplements, Multivitamins, Mucolytics, Antibiotics, Bronchodilators, Anti-inflammatory agents, Medications treating related conditions or complications (such as insulin, bisphosphonates), Medications that can counteract chloride transport abnormalities (such as ivacaftor).

• #6 Nursing Care Plan & Diagnosis for Cystic Fibrosis with Nursing Interventions & Goals

  https://www.registerednursern.com/nursing-care-plan-diagnosis-for-cystic-fibrosis-with-nursing-interventions-goals/

  This nursing care plan for Cystic Fibrosis includes a diagnosis and care plan for nurses with nursing interventions and outcomes for the following conditions: Ineffective Airway Clearance Activity Intolerance. Patients who have cystic fibrosis are at risk for lung infections due to the body’s overproduction of secretions. […] Nursing Diagnosis: Ineffective Airway Clearance related to mucopurulent secretions related to inability to remove airway secretions secondary to pathophysiology of cystic fibrosis evidence by patient requiring deep suctions and reports inability to remove secretion with coughing. Activity Intolerance related to impaired oxygen transport secondary to mucopurulent secretions as evidence by reports and demonstrates dyspnea with activity. […] Nursing Interventions: The nurse will perform every 4 hours chest physiotherapy. The nurse will teach the patient how to perform effective coughing techniques daily. […] The nurse will collaborate with respiratory therapy regarding as needed breathing treatments and deep suctioning for shortness of breath and ineffective airway clearance.

• #7 Cystic Fibrosis Nursing Care Plan & Management

  https://www.rnpedia.com/nursing-notes/medical-surgical-nursing-notes/cystic-fibrosis/

  Cystic Fibrosis Nursing Care Plan Management […] Cystic Fibrosis is an autosomal recessive disorder affecting the exocrine glands, in which their secretions become abnormally viscous and liable to obstruct glandular ducts. It primarily affects pulmonary and GI function. The average life expectancy for the cystic fibrosis patient is currently age 30 to 40. Death may occur because of respiratory infection and failure. Other complications include esophageal varices, diabetes, chronic sinusitis, pancreatitis, rectal polyps, intussusceptions, growth retardation, and infertility. […] Primary Nursing Diagnosis: Ineffective airway clearance related to excess tenacious mucus. […] Therapeutic Intervention / Medical Management: Treatment for lung problems includes antibiotics to prevent and treat lung and sinus infections. They may be taken by mouth, or given in the veins or

• #8 Cystic Fibrosis Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/cystic-fibrosis-nursing-diagnosis/

  The patient maintains an effective breathing pattern […] Demonstrates improved respiratory function […] Shows decreased use of accessory muscles […] Imbalanced nutrition: less than body requirements related to pancreatic insufficiency as evidenced by weight loss and failure to thrive. […] Monitor weight and nutritional intake Rationale: Tracks nutritional status and effectiveness of interventions […] Administer pancreatic enzymes Rationale: Improves nutrient absorption […] Provide a high-calorie, high-protein diet Rationale: Meets increased metabolic demands […] Schedule small, frequent meals Rationale: Maximizes nutrient intake and absorption […] Patient maintains appropriate weight for height/age […] Demonstrates improved nutritional status […] Shows normal growth patterns

• #9 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Goals and expected outcomes may include: The client will maintain optimal gas exchange as evidenced by oxygen saturation of 90% or greater, arterial blood gases (ABGs) within the clients usual range, relaxed breathing, baseline heart rate, alert response mentation, and no further deterioration in the level of consciousness. The client will demonstrate comprehension of causative factors and appropriate interventions, actively engaging in the treatment regimen based on their abilities and individual circumstances. The client will be proficient in using effective airway clearance therapies to clear secretions on a daily basis, as evidenced by decreased work of breathing and improved pulmonary function. The client will maintain a clear, open airway as evidenced by normal breath sounds, normal rate and depth of respirations, and an airway free of secretions, with an effective cough. The client will experience improvement in infection and suppression of bacterial growth, as evidenced by a decrease in a cough, mucus production to baseline, normothermia, and normal white blood cell count.

• #10 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #11 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Nursing management for adults with CF involves addressing pulmonary symptoms, promoting secretion removal, and providing end-of-life support. This includes chest physiotherapy, breathing exercises, and ensuring adequate fluid and dietary intake. Regular reassessment and support for patients and families are essential. Therapeutic interventions and nursing actions for patients with cystic fibrosis (CF) may include: Maintaining patent airways and improving gas exchange are key objectives in the management of patients with cystic fibrosis (CF). CF is a genetic condition characterized by the production of thick mucus that can obstruct the airways and impair breathing. Effective airway clearance techniques, such as chest physiotherapy and inhalation therapies, are employed to help mobilize and remove mucus, ensuring proper airflow. Additionally, interventions like bronchodilators and mucolytic agents may be utilized to open the airways and improve gas exchange. By prioritizing these strategies, healthcare professionals aim to optimize respiratory function and enhance the overall well-being of individuals with CF.

• #12 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Treatments addressing malnutrition and sodium imbalance: Pancreatic enzyme supplements (amylase and/or lipase), Fat soluble vitamins; individuals with CF often have difficulty digesting and absorbing fat, Increased sodium intake, especially during hot weather and exercise, Calcium supplement, especially if pancreatic insufficiency is present, Increased calories, which can come from a well-balanced diet, or may need to be provided with nutritional supplements. […] Treatments addressing respiratory symptoms: Medications include bronchodilators, mucolytics, antibiotics, anti-inflammatory medications. […] Chest physiotherapy – Best done before meals to reduce risk of emesis. Involves both percussion and vibration. Can be very fatiguing for the patient and provider of therapy, so allow adequate time for rest.

• #13 Cystic Fibrosis NCLEX Review

  https://www.registerednursern.com/cystic-fibrosis-nclex-review/

  Chest physiotherapy (Chest PT): helps drain the airways of that thick sticky mucous. […] Chest PT: percussion (cupping hands and percussing of the over the lung fields and take special care when percussing over spine, stomach, breast bone, organs to avoid injury), some patients use vibration with a special vest and then huff coughing is performed. […] **Patient usually performs this 2-4 times per day or more depending on if they are fighting a lung infection. […] Airway Clearance devices: PEP (positive expiratory pressure): Helps with clearing the airway. […] Prevent infection: wearing a mask due flu times or when sick, hand hygiene, avoid sick people, and stay up-to-date with vaccinations, lung transplant possible if lung problems severe. […] Exercise: regular aerobic exercise to help keep lungs healthy and clear secretions.

• #14 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  Cystic fibrosis (CF) is a genetic disease that causes sticky, thick mucus to build up in your body. This can damage your lungs, pancreas and other organs. It can be difficult to breathe and to get enough nutrition. People with CF often get frequent infections. Management includes methods of clearing your airways, medications and a special diet. […] Management involves: Keeping your airways clear and open with breathing techniques and devices to loosen mucus. Medications that help correct issues with CFTR proteins (CFTR modulators). Medications that reduce specific symptoms. Ensuring you get enough of the right kinds of calories from food. Surgery. […] You can help to keep your airways clear if you have cystic fibrosis in a number of ways: Coughing and breathing techniques. A physical therapist who specializes in CF can teach you techniques that open your airways and loosen mucus. Positive expiratory pressure (PEP). PEP devices fit in your mouth or with a mask on your face. They provide resistance so you have to work harder to breathe out, holding your airways open and forcing out mucus.

• #15 Cystic Fibrosis Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/cystic-fibrosis-nursing-diagnosis/

  Cystic Fibrosis (CF) is a complex genetic disorder that primarily affects the respiratory and digestive systems. As a progressive condition, it requires comprehensive nursing care and ongoing management. This article provides detailed nursing diagnoses, interventions, and care plans for patients with cystic fibrosis. […] Nurses should be familiar with these key symptoms: […] Respiratory Assessment: […] Monitor respiratory rate, depth, and pattern Rationale: Enables early detection of respiratory deterioration […] Perform chest physiotherapy Rationale: Helps mobilize secretions and improve airway clearance […] Teach pursed-lip breathing Rationale: Improves ventilation and reduces work of breathing […] Position patient for optimal breathing Rationale: Promotes lung expansion and easier breathing

• #16 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  Cystic fibrosis (CF) is a genetic disease that causes sticky, thick mucus to build up in your body. This can damage your lungs, pancreas and other organs. It can be difficult to breathe and to get enough nutrition. People with CF often get frequent infections. Management includes methods of clearing your airways, medications and a special diet. […] Management involves: Keeping your airways clear and open with breathing techniques and devices to loosen mucus. Medications that help correct issues with CFTR proteins (CFTR modulators). Medications that reduce specific symptoms. Ensuring you get enough of the right kinds of calories from food. Surgery. […] You can help to keep your airways clear if you have cystic fibrosis in a number of ways: Coughing and breathing techniques. A physical therapist who specializes in CF can teach you techniques that open your airways and loosen mucus. Positive expiratory pressure (PEP). PEP devices fit in your mouth or with a mask on your face. They provide resistance so you have to work harder to breathe out, holding your airways open and forcing out mucus.

• #17 Caring for Cystic Fibrosis | Pulmonary & Respiratory Care | UNM Health System | Albuquerque, New Mexico

  https://unmhealth.org/services/pulmonology-respiratory-care/cystic-fibrosis-care.html

  Cystic fibrosis requires ongoing care to manage your symptoms including a few at-home techniques to open your airways. […] Your respiratory therapist will teach you the correct method. […] Autogenic drainage (AD) uses controlled breathing to move large amounts of thick mucus. […] Each level requires two to three minutes. The full cycle takes six to nine minutes. […] CPT for cystic fibrosis should be done three to four times a day. […] Nutritional therapy can improve your growth, development, strength and exercise tolerance.

• #18 Nursing Care Plan (NCP) for Cystic Fibrosis | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-cystic-fibrosis

  Monitor lung function through regular pulmonary function tests to assess the effectiveness of respiratory treatments. […] Assess weight gain and growth patterns, monitoring for improvements in nutritional status. […] Evaluate the patients adherence to the prescribed medication regimen. […] Assess the emotional well-being of the patient and family, considering the impact of CF on their daily lives. […] Evaluate the patients ability to independently perform airway clearance techniques.

• #19 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Nursing care plans help prioritize assessments and interventions for both short and long-term goals of care. […] The buildup of mucus also prevents the release of digestive enzymes from the pancreas causing malnutrition. […] Nursing Diagnosis: Imbalanced Nutrition […] Nursing Diagnosis: Impaired Gas Exchange […] Nursing Diagnosis: Impaired Spontaneous Ventilation […] Nursing Diagnosis: Ineffective Airway Clearance […] Nursing Diagnosis: Risk for Infection […] Administer medications as ordered. These are the following medications given to patients with CF: Pancreatic enzyme supplements, Multivitamins, Mucolytics, Antibiotics, Bronchodilators, Anti-inflammatory agents, Medications treating related conditions or complications (such as insulin, bisphosphonates), Medications that can counteract chloride transport abnormalities (such as ivacaftor).

• #20 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Administering medications and pharmacological support is essential in managing cystic fibrosis (CF), addressing digestion, airway function, and infections. From pancreatic enzyme replacement therapy to bronchodilators, mucolytics, CFTR modulators, and antibiotics, these tailored medications aim to optimize health outcomes and improve the quality of life for CF patients. […] Adequate nutrition is essential for individuals with CF as it supports overall health, enhances lung function, and improves the effectiveness of treatments. The management of CF-related nutrition typically involves a multidisciplinary approach that includes dietitians, physicians, and other healthcare professionals. Individualized nutritional plans are developed based on the unique needs of each patient, taking into account factors such as age, disease severity, growth patterns, and metabolic demands.

• #21 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Clear the airway. CF patients secrete viscous lung secretions. Administer mucolytic medications to improve secretion clearance and lessen sputum thickness. […] Administer hypertonic saline. For patients with CF aged six years and older, the long-term administration of hypertonic saline is advised to enhance lung function and prevent exacerbations by increasing the hydration of airway surface liquid. […] Instruct on pancreatic enzymes. Pancreatic enzymes are taken before meals to help patients digest their food and absorb nutrients. […] Encourage routine vaccinations. Patients with CF should receive routine vaccines, such as the seasonal influenza vaccine.

• #22 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Clear the airway. CF patients secrete viscous lung secretions. Administer mucolytic medications to improve secretion clearance and lessen sputum thickness. […] Administer hypertonic saline. For patients with CF aged six years and older, the long-term administration of hypertonic saline is advised to enhance lung function and prevent exacerbations by increasing the hydration of airway surface liquid. […] Instruct on pancreatic enzymes. Pancreatic enzymes are taken before meals to help patients digest their food and absorb nutrients. […] Encourage routine vaccinations. Patients with CF should receive routine vaccines, such as the seasonal influenza vaccine.

• #23 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Clear the airway. CF patients secrete viscous lung secretions. Administer mucolytic medications to improve secretion clearance and lessen sputum thickness. […] Administer hypertonic saline. For patients with CF aged six years and older, the long-term administration of hypertonic saline is advised to enhance lung function and prevent exacerbations by increasing the hydration of airway surface liquid. […] Instruct on pancreatic enzymes. Pancreatic enzymes are taken before meals to help patients digest their food and absorb nutrients. […] Encourage routine vaccinations. Patients with CF should receive routine vaccines, such as the seasonal influenza vaccine.

• #24 Cystic fibrosis – Symptoms and causes – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/symptoms-causes/syc-20353700

  Cystic fibrosis (CF) is a condition passed down in families that causes damage to the lungs, digestive system and other organs in the body. […] CF requires regular follow-up with your healthcare professional, at least every three months. Call your healthcare professional if you have new or worsening symptoms, such as more mucus than usual or a change in the mucus color, lack of energy, weight loss, or severe constipation. […] Managing cystic fibrosis can be very complex. So consider getting treatment at a center with medical professionals trained in the disorder to evaluate and treat your condition. […] Unfortunately, there is no cure for cystic fibrosis, but proper treatment can ease your symptoms, reduce complications, and improve your quality of life. […] Doctors may decide that certain medications are necessary. These could include antibiotics to treat and prevent lung infections, anti-inflammatories to lessen the swelling in your airways, or mucus-thinning drugs to help expel mucus and improve lung function.

• #25 Cystic Fibrosis Nursing CE Course for RNs and LPNs | NursingCE

  https://www.nursingce.com/ceu-courses/cystic-fibrosis-nursing-ce-course-for-rns-and-lpns

  Collectively, the disease results in a cascade of recurrent infections and chronic inflammatory processes. […] The CFF recommends that chronic respiratory medications only be administered to patients 6 years and older, as there is insufficient evidence to support the use of chronic respiratory agents in children younger than 6 years. […] Airway Clearance Therapy (ACT) is the backbone of preventative therapy in CF to preserve lung health for routine maintenance and during acute exacerbations. […] Daily ACT should be used in conjunction with medication therapy and all other pulmonary interventions offered. […] CFTR modulators are a novel group of medications that target the defective CF gene. […] These therapies are designed to correct the genetic dysfunction by refining the CFTR proteins production, intracellular processing, or functioning.

• #26 cystic fibrosis | PPT

  https://www.slideshare.net/hanasheque/cystic-fibrosis-14846489

  Cystic fibrosis is a genetic disease that causes thick, sticky mucus to build up in the lungs and digestive tract. […] Nursing care involves managing respiratory symptoms, maintaining nutrition, and reducing anxiety related to dyspnea. […] Treatments focus on airway clearance, antibiotics, nutrition support, and managing complications. […] Nursing diagnosis: Ineffective airway clearance related to excess tenacious mucus. Expected outcome: To improve pulmonary, GI and pancreatic status. […] Encourage regular exercise. Exercise helps maintain physical wellness and supplements the patients airways clearance strategies by helping to loosen pulmonary secretion. […] Administer oxygen therapy and receive digoxin to decrease the lungs work. […] Encourage coughing, deep breathing exercise, and frequent position changes to promote lung expansion, mobilization, and drainage of secretions.

• #27 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  CFTR modulators are medications that can help correct issues with proteins made by mutated CFTR genes and increase the amount of functioning proteins on your cells surfaces. Theyre not a cure for CF. But for certain people, theyve made dramatic improvements in symptoms and life expectancy. […] Your CF specialist or a registered dietitian may recommend a nutrition plan. It could include: Taking in extra calories each day. This might be up to twice as many calories as someone without CF. Eating foods that are high in fat. This is important in helping you get more fat-soluble vitamins. […] You may need surgery for cystic fibrosis or one of its complications. These might include: Surgery on your nose or sinuses. Bowel surgery to remove blockages. Lung transplant. Liver transplant. […] Taking care of yourself with CF includes developing a treatment plan with your healthcare team. You must follow this plan very closely to stay well, including: Strictly following your airway clearance regimen. Taking medications as prescribed. Attending regular office visits with your team of CF providers. […] You can reduce your risk of infections by avoiding people who are sick, practicing good handwashing techniques, and getting any recommended vaccinations.

• #28 The changing face of cystic fibrosis

  https://www.myamericannurse.com/the-changing-face-of-cystic-fibrosis/

  Its no longer a childhood illness. […] Nurses should be acquainted with the underlying cause, treatments, and basic cystic fibrosis care guidelines. […] With the growing number of adults with CF and continued improvements in clinical care and prescribed therapies, nurses should be familiar with the underlying cause of CF, its treatments and basic care guidelines, and the changing face of the disease. […] When caring for patients with CF, nurses must be aware of drug-to-food and drug-to-drug interactions and treatment side effects. Individualized treatment plans are the standard of care to address specific genetic mutations. And as this patient population survives longer, nurses will encounter them in a variety of adult care settings. […] As more patients with CF are seen in adult care settings, nurses will need to learn about the disease and the model of care used to meet patient needs.

• #29 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Administering medications and pharmacological support is essential in managing cystic fibrosis (CF), addressing digestion, airway function, and infections. From pancreatic enzyme replacement therapy to bronchodilators, mucolytics, CFTR modulators, and antibiotics, these tailored medications aim to optimize health outcomes and improve the quality of life for CF patients. […] Adequate nutrition is essential for individuals with CF as it supports overall health, enhances lung function, and improves the effectiveness of treatments. The management of CF-related nutrition typically involves a multidisciplinary approach that includes dietitians, physicians, and other healthcare professionals. Individualized nutritional plans are developed based on the unique needs of each patient, taking into account factors such as age, disease severity, growth patterns, and metabolic demands.

• #30 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  In the pancreas, mucus plugs clog the pancreatic ducts and prevent pancreatic enzymes from reaching the intestine. This leads to malabsorption of nutrients and failure-to-thrive (FTT). It can also damage beta islet cells, leading to cystic fibrosis related diabetes (CFRD). Common complications you’ll see with your CF patients include pancreatitis, cholelithiasis and cirrhosis. […] In the respiratory tract, mucus plugs block airways, impair gas exchange and put the individual at high risk for respiratory infection. Ninety percent of patients with CF will have some degree of pulmonary involvement. Significant complications that can occur are pneumothorax, significant hemoptysis and pulmonary hypertension. […] It’s important to note that there is no cure for CF and treatment is focused on managing symptoms related to malnutrition, impaired gas exchange, and infections.

• #31 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  CFTR modulators are medications that can help correct issues with proteins made by mutated CFTR genes and increase the amount of functioning proteins on your cells surfaces. Theyre not a cure for CF. But for certain people, theyve made dramatic improvements in symptoms and life expectancy. […] Your CF specialist or a registered dietitian may recommend a nutrition plan. It could include: Taking in extra calories each day. This might be up to twice as many calories as someone without CF. Eating foods that are high in fat. This is important in helping you get more fat-soluble vitamins. […] You may need surgery for cystic fibrosis or one of its complications. These might include: Surgery on your nose or sinuses. Bowel surgery to remove blockages. Lung transplant. Liver transplant. […] Taking care of yourself with CF includes developing a treatment plan with your healthcare team. You must follow this plan very closely to stay well, including: Strictly following your airway clearance regimen. Taking medications as prescribed. Attending regular office visits with your team of CF providers. […] You can reduce your risk of infections by avoiding people who are sick, practicing good handwashing techniques, and getting any recommended vaccinations.

• #32 Cystic Fibrosis for Med-Surg Nursing – LevelUpRN

  https://leveluprn.com/blogs/medical-surgical-nursing/respiratory-6-cystic-fibrosis?srsltid=AfmBOoq2qe4hPWpU4x3BlgoChIsrRQpSKQ8I9wWvdBrB3uJ8lrZXrBUy

  Cystic fibrosis is a genetic disorder that severely impairs lung function and causes dysfunction in other organs and tissues that make mucus or sweat. […] For nursing care of a patient with cystic fibrosis: Administer oxygen, encourage increased fluid intake, encourage a higher protein and calorie diet, and provide supplements, including fat-soluble vitamins A, D, E, and K. […] In terms of nursing care of cystic fibrosis, you’re going to administer oxygen as ordered. You’re going to encourage the patient to increase their fluid intake as well as their protein and calorie intake. And then you want to provide fat-soluble vitamin supplements as well. So this is vitamins A, D, E, and K.

• #33 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Treatments addressing malnutrition and sodium imbalance: Pancreatic enzyme supplements (amylase and/or lipase), Fat soluble vitamins; individuals with CF often have difficulty digesting and absorbing fat, Increased sodium intake, especially during hot weather and exercise, Calcium supplement, especially if pancreatic insufficiency is present, Increased calories, which can come from a well-balanced diet, or may need to be provided with nutritional supplements. […] Treatments addressing respiratory symptoms: Medications include bronchodilators, mucolytics, antibiotics, anti-inflammatory medications. […] Chest physiotherapy – Best done before meals to reduce risk of emesis. Involves both percussion and vibration. Can be very fatiguing for the patient and provider of therapy, so allow adequate time for rest.

• #34 cystic fibrosis | PPT

  https://www.slideshare.net/hanasheque/cystic-fibrosis-14846489

  Nursing diagnosis: Imbalanced nutrition related to poor appetite and increased calorie expenditure. Expected outcome: The patients weight will be stable at desired weight for height. […] Monitor food intake and weekly weight. Regular monitoring can help identify nutrition problems that are severe. […] Nursing diagnosis: Anxiety related to dyspnea. Expected outcome: The patient will state anxiety is controlled. The patient will be able to use techniques to control dyspnea and anxiety when they occur. […] Administer anti-anxiety medication. Medication can reduce anxiety but can also depress respiration, so should be used with caution. […] Although there is no cure for CF, treatments have improved greatly in recent years.

• #35 Cystic Fibrosis NCLEX Review

  https://www.registerednursern.com/cystic-fibrosis-nclex-review/

  GI: pancreatic enzymes, fat-soluble vitamins, high calories, high protein and high fat diet. […] How do you know the patient is receiving an adequate amount of enzymes? The patients stool is NOT greasy or odorous and they are free from abdominal bloating or pain. […] Some patients have feeding tubes because their caloric intake is very high, especially during illness or during the late stages of the disease. High protein and high calorie and fat diet with vitamin supplements like the fat-soluble: DEKA. […] Monitor for bowel obstruction: signs: no bowel movement, pain, cant pass gas etc.

• #36 Cystic Fibrosis NCLEX Review

  https://www.registerednursern.com/cystic-fibrosis-nclex-review/

  GI: pancreatic enzymes, fat-soluble vitamins, high calories, high protein and high fat diet. […] How do you know the patient is receiving an adequate amount of enzymes? The patients stool is NOT greasy or odorous and they are free from abdominal bloating or pain. […] Some patients have feeding tubes because their caloric intake is very high, especially during illness or during the late stages of the disease. High protein and high calorie and fat diet with vitamin supplements like the fat-soluble: DEKA. […] Monitor for bowel obstruction: signs: no bowel movement, pain, cant pass gas etc.

• #37 Cystic Fibrosis Nursing CE Course for RNs and LPNs | NursingCE

  https://www.nursingce.com/ceu-courses/cystic-fibrosis-nursing-ce-course-for-rns-and-lpns

  Management focuses on infection control and symptom management, intending to optimize function and maintain health for as long as possible. […] The ultimate goal is to preserve the quality of life and help patients optimize their functioning. […] Infection prevention and control strategies are the cornerstone of CF care. […] Adherence to IPC guidelines is encouraged to avoid infections, the transmission of CF pathogens, and the potential for pulmonary exacerbations. […] The clinical consequences of the mutations outlined in Table 2 are decreased chloride secretion and increased sodium reabsorption into the cellular space. […] The most commonly affected organs include the lungs, sinuses, pancreas, biliary and hepatic systems, intestines, and sweat glands. […] The symptoms of CF depend on which organ systems are affected and the severity of the disease.

• #38 Cystic Fibrosis: Nursing Diagnoses, Care Plans, Assessment & Interventions | NurseTogether

  https://www.nursetogether.com/cystic-fibrosis-nursing-diagnosis-care-plan/

  Clear the airway. CF patients secrete viscous lung secretions. Administer mucolytic medications to improve secretion clearance and lessen sputum thickness. […] Administer hypertonic saline. For patients with CF aged six years and older, the long-term administration of hypertonic saline is advised to enhance lung function and prevent exacerbations by increasing the hydration of airway surface liquid. […] Instruct on pancreatic enzymes. Pancreatic enzymes are taken before meals to help patients digest their food and absorb nutrients. […] Encourage routine vaccinations. Patients with CF should receive routine vaccines, such as the seasonal influenza vaccine.

• #39 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #40 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #41 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #42 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #43 Cystic Fibrosis Teaching 1422 | Nurse Teachings

  https://www.nurseteachings.com/teaching-1422

  The patient was instructed in cystic fibrosis the importance of breathing exercises, percussion and postural drainage techniques. The patient was taught to use the home nebulizer, metered-dose nebulizer, and other respiratory equipment necessary to release secretions and dilate the bronchi. The patient was reviewed the need to avoid known respiratory irritants such as smoke and air pollutants and persons with upper respiratory infections. The patient was taught on methods of clearing secretions, such as coughing, positioning, or suctioning. The patient was instructed on adaptive breathing techniques to decrease work of breathing. The patient was encouraged to participate in a program of aerobic exercise; swimming helps strengthen the muscles of respiration and promotes good breathing habits. […] Instructed on the importance of notifying physician, nurse or other health care provider immediately.

• #44 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #45 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Nurses play a crucial role in supporting infants, children, and adolescents with CF and their families as they navigate the challenges of a chronic illness. Successful adaptation and coping depend on both the client and the family, as well as the support they receive from various sources. Collaboration among healthcare professionals is essential to deliver comprehensive services that meet the unique needs of each family. […] Cystic fibrosis is a complex disease state which requires education related to a variety of topics, including lung health, nutrition, treatment, and genetics. Proper management of CF clients requires the thoughtful provision of client education to both clients and their caregivers.

• #46

• #47 Nursing Assignment: Cystic Fibrosis SOAP Note & Care Plan

  https://desklib.com/document/cystic-fibrosis-soap-note/

  The care provider would refer a psychotherapist in order to motivate and counsel the patient to feel better in mood and participate in regular chores. […] The patient as well as his family members would be educated about Cystic Fibrosis and its mode of inheritance and pathophysiology. […] It can thus, be expected that if the mentioned nursing goals are addressed appropriately to acquire positive nursing outcomes then the patient would be treated effectively and would be able to resume his normal living.

• #48 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Social workers can provide direct guidance to help you navigate your health insurance coverage, make tough decisions about school or the next steps in your career. […] Your CF social worker may refer you to a specialist such as a psychologist. […] The CF psychologist on your team may also help you overcome problems with balancing treatments and other aspects of your life by teaching you coping strategies. […] During your care center visits, the CF respiratory therapist performs pulmonary function tests (PFTs) to measure the air flow and volume in your lungs. […] Your physical therapist will work with you to design an exercise or fitness program that is based on your age, health status and include sports or other physical activities that you enjoy doing in order to maintain lung function and a generally good physical fitness level.

• #49 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  If your care team includes a CF pharmacist, he or she will help you learn about the benefits and potential side effects of your CF medications, including how to take your medication both at home and while you’re in the hospital. […] Your new team will still include a doctor, nurse, dietitian, social worker, respiratory therapist and program or care center coordinator, along with other specialists you may need, but they’re all experts in providing for the special health care needs of adults living with CF. […] As you become an adult and gain more freedom, you will be take on more responsibility in managing your CF.

• #50 Cystic Fibrosis | San Antonio | University Health

  https://www.universityhealth.com/services/lung-respiratory/conditions/cystic-fibrosis

  We are committed to providing superior health care for adults with cystic fibrosis. Our cystic fibrosis center actively provides a comprehensive approach to care through individual attention and specialized treatments designed to meet your unique medical needs. […] Our adult cystic fibrosis program is located in the same center as our pediatric cystic fibrosis program, resulting in a smooth treatment transition. […] Our outcomes are among the best in the nation. But thinking beyond that, we treat the whole person, and our discussions often include support for big life decisions. Our team works collaboratively to encourage you to move forward toward exciting milestones, such as: beginning your career, getting married or discussions about the possibility of starting a family. […] Treatment for cystic fibrosis takes place in multiple settings, including the clinic, hospital and home. Our clinical team is constantly keeping up with the latest therapies and continually showing our patients how to do some of the therapies away from the hospital, in the convenience of their own homes.

• #51 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Utilize this comprehensive nursing care plan and management guide to provide effective care for patients with cystic fibrosis. Gain valuable insights on nursing assessment, interventions, goals, and nursing diagnosis specifically tailored for cystic fibrosis in this guide. […] Nursing management is essential in the interdisciplinary care of adults with cystic fibrosis (CF). Nurses help patients manage pulmonary symptoms, prevent complications, and promote secretion removal through strategies like chest physiotherapy and breathing exercises. Patients are educated on reducing respiratory infection risks and recognizing early signs of infection. Adequate fluid and dietary intake are emphasized for secretion removal and nutrition. As CF is a lifelong disorder, patients adapt daily activities as the disease progresses. Palliative care and end-of-life discussions should be addressed when necessary, providing support to patients and families facing a shortened lifespan and uncertainty.

• #52 7 Cystic Fibrosis Nursing Care Plans – Nurseslabs

  https://nurseslabs.com/cystic-fibrosis-nursing-care-plans/

  Utilize this comprehensive nursing care plan and management guide to provide effective care for patients with cystic fibrosis. Gain valuable insights on nursing assessment, interventions, goals, and nursing diagnosis specifically tailored for cystic fibrosis in this guide. […] Nursing management is essential in the interdisciplinary care of adults with cystic fibrosis (CF). Nurses help patients manage pulmonary symptoms, prevent complications, and promote secretion removal through strategies like chest physiotherapy and breathing exercises. Patients are educated on reducing respiratory infection risks and recognizing early signs of infection. Adequate fluid and dietary intake are emphasized for secretion removal and nutrition. As CF is a lifelong disorder, patients adapt daily activities as the disease progresses. Palliative care and end-of-life discussions should be addressed when necessary, providing support to patients and families facing a shortened lifespan and uncertainty.

• #53 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  The identification of educational needs is crucial for nursing, especially at the time of diagnosis, in genetic counselling, in the life cycle transition periods in pre and post pulmonary transplantation, hospitalization and return home, in daily life activities, re-entry in school and in the promotion of the quality of life of adolescents with cystic fibrosis and family caregivers. […] Emphasis should also be given to the nurses’ role in training these adolescents and their family members to pay special attention to feeding, nebulization, oxygen therapy, which will most likely result in benefits to the adolescent and avoid hospital readmissions. […] The nurse, as a health team member who interacts closely with the adolescent and family in the transition health-illness process, is able to establish a close relationship and offer emotional support, contributing to the autonomy of the adolescents and their family members.

• #54 Nursing Care Plan (NCP) for Cystic Fibrosis | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-cystic-fibrosis

  Cystic fibrosis results from mutations in the CFTR (cystic fibrosis transmembrane conductance regulator) gene located on chromosome 7, leading to a dysfunctional CFTR protein. […] Learn the principles of providing holistic care for individuals with cystic fibrosis, including the management of respiratory and nutritional challenges, infection prevention, and psychosocial support. […] Administer respiratory treatments, including bronchodilators, mucolytics, and airway clearance therapies as prescribed. […] Monitor growth and development in pediatric patients. […] Administer pancreatic enzyme replacement therapy with meals to support nutrient absorption. […] Provide emotional support to the patient and family, addressing the challenges and impact of CF on daily life. […] Educate the patient and family about the importance of adherence to the treatment plan.

• #55 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #56 Phage Therapy May Treat Drug Resistance in Patients With Cystic Fibrosis, Study Finds < Yale School of Medicine

  https://medicine.yale.edu/news-article/phage-therapy-may-treat-drug-resistance-in-patients-with-cystic-fibrosis-study-finds/

  For the study, the research team investigated the use of phage therapythe use of viruses, or phages, to target and kill bacteriato help patients with cystic fibrosis, a disease in which antimicrobial resistance is a significant issue. […] By using phage therapy to help patients with cystic fibrosis, we are also finding solutions to address a growing crisis. […] The study found improved lung function, reduced sputum P. aeruginosaone of the most prevalent infection-causing bacteria in cystic fibrosisand evidence of phage-resistant bacteria having reduced pathogenicity in the nine adults treated with this therapy. […] Members of the research team have had conversations with the U.S. Centers for Disease Control and Prevention and the Cystic Fibrosis Foundation about setting up centers for phage therapy around the United States.

• #57 Cystic Fibrosis Teaching 1422 | Nurse Teachings

  https://www.nurseteachings.com/teaching-1422

  The patient was instructed in cystic fibrosis the importance of breathing exercises, percussion and postural drainage techniques. The patient was taught to use the home nebulizer, metered-dose nebulizer, and other respiratory equipment necessary to release secretions and dilate the bronchi. The patient was reviewed the need to avoid known respiratory irritants such as smoke and air pollutants and persons with upper respiratory infections. The patient was taught on methods of clearing secretions, such as coughing, positioning, or suctioning. The patient was instructed on adaptive breathing techniques to decrease work of breathing. The patient was encouraged to participate in a program of aerobic exercise; swimming helps strengthen the muscles of respiration and promotes good breathing habits. […] Instructed on the importance of notifying physician, nurse or other health care provider immediately.

• #58 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #59 Cystic fibrosis – Diagnosis and treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/diagnosis-treatment/drc-20353706

  Options for certain conditions caused by cystic fibrosis include nasal and sinus surgery, oxygen therapy, noninvasive ventilation, feeding tube, bowel surgery, lung transplant, and liver transplant. […] Cystic fibrosis can cause poor nutrition because the enzymes needed for digestion can’t reach the small intestine. This prevents food from being taken in and used by the body. […] Regular exercise helps loosen mucus in your airways and makes your heart stronger. […] Keep your regular follow-up appointments, take your medicines as prescribed and follow therapies as instructed. […] If you or someone you love has cystic fibrosis, you may have strong emotions such as depression, anxiety, anger or fear.

• #60 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  CFTR modulators are medications that can help correct issues with proteins made by mutated CFTR genes and increase the amount of functioning proteins on your cells surfaces. Theyre not a cure for CF. But for certain people, theyve made dramatic improvements in symptoms and life expectancy. […] Your CF specialist or a registered dietitian may recommend a nutrition plan. It could include: Taking in extra calories each day. This might be up to twice as many calories as someone without CF. Eating foods that are high in fat. This is important in helping you get more fat-soluble vitamins. […] You may need surgery for cystic fibrosis or one of its complications. These might include: Surgery on your nose or sinuses. Bowel surgery to remove blockages. Lung transplant. Liver transplant. […] Taking care of yourself with CF includes developing a treatment plan with your healthcare team. You must follow this plan very closely to stay well, including: Strictly following your airway clearance regimen. Taking medications as prescribed. Attending regular office visits with your team of CF providers. […] You can reduce your risk of infections by avoiding people who are sick, practicing good handwashing techniques, and getting any recommended vaccinations.

• #61 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  Caring for adolescents with a chronic disease implies knowing the different circumstances of these patients’ daily lives, whether these are factors related to the actual disease, such as family factors (family atmosphere, household members, socioeconomic status, degree of interference in family organisation), personal factors (temperament, motivation, problem-solving capacity, cognitive and intellectual capacity, self-awareness and self-esteem) and socio-environmental factors (social support and support from group of friends, community resources and school. […] The role of the family in the wellbeing of the adolescent is a determining factor in the adolescent’s capacity to adapt to this chronic disease. […] Healthcare professionals should have detailed information to be able to identify the different phases of the chronic disease and the way that adolescents and their parents/family deal with the situation.

• #62 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  The nurses play a decisive role in the follow-up provided in the different phases of life and in the different phases of the disease, and should also be the coordinating element of the healthcare team that takes care of these adolescents and their families. […] The College of the Speciality of Child Health and Paediatrics of the Portuguese Nurses’ Association, recommends that a nurse should „work in partnership with the adolescent and family/significant person, in any context in which the adolescent is found (hospitals, continuous care, health centres, school, community, home, …), so as to promote the highest status of health possible, provide care to a healthy or sick adolescent and provide education towards health as well as identify and mobilise resources to support the family/significant person.”

• #63 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  The CF care team approach means that health care professionals work together in partnership with you to provide comprehensive and high quality care for you or your child. […] You are an important member of your or your child’s CF care team. While you depend on your CF care team for essential guidance on your medical care, you are the expert in the daily management of your CF. […] There is a lot that you and your CF care team can do together to help you maintain your health with CF. As an active member on your own care team, you can help make sure that your treatment plan and comprehensive CF care reflects your personal needs and goals so that you can live a longer and healthier life. […] CF nurses specialize in CF care and fill a variety of nursing roles in the CF care center setting.

• #64 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Your CF nurse is your primary contact and is there to address your concerns, answer questions or direct you to the right CF care team member when discussing a specific part of your treatment plan. […] CF nurses also have the primary responsibility of providing CF education at initial diagnosis and throughout life. […] Your CF doctor is an expert in CF care and is often the director for the CF program. […] In order to provide you with comprehensive care based on current medical best practices, your CF doctor is responsible for staying on top of the latest CF care guidelines, trends in patient outcomes and new medications and therapies. […] Registered dietitians are trained to assess your daily food intake, growth and your overall nutritional status. They help you work towards your optimal body weight so that you have the calories and nutrients needed to fight off lung infections and maintain lung function.

• #65 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Your CF nurse is your primary contact and is there to address your concerns, answer questions or direct you to the right CF care team member when discussing a specific part of your treatment plan. […] CF nurses also have the primary responsibility of providing CF education at initial diagnosis and throughout life. […] Your CF doctor is an expert in CF care and is often the director for the CF program. […] In order to provide you with comprehensive care based on current medical best practices, your CF doctor is responsible for staying on top of the latest CF care guidelines, trends in patient outcomes and new medications and therapies. […] Registered dietitians are trained to assess your daily food intake, growth and your overall nutritional status. They help you work towards your optimal body weight so that you have the calories and nutrients needed to fight off lung infections and maintain lung function.

• #66 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Your CF nurse is your primary contact and is there to address your concerns, answer questions or direct you to the right CF care team member when discussing a specific part of your treatment plan. […] CF nurses also have the primary responsibility of providing CF education at initial diagnosis and throughout life. […] Your CF doctor is an expert in CF care and is often the director for the CF program. […] In order to provide you with comprehensive care based on current medical best practices, your CF doctor is responsible for staying on top of the latest CF care guidelines, trends in patient outcomes and new medications and therapies. […] Registered dietitians are trained to assess your daily food intake, growth and your overall nutritional status. They help you work towards your optimal body weight so that you have the calories and nutrients needed to fight off lung infections and maintain lung function.

• #67 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Social workers can provide direct guidance to help you navigate your health insurance coverage, make tough decisions about school or the next steps in your career. […] Your CF social worker may refer you to a specialist such as a psychologist. […] The CF psychologist on your team may also help you overcome problems with balancing treatments and other aspects of your life by teaching you coping strategies. […] During your care center visits, the CF respiratory therapist performs pulmonary function tests (PFTs) to measure the air flow and volume in your lungs. […] Your physical therapist will work with you to design an exercise or fitness program that is based on your age, health status and include sports or other physical activities that you enjoy doing in order to maintain lung function and a generally good physical fitness level.

• #68 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Social workers can provide direct guidance to help you navigate your health insurance coverage, make tough decisions about school or the next steps in your career. […] Your CF social worker may refer you to a specialist such as a psychologist. […] The CF psychologist on your team may also help you overcome problems with balancing treatments and other aspects of your life by teaching you coping strategies. […] During your care center visits, the CF respiratory therapist performs pulmonary function tests (PFTs) to measure the air flow and volume in your lungs. […] Your physical therapist will work with you to design an exercise or fitness program that is based on your age, health status and include sports or other physical activities that you enjoy doing in order to maintain lung function and a generally good physical fitness level.

• #69 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Social workers can provide direct guidance to help you navigate your health insurance coverage, make tough decisions about school or the next steps in your career. […] Your CF social worker may refer you to a specialist such as a psychologist. […] The CF psychologist on your team may also help you overcome problems with balancing treatments and other aspects of your life by teaching you coping strategies. […] During your care center visits, the CF respiratory therapist performs pulmonary function tests (PFTs) to measure the air flow and volume in your lungs. […] Your physical therapist will work with you to design an exercise or fitness program that is based on your age, health status and include sports or other physical activities that you enjoy doing in order to maintain lung function and a generally good physical fitness level.

• #70 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  Social workers can provide direct guidance to help you navigate your health insurance coverage, make tough decisions about school or the next steps in your career. […] Your CF social worker may refer you to a specialist such as a psychologist. […] The CF psychologist on your team may also help you overcome problems with balancing treatments and other aspects of your life by teaching you coping strategies. […] During your care center visits, the CF respiratory therapist performs pulmonary function tests (PFTs) to measure the air flow and volume in your lungs. […] Your physical therapist will work with you to design an exercise or fitness program that is based on your age, health status and include sports or other physical activities that you enjoy doing in order to maintain lung function and a generally good physical fitness level.

• #71 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  If your care team includes a CF pharmacist, he or she will help you learn about the benefits and potential side effects of your CF medications, including how to take your medication both at home and while you’re in the hospital. […] Your new team will still include a doctor, nurse, dietitian, social worker, respiratory therapist and program or care center coordinator, along with other specialists you may need, but they’re all experts in providing for the special health care needs of adults living with CF. […] As you become an adult and gain more freedom, you will be take on more responsibility in managing your CF.

• #72 Adult Cystic Fibrosis Care | MaineHealth Maine Medical Center | MaineHealth

  https://www.mainehealth.org/maine-medical-center/care-services/lung-care-pulmonology-mainehealth-maine-medical-center/adult-cystic-fibrosis-care-mainehealth-maine-medical-center

  Our compassionate team helps raise awareness of the disease in the general community, serving as an education and information resource, and conducting clinical research to improve the quality of care for CF patients. […] MaineHealth Adult Cystic Fibrosis Care Portland provides sweat testing and genotyping as well as other diagnostic techniques to confirm or exclude a cystic fibrosis diagnosis. Most diagnosed patients are seen four times a year: Two comprehensive visits, One multidisciplinary visit, One „Goals of Care” visit where long range goals and planning for major life events may be discussed. […] For nearly all visits you will be seen by one of the attending cystic fibrosis physicians and have spirometry (lung function testing) performed in addition to the general checkup. […] This is a comprehensive annual evaluation that includes assessment of blood chemistries, liver function, kidney function, lung function, blood sugar control, and vitamin levels.

• #73 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  If your care team includes a CF pharmacist, he or she will help you learn about the benefits and potential side effects of your CF medications, including how to take your medication both at home and while you’re in the hospital. […] Your new team will still include a doctor, nurse, dietitian, social worker, respiratory therapist and program or care center coordinator, along with other specialists you may need, but they’re all experts in providing for the special health care needs of adults living with CF. […] As you become an adult and gain more freedom, you will be take on more responsibility in managing your CF.

• #74 The changing face of cystic fibrosis

  https://www.myamericannurse.com/the-changing-face-of-cystic-fibrosis/

  Its no longer a childhood illness. […] Nurses should be acquainted with the underlying cause, treatments, and basic cystic fibrosis care guidelines. […] With the growing number of adults with CF and continued improvements in clinical care and prescribed therapies, nurses should be familiar with the underlying cause of CF, its treatments and basic care guidelines, and the changing face of the disease. […] When caring for patients with CF, nurses must be aware of drug-to-food and drug-to-drug interactions and treatment side effects. Individualized treatment plans are the standard of care to address specific genetic mutations. And as this patient population survives longer, nurses will encounter them in a variety of adult care settings. […] As more patients with CF are seen in adult care settings, nurses will need to learn about the disease and the model of care used to meet patient needs.

• #75 Your CF Care Team | Cystic Fibrosis Foundation

  https://www.cff.org/managing-cf/your-cf-care-team

  If your care team includes a CF pharmacist, he or she will help you learn about the benefits and potential side effects of your CF medications, including how to take your medication both at home and while you’re in the hospital. […] Your new team will still include a doctor, nurse, dietitian, social worker, respiratory therapist and program or care center coordinator, along with other specialists you may need, but they’re all experts in providing for the special health care needs of adults living with CF. […] As you become an adult and gain more freedom, you will be take on more responsibility in managing your CF.

• #76

  https://atriumhealth.org/medical-services/childrens-services/childrens-specialty-care/pediatric-pulmonary-medicine/cystic-fibrosis

  Cystic fibrosis requires complex, consistent treatment, and our treatment plans are designed around your childs unique needs. […] Here are a few of the ways we treat cystic fibrosis: […] Cystic fibrosis modulators, or drugs that target the basic defect causing CF. […] Social workers, who care for your family and every aspect of this disease at Levine Childrens. They make sure your child gets the support they need at school and help your family find financial resources. […] Dietitians, who are specially trained to care for children with cystic fibrosis and help them maintain good nutritional health. […] A nurse navigator, who helps you and your child coordinate care in our cystic fibrosis center and with other specialties, including gastroenterology; endocrinology; and ear, nose and throat. […] Cystic fibrosis can feel isolating for kids and their families. At Levine Childrens, we want you to know youre never alone were always here for you, and so are other CF families who know exactly what youre going through.

• #77

  https://atriumhealth.org/medical-services/childrens-services/childrens-specialty-care/pediatric-pulmonary-medicine/cystic-fibrosis

  Children with cystic fibrosis can be in and out of the hospital as they deal with managing their condition and infections. As a kid, it can be hard spending so much time away from home and other people. From our kid-friendly environment to child life specialists, our goal is to keep your child feeling as comfortable and as much like a kid as possible. […] We have all the experts your child needs in one place, including pediatric pulmonologists, gastroenterologists, dietitians, respiratory therapists, registered nurses and social workers. We work together to build the best care plan for your child and help them navigate life with a chronic disease. […] Atrium Health has accredited pediatric and adult cystic fibrosis programs, which means we can provide your child lifelong care. Were dedicated to helping patients understand how to care for their condition at an early age, and as they get older, we help them seamlessly transition to our adult program.

• #78 Discharge Instructions for Cystic Fibrosis | Saint Luke’s Health System

  https://www.saintlukeskc.org/health-library/discharge-instructions-cystic-fibrosis

  Oxygen therapy may be advised to treat low levels of oxygen in your child’s blood when they do physical activities or are at school or work. Encourage your child to exercise regularly and drink lots of fluids, as directed by their health care provider. […] Be sensitive to your childs mental health needs. Living with cystic fibrosis can be overwhelming. Connect with a support group or get professional counseling for your child and other family members as needed.

• #79

  https://atriumhealth.org/medical-services/childrens-services/childrens-specialty-care/pediatric-pulmonary-medicine/cystic-fibrosis

  Children with cystic fibrosis can be in and out of the hospital as they deal with managing their condition and infections. As a kid, it can be hard spending so much time away from home and other people. From our kid-friendly environment to child life specialists, our goal is to keep your child feeling as comfortable and as much like a kid as possible. […] We have all the experts your child needs in one place, including pediatric pulmonologists, gastroenterologists, dietitians, respiratory therapists, registered nurses and social workers. We work together to build the best care plan for your child and help them navigate life with a chronic disease. […] Atrium Health has accredited pediatric and adult cystic fibrosis programs, which means we can provide your child lifelong care. Were dedicated to helping patients understand how to care for their condition at an early age, and as they get older, we help them seamlessly transition to our adult program.

• #80 Cystic Fibrosis | Atrium Health Wake Forest Baptist

  https://www.wakehealth.edu/condition/c/cystic-fibrosis

  Cystic fibrosis is a disease that causes thick, sticky mucus to build up in the lungs, digestive tract, and other areas of the body. […] An early diagnosis of CF and treatment plan can improve both survival and quality of life. Follow-up and monitoring are very important. When possible, care should be received at a cystic fibrosis specialty clinic. When children reach adulthood, they should transfer to a cystic fibrosis specialty center for adults. […] At Wake Forest Baptist Medical Center, patients with cystic fibrosis are routinely followed by a multidisciplinary care team that includes nutritionists, respiratory therapists, physical therapists, and nurse practitioners skilled in their complicated care. […] Care and monitoring at home should include: Avoiding smoke, dust, dirt, fumes, household chemicals, fireplace smoke, and mold or mildew. Giving plenty of fluids, especially to infants and children in hot weather, when there is diarrhea or loose stools, or during extra physical activity. Exercising 2 or 3 times each week. Swimming, jogging, and cycling are good options. Clearing or bringing up mucus or secretions from the airways. This must be done 1 to 4 times each day. Patients, families, and caregivers must learn about doing chest percussion and postural drainage to help keep the airways clear.

• #81 Cystic Fibrosis My Way: Managing Daily CF Care | Children’s Hospital of Philadelphia

  https://www.chop.edu/video/cystic-fibrosis-my-way-managing-daily-cf-care

  Children and families with cystic fibrosis (CF) must carefully manage daily care at home to stay as healthy as possible. […] Be sure to always consult with your cystic fibrosis care team for individualized instructions on managing your childs CF.

• #82 Cystic Fibrosis | Atrium Health Wake Forest Baptist

  https://www.wakehealth.edu/condition/c/cystic-fibrosis

  Cystic fibrosis is a disease that causes thick, sticky mucus to build up in the lungs, digestive tract, and other areas of the body. […] An early diagnosis of CF and treatment plan can improve both survival and quality of life. Follow-up and monitoring are very important. When possible, care should be received at a cystic fibrosis specialty clinic. When children reach adulthood, they should transfer to a cystic fibrosis specialty center for adults. […] At Wake Forest Baptist Medical Center, patients with cystic fibrosis are routinely followed by a multidisciplinary care team that includes nutritionists, respiratory therapists, physical therapists, and nurse practitioners skilled in their complicated care. […] Care and monitoring at home should include: Avoiding smoke, dust, dirt, fumes, household chemicals, fireplace smoke, and mold or mildew. Giving plenty of fluids, especially to infants and children in hot weather, when there is diarrhea or loose stools, or during extra physical activity. Exercising 2 or 3 times each week. Swimming, jogging, and cycling are good options. Clearing or bringing up mucus or secretions from the airways. This must be done 1 to 4 times each day. Patients, families, and caregivers must learn about doing chest percussion and postural drainage to help keep the airways clear.

• #83 Treating and Managing Cystic Fibrosis | American Lung Association

  https://www.lung.org/lung-health-diseases/lung-disease-lookup/cystic-fibrosis/treating-and-managing

  There is no cure for CF, but there have been many advances in CF treatment that are helping patients live longer. […] Your treatment plan will be tailored to meet your needs. […] People with CF need to perform airway clearance therapy (ACT). […] People living with CF need to take certain enzymes and nutritional supplements. […] Antibiotics are frequently needed to treat bacteria that grow in the mucus of the lungs. […] Managing cystic fibrosis requires a team approach. […] Regular check-ups with your doctor are needed as patients with CF will require constant monitoring and health management to control symptoms and prevent complications. […] Most importantly all patients with CF need to continue treatments, including medicines, supplements, and daily airway clearance techniques as directed by their physicians.

• #84 Nursing Care for Cystic Fibrosis – Straight A Nursing

  https://straightanursingstudent.com/nursing-care-for-cystic-fibrosis/

  Teach the caregiver how to perform CPT and postural drainage. […] Teach the patient or caregiver about nutritional needs such as increased calories and fat, increased salt intake, and vitamin supplementation. […] Teach the patient and caregiver that special care must be taken to avoid infection. Basic guidelines are frequent hand hygiene, avoiding being around ill individuals, maintaining a distance of six feet from other individuals with cystic fibrosis, covering coughs and receiving all recommended vaccinations. […] So there you have it… your basic introduction to caring for patients with cystic fibrosis.

• #85 Cystic fibrosis – Symptoms and causes – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/symptoms-causes/syc-20353700

  Cystic fibrosis (CF) is a condition passed down in families that causes damage to the lungs, digestive system and other organs in the body. […] CF requires regular follow-up with your healthcare professional, at least every three months. Call your healthcare professional if you have new or worsening symptoms, such as more mucus than usual or a change in the mucus color, lack of energy, weight loss, or severe constipation. […] Managing cystic fibrosis can be very complex. So consider getting treatment at a center with medical professionals trained in the disorder to evaluate and treat your condition. […] Unfortunately, there is no cure for cystic fibrosis, but proper treatment can ease your symptoms, reduce complications, and improve your quality of life. […] Doctors may decide that certain medications are necessary. These could include antibiotics to treat and prevent lung infections, anti-inflammatories to lessen the swelling in your airways, or mucus-thinning drugs to help expel mucus and improve lung function.

• #86 Cystic Fibrosis Centers

  https://www.rwjbh.org/treatment-care/cystic-fibrosis/

  Cystic fibrosis is a genetic disorder and most people who have it will be diagnosed in the early stages of life. This condition creates a buildup of mucus in the lungs and airways, trapping bacteria and making the patient more susceptible to infection. […] Our clinics treat both adult and pediatric patients, providing families with quality care and referrals to community resources that can aid in their treatment. […] There is no cure for cystic fibrosis, but treatment and management can allow patients to live a comfortable, independent lifestyle without complication. Finding a treatment center with a medical staff you can trust and rely on is a key part of the process. […] At our Cystic Fibrosis Centers, we provide: Cystic fibrosis testing and screening, Consultations with parents who have a positive newborn screening, Education on nutrition and cystic fibrosis management, Counseling services, Life-long follow up care, Services for families caring for loved ones who have been diagnosed with cystic fibrosis, Patient checkups at least every three months for pulmonary function tests, throat cultures and consultations.

• #87 Cystic Fibrosis | Atrium Health Wake Forest Baptist

  https://www.wakehealth.edu/condition/c/cystic-fibrosis

  Cystic fibrosis is a disease that causes thick, sticky mucus to build up in the lungs, digestive tract, and other areas of the body. […] An early diagnosis of CF and treatment plan can improve both survival and quality of life. Follow-up and monitoring are very important. When possible, care should be received at a cystic fibrosis specialty clinic. When children reach adulthood, they should transfer to a cystic fibrosis specialty center for adults. […] At Wake Forest Baptist Medical Center, patients with cystic fibrosis are routinely followed by a multidisciplinary care team that includes nutritionists, respiratory therapists, physical therapists, and nurse practitioners skilled in their complicated care. […] Care and monitoring at home should include: Avoiding smoke, dust, dirt, fumes, household chemicals, fireplace smoke, and mold or mildew. Giving plenty of fluids, especially to infants and children in hot weather, when there is diarrhea or loose stools, or during extra physical activity. Exercising 2 or 3 times each week. Swimming, jogging, and cycling are good options. Clearing or bringing up mucus or secretions from the airways. This must be done 1 to 4 times each day. Patients, families, and caregivers must learn about doing chest percussion and postural drainage to help keep the airways clear.

• #88 Cystic Fibrosis | Atrium Health Wake Forest Baptist

  https://www.wakehealth.edu/condition/c/cystic-fibrosis

  Cystic fibrosis is a disease that causes thick, sticky mucus to build up in the lungs, digestive tract, and other areas of the body. […] An early diagnosis of CF and treatment plan can improve both survival and quality of life. Follow-up and monitoring are very important. When possible, care should be received at a cystic fibrosis specialty clinic. When children reach adulthood, they should transfer to a cystic fibrosis specialty center for adults. […] At Wake Forest Baptist Medical Center, patients with cystic fibrosis are routinely followed by a multidisciplinary care team that includes nutritionists, respiratory therapists, physical therapists, and nurse practitioners skilled in their complicated care. […] Care and monitoring at home should include: Avoiding smoke, dust, dirt, fumes, household chemicals, fireplace smoke, and mold or mildew. Giving plenty of fluids, especially to infants and children in hot weather, when there is diarrhea or loose stools, or during extra physical activity. Exercising 2 or 3 times each week. Swimming, jogging, and cycling are good options. Clearing or bringing up mucus or secretions from the airways. This must be done 1 to 4 times each day. Patients, families, and caregivers must learn about doing chest percussion and postural drainage to help keep the airways clear.

• #89 Nursing Care Plan (NCP) for Cystic Fibrosis | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-cystic-fibrosis

  Monitor lung function through regular pulmonary function tests to assess the effectiveness of respiratory treatments. […] Assess weight gain and growth patterns, monitoring for improvements in nutritional status. […] Evaluate the patients adherence to the prescribed medication regimen. […] Assess the emotional well-being of the patient and family, considering the impact of CF on their daily lives. […] Evaluate the patients ability to independently perform airway clearance techniques.

• #90 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #91 Cystic fibrosis – Symptoms and causes – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/symptoms-causes/syc-20353700

  Cystic fibrosis (CF) is a condition passed down in families that causes damage to the lungs, digestive system and other organs in the body. […] CF requires regular follow-up with your healthcare professional, at least every three months. Call your healthcare professional if you have new or worsening symptoms, such as more mucus than usual or a change in the mucus color, lack of energy, weight loss, or severe constipation. […] Managing cystic fibrosis can be very complex. So consider getting treatment at a center with medical professionals trained in the disorder to evaluate and treat your condition. […] Unfortunately, there is no cure for cystic fibrosis, but proper treatment can ease your symptoms, reduce complications, and improve your quality of life. […] Doctors may decide that certain medications are necessary. These could include antibiotics to treat and prevent lung infections, anti-inflammatories to lessen the swelling in your airways, or mucus-thinning drugs to help expel mucus and improve lung function.

• #92 Improving the care of patients with cystic fibrosis (CF)

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5609348/

  The West Midlands Adult Cystic Fibrosis (CF) Centre based at Birmingham Heartlands Hospital provides care for adults with CF in the West Midlands. […] We were concerned that this was resulting in quality and potential safety issues by causing delays in starting treatment and prolonging hospital inpatient stays. […] We therefore undertook a quality improvement project (QIP) aimed at addressing these issues. […] This QIP has improved the out-of-hours admissions process for adults with CF in our centre. […] Our aim was that 100% of patients with CF arriving out of hours (17:00-9:00, Monday-Friday and weekends) are clerked within 4 hours and prescribed appropriate treatment. […] Optimal treatment of pulmonary exacerbations requires recognition of unwell patients with CF by the clinicians, proactive admission to a specialised CF unit and prompt initiation of treatment, the mainstay of which is intravenous antibiotics.

• #93 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #94 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #95 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #96 Cystic fibrosis – Diagnosis and treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/diagnosis-treatment/drc-20353706

  Cystic fibrosis care at Mayo Clinic can help you with your cystic fibrosis-related health concerns. […] Managing CF is complicated, so it’s best to get treatment at a center with a multispecialty team of doctors and other healthcare professionals trained in CF. They can evaluate and treat your condition. […] The goals of treatment include preventing and controlling infections that occur in the lungs, removing and loosening mucus from the lungs, treating and preventing intestinal blockage, and getting enough nutrition. […] Airway clearance techniques, also called chest physical therapy, can help get rid of mucus blocking the airways. It also can help to lessen infection and inflammation in the airways. […] Your healthcare professional may recommend a long-term program called pulmonary rehabilitation. The program may improve your lung function and your overall well-being.

• #97 Pediatric Cystic Fibrosis Care Center | Children’s Hospital Los Angeles

  https://www.chla.org/pulmonology-and-sleep-medicine/programs-and-services/cystic-fibrosis-care-center

  Cystic fibrosis is an inherited condition that causes thick, sticky mucus to build up in a child’s lungs. This mucus blocks airways, making it hard to breathe. The condition also affects digestion. Cystic fibrosis is a lifelong condition that requires advanced care from a team of specialists. […] As a Cystic Fibrosis (CF) Foundation-accredited care center, we’re committed to providing the treatments, education and support your family needs. We provide comprehensive services to help your child enjoy life to the fullest. […] We offer a full suite of treatments, including emerging modulator drugs, nutritional counseling, respiratory therapy and more. Our team customizes a treatment plan based on your child’s unique symptoms and needs. […] We provide expert care for children who have CFTR-related metabolic syndrome (CRMS).

• #98 Pediatric Cystic Fibrosis Care Center | Children’s Hospital Los Angeles

  https://www.chla.org/pulmonology-and-sleep-medicine/programs-and-services/cystic-fibrosis-care-center

  Cystic fibrosis affects different body systems. We bring together specialists from different medical fields to manage all your child’s health care needs. […] Our care team helps children 8 and older take charge of their health. […] We foster strong relationships with families, ensuring your family has the necessary resources and support to manage this lifelong condition. […] We customize a care plan that meets your child’s unique needs. […] Our pediatric respiratory care practitioners teach you and your child airway clearance techniques. These methods clear mucus from your child’s lungs and open airways. […] Our registered dietitian nutritionists (RDNs) work with your family to ensure your child gets the calories and nutrients they need to grow and thrive. […] Children with cystic fibrosis receive coordinated care from a team of experts from various medical specialties. […] Our expert team of pulmonology and sleep medicine specialists diagnoses and manages all types of breathing, lung and sleep issues in children.

• #99 Cystic Fibrosis Centers

  https://www.rwjbh.org/treatment-care/cystic-fibrosis/

  Cystic fibrosis is a genetic disorder and most people who have it will be diagnosed in the early stages of life. This condition creates a buildup of mucus in the lungs and airways, trapping bacteria and making the patient more susceptible to infection. […] Our clinics treat both adult and pediatric patients, providing families with quality care and referrals to community resources that can aid in their treatment. […] There is no cure for cystic fibrosis, but treatment and management can allow patients to live a comfortable, independent lifestyle without complication. Finding a treatment center with a medical staff you can trust and rely on is a key part of the process. […] At our Cystic Fibrosis Centers, we provide: Cystic fibrosis testing and screening, Consultations with parents who have a positive newborn screening, Education on nutrition and cystic fibrosis management, Counseling services, Life-long follow up care, Services for families caring for loved ones who have been diagnosed with cystic fibrosis, Patient checkups at least every three months for pulmonary function tests, throat cultures and consultations.

• #100 Adult Cystic Fibrosis Care | MaineHealth Maine Medical Center | MaineHealth

  https://www.mainehealth.org/maine-medical-center/care-services/lung-care-pulmonology-mainehealth-maine-medical-center/adult-cystic-fibrosis-care-mainehealth-maine-medical-center

  MaineHealth Maine Medical Center has been accredited by the Cystic Fibrosis Foundation as cystic fibrosis (CF) teaching center. Lead by board-certified pulmonologists, MaineHealth Adult Cystic Fibrosis Care Portland is the primary cystic fibrosis treatment center in Maine. Our state of-the-art care includes advanced technology, patient educational materials and medication management. […] At MaineHealth Adult Cystic Fibrosis Care Portland, our goal is to help adults integrate daily CF care into their daily lives. We focus on independent breathing and airway clearance techniques; medication management; and care for related diseases such as bronchiectasis, immotile cilia syndromes and sinopulmonary disorders. Our multidisciplinary team includes: Pulmonologists, Nurses, Nutritionists, Social workers, Physical therapists, Respiratory therapists, Palliative care specialists.

• #101 Adult Cystic Fibrosis Care | MaineHealth Maine Medical Center | MaineHealth

  https://www.mainehealth.org/maine-medical-center/care-services/lung-care-pulmonology-mainehealth-maine-medical-center/adult-cystic-fibrosis-care-mainehealth-maine-medical-center

  An in-depth evaluation of nutritional, social and physical fitness needs will also be done. […] MaineHealth Adult Cystic Fibrosis Care Portland actively participates in the Northern New England CF Consortium (NNECFC). […] The mission of the group is to enhance CF care and patient outcomes within our region through clinical research and quality improvement projects. […] As a designated TDN Center, we participate in clinical trials to identify new and improved treatments for CF. […] The mission of the Cystic Fibrosis Foundation is to assure the development of the means to cure and control cystic fibrosis and to improve the quality of life for those with the disease. […] The mission of the NNECFC is to continuously improve the quality, safety, effectiveness and costs of care of CF patients and their families.

• #102 Adult Cystic Fibrosis Care | MaineHealth Maine Medical Center | MaineHealth

  https://www.mainehealth.org/maine-medical-center/care-services/lung-care-pulmonology-mainehealth-maine-medical-center/adult-cystic-fibrosis-care-mainehealth-maine-medical-center

  The Southern Maine Family Advisory Board aims to support and empower individuals living with Cystic Fibrosis and their families in their relationships with CF centers and hospitals in Maine; affect positive change by influencing the medical community, educational systems, workplace and government sectors; and accelerate the rate of improvement in CF care.

• #103 Cystic fibrosis

  https://www.nhs.uk/conditions/cystic-fibrosis/

  Cystic fibrosis requires life-long care. If you or your child are diagnosed with it, you will usually be referred to your nearest NHS cystic fibrosis care team. […] These teams are made up of different health professionals, usually based in larger NHS hospitals, who can provide treatment, support and advice on living with cystic fibrosis. […] You’ll be supported by different healthcare professionals. This may include specialist nurses and doctors, a physiotherapist and a dietitian. […] You may also need other treatments to help relieve symptoms and reduce the risk of complications. […] A physiotherapist can teach you ways you can improve your breathing and posture to help clear mucus from your lungs. […] A dietitian can provide advice on a high-energy diet that is easy to digest and you may be given supplements to help your digestion. […] Some people may eventually need a lung transplant if other treatments are not controlling their symptoms, although this is not suitable for everyone.

• #104 Cystic Fibrosis | University of Iowa Health Care Stead Family Children’s Hospital

  https://uihc.org/childrens/services/cystic-fibrosis

  There is no cure for cystic fibrosis, but symptoms can be eased or reduced with treatment. […] Our centers multidisciplinary specialists provide comprehensive care to address any symptoms or complications that may arise, aiming to improve the quality of life of our patients. […] Cystic fibrosis affects many areas of a patients health; we provide comprehensive, expert care that addresses the unique needs of each patient. […] The University of Iowa Cystic Fibrosis Center is certified as a care, education, and resource center by the Cystic Fibrosis Foundation.

• #105 Cystic fibrosis – Diagnosis and treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/cystic-fibrosis/diagnosis-treatment/drc-20353706

  Cystic fibrosis care at Mayo Clinic can help you with your cystic fibrosis-related health concerns. […] Managing CF is complicated, so it’s best to get treatment at a center with a multispecialty team of doctors and other healthcare professionals trained in CF. They can evaluate and treat your condition. […] The goals of treatment include preventing and controlling infections that occur in the lungs, removing and loosening mucus from the lungs, treating and preventing intestinal blockage, and getting enough nutrition. […] Airway clearance techniques, also called chest physical therapy, can help get rid of mucus blocking the airways. It also can help to lessen infection and inflammation in the airways. […] Your healthcare professional may recommend a long-term program called pulmonary rehabilitation. The program may improve your lung function and your overall well-being.

• #106 cystic fibrosis | PPT

  https://www.slideshare.net/hanasheque/cystic-fibrosis-14846489

  Cystic fibrosis is a genetic disease that causes thick, sticky mucus to build up in the lungs and digestive tract. […] Nursing care involves managing respiratory symptoms, maintaining nutrition, and reducing anxiety related to dyspnea. […] Treatments focus on airway clearance, antibiotics, nutrition support, and managing complications. […] Nursing diagnosis: Ineffective airway clearance related to excess tenacious mucus. Expected outcome: To improve pulmonary, GI and pancreatic status. […] Encourage regular exercise. Exercise helps maintain physical wellness and supplements the patients airways clearance strategies by helping to loosen pulmonary secretion. […] Administer oxygen therapy and receive digoxin to decrease the lungs work. […] Encourage coughing, deep breathing exercise, and frequent position changes to promote lung expansion, mobilization, and drainage of secretions.

• #107 Cystic Fibrosis Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/cystic-fibrosis-nursing-diagnosis/

  Risk for infection related to thick mucus accumulation and compromised respiratory defense mechanisms. […] Implement infection control measures Rationale: Reduces risk of cross-contamination […] Monitor for signs of infection Rationale: Enables early detection and treatment […] Promote immunization compliance Rationale: Protects against preventable infections […] Teach proper hand hygiene Rationale: Reduces transmission of pathogens […] The patient remains free from infection […] Demonstrates understanding of infection prevention […] Maintains effective airway clearance […] Activity intolerance related to impaired gas exchange and increased work of breathing as evidenced by fatigue and dyspnea with activity. […] Assess activity tolerance Rationale: Determines appropriate activity level

• #108 Cystic Fibrosis: Causes, Symptoms & Treatment

  https://my.clevelandclinic.org/health/diseases/9358-cystic-fibrosis

  Cystic fibrosis (CF) is a genetic disease that causes sticky, thick mucus to build up in your body. This can damage your lungs, pancreas and other organs. It can be difficult to breathe and to get enough nutrition. People with CF often get frequent infections. Management includes methods of clearing your airways, medications and a special diet. […] Management involves: Keeping your airways clear and open with breathing techniques and devices to loosen mucus. Medications that help correct issues with CFTR proteins (CFTR modulators). Medications that reduce specific symptoms. Ensuring you get enough of the right kinds of calories from food. Surgery. […] You can help to keep your airways clear if you have cystic fibrosis in a number of ways: Coughing and breathing techniques. A physical therapist who specializes in CF can teach you techniques that open your airways and loosen mucus. Positive expiratory pressure (PEP). PEP devices fit in your mouth or with a mask on your face. They provide resistance so you have to work harder to breathe out, holding your airways open and forcing out mucus.

• #109 cystic fibrosis | PPT

  https://www.slideshare.net/hanasheque/cystic-fibrosis-14846489

  Nursing diagnosis: Imbalanced nutrition related to poor appetite and increased calorie expenditure. Expected outcome: The patients weight will be stable at desired weight for height. […] Monitor food intake and weekly weight. Regular monitoring can help identify nutrition problems that are severe. […] Nursing diagnosis: Anxiety related to dyspnea. Expected outcome: The patient will state anxiety is controlled. The patient will be able to use techniques to control dyspnea and anxiety when they occur. […] Administer anti-anxiety medication. Medication can reduce anxiety but can also depress respiration, so should be used with caution. […] Although there is no cure for CF, treatments have improved greatly in recent years.

• #110 Adult Cystic Fibrosis Care | MaineHealth Maine Medical Center | MaineHealth

  https://www.mainehealth.org/maine-medical-center/care-services/lung-care-pulmonology-mainehealth-maine-medical-center/adult-cystic-fibrosis-care-mainehealth-maine-medical-center

  MaineHealth Maine Medical Center has been accredited by the Cystic Fibrosis Foundation as cystic fibrosis (CF) teaching center. Lead by board-certified pulmonologists, MaineHealth Adult Cystic Fibrosis Care Portland is the primary cystic fibrosis treatment center in Maine. Our state of-the-art care includes advanced technology, patient educational materials and medication management. […] At MaineHealth Adult Cystic Fibrosis Care Portland, our goal is to help adults integrate daily CF care into their daily lives. We focus on independent breathing and airway clearance techniques; medication management; and care for related diseases such as bronchiectasis, immotile cilia syndromes and sinopulmonary disorders. Our multidisciplinary team includes: Pulmonologists, Nurses, Nutritionists, Social workers, Physical therapists, Respiratory therapists, Palliative care specialists.

• #111 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  Caring for adolescents with a chronic disease implies knowing the different circumstances of these patients’ daily lives, whether these are factors related to the actual disease, such as family factors (family atmosphere, household members, socioeconomic status, degree of interference in family organisation), personal factors (temperament, motivation, problem-solving capacity, cognitive and intellectual capacity, self-awareness and self-esteem) and socio-environmental factors (social support and support from group of friends, community resources and school. […] The role of the family in the wellbeing of the adolescent is a determining factor in the adolescent’s capacity to adapt to this chronic disease. […] Healthcare professionals should have detailed information to be able to identify the different phases of the chronic disease and the way that adolescents and their parents/family deal with the situation.

• #112 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  This study revealed that nurses plan and implement interventions targeted at the adolescents’ needs in the several stages of life and disease, and also provide support to family caregivers, namely the parents. […] Results also show clear evidence on the nurse’s role as a caregiver, particularly in what concerns inhaled and intravenous medication administration, enteral and parenteral nutrition, ventilator weaning and oxygen administration. […] In this literature review, all studies refer to nursing interventions, mainly focused on communication processes, considered an important and efficient method to provide emotional and psychologic support, aiming at tailor-made care plans. […] Encouraging the involvement of family members in the therapeutic process and the support to the family as the most important promoter of the adolescent well-being is a key factor that will enable the adolescent to better adapt to the chronic disease.

• #113 Pediatric Cystic Fibrosis Care Center | Children’s Hospital Los Angeles

  https://www.chla.org/pulmonology-and-sleep-medicine/programs-and-services/cystic-fibrosis-care-center

  Cystic fibrosis affects different body systems. We bring together specialists from different medical fields to manage all your child’s health care needs. […] Our care team helps children 8 and older take charge of their health. […] We foster strong relationships with families, ensuring your family has the necessary resources and support to manage this lifelong condition. […] We customize a care plan that meets your child’s unique needs. […] Our pediatric respiratory care practitioners teach you and your child airway clearance techniques. These methods clear mucus from your child’s lungs and open airways. […] Our registered dietitian nutritionists (RDNs) work with your family to ensure your child gets the calories and nutrients they need to grow and thrive. […] Children with cystic fibrosis receive coordinated care from a team of experts from various medical specialties. […] Our expert team of pulmonology and sleep medicine specialists diagnoses and manages all types of breathing, lung and sleep issues in children.

• #114 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #115 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #116 Cystic Fibrosis | San Antonio | University Health

  https://www.universityhealth.com/services/lung-respiratory/conditions/cystic-fibrosis

  We are committed to providing superior health care for adults with cystic fibrosis. Our cystic fibrosis center actively provides a comprehensive approach to care through individual attention and specialized treatments designed to meet your unique medical needs. […] Our adult cystic fibrosis program is located in the same center as our pediatric cystic fibrosis program, resulting in a smooth treatment transition. […] Our outcomes are among the best in the nation. But thinking beyond that, we treat the whole person, and our discussions often include support for big life decisions. Our team works collaboratively to encourage you to move forward toward exciting milestones, such as: beginning your career, getting married or discussions about the possibility of starting a family. […] Treatment for cystic fibrosis takes place in multiple settings, including the clinic, hospital and home. Our clinical team is constantly keeping up with the latest therapies and continually showing our patients how to do some of the therapies away from the hospital, in the convenience of their own homes.

• #117 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  The identification of educational needs is crucial for nursing, especially at the time of diagnosis, in genetic counselling, in the life cycle transition periods in pre and post pulmonary transplantation, hospitalization and return home, in daily life activities, re-entry in school and in the promotion of the quality of life of adolescents with cystic fibrosis and family caregivers. […] Emphasis should also be given to the nurses’ role in training these adolescents and their family members to pay special attention to feeding, nebulization, oxygen therapy, which will most likely result in benefits to the adolescent and avoid hospital readmissions. […] The nurse, as a health team member who interacts closely with the adolescent and family in the transition health-illness process, is able to establish a close relationship and offer emotional support, contributing to the autonomy of the adolescents and their family members.

• #118 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  The nurses play a decisive role in the follow-up provided in the different phases of life and in the different phases of the disease, and should also be the coordinating element of the healthcare team that takes care of these adolescents and their families. […] The College of the Speciality of Child Health and Paediatrics of the Portuguese Nurses’ Association, recommends that a nurse should „work in partnership with the adolescent and family/significant person, in any context in which the adolescent is found (hospitals, continuous care, health centres, school, community, home, …), so as to promote the highest status of health possible, provide care to a healthy or sick adolescent and provide education towards health as well as identify and mobilise resources to support the family/significant person.”

• #119 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  Cystic Fibrosis (CF) is an inherited chronic health condition characterized by exocrine (or mucus-producing) gland dysfunction. CF is characterized by: Increased viscosity of mucous gland secretions, Elevation of sweat electrolytes, Increase in several organic and enzymatic constituents of saliva, Abnormalities in autonomic nervous system function. […] Symptoms associated with CF depend on which organs are affected and how severe the condition is. The most common symptoms associated with CF affect the lungs and include a chronic cough and wheezing. […] It is important that the school nurse advocates for the student and talks with the teacher(s) to educate them about the students cough. The student should be permitted to leave the classroom, if that makes them feel more comfortable but should not feel as though they are required to. Additionally, students with CF should not be given medications to suppress their cough or dry up their secretions, as these medications are counterproductive to having the student thinning the mucus and coughing it out.

• #120 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #121 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #122 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #123 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  Cystic Fibrosis (CF) is an inherited chronic health condition characterized by exocrine (or mucus-producing) gland dysfunction. CF is characterized by: Increased viscosity of mucous gland secretions, Elevation of sweat electrolytes, Increase in several organic and enzymatic constituents of saliva, Abnormalities in autonomic nervous system function. […] Symptoms associated with CF depend on which organs are affected and how severe the condition is. The most common symptoms associated with CF affect the lungs and include a chronic cough and wheezing. […] It is important that the school nurse advocates for the student and talks with the teacher(s) to educate them about the students cough. The student should be permitted to leave the classroom, if that makes them feel more comfortable but should not feel as though they are required to. Additionally, students with CF should not be given medications to suppress their cough or dry up their secretions, as these medications are counterproductive to having the student thinning the mucus and coughing it out.

• #124 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  Cystic Fibrosis (CF) is an inherited chronic health condition characterized by exocrine (or mucus-producing) gland dysfunction. CF is characterized by: Increased viscosity of mucous gland secretions, Elevation of sweat electrolytes, Increase in several organic and enzymatic constituents of saliva, Abnormalities in autonomic nervous system function. […] Symptoms associated with CF depend on which organs are affected and how severe the condition is. The most common symptoms associated with CF affect the lungs and include a chronic cough and wheezing. […] It is important that the school nurse advocates for the student and talks with the teacher(s) to educate them about the students cough. The student should be permitted to leave the classroom, if that makes them feel more comfortable but should not feel as though they are required to. Additionally, students with CF should not be given medications to suppress their cough or dry up their secretions, as these medications are counterproductive to having the student thinning the mucus and coughing it out.

• #125 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should review the health care providers order to see if there are any activity restrictions or precautions during physical education class or at recess. […] The school nurse should discuss with the student and their family about the students desire for the students peers and school staff to be made aware and educated about the students CF. […] An important first step when caring for a student who is diagnosed with a CF would be to complete a health history and physical assessment, preferably with the student and their parents present. […] The school nurse should assess the students current and desired level of independence to determine what goals should be established for the student. […] The school nurse will want to receive an order from a health care provider. […] The school nurse should collaborate with the health care provider and parent/guardian to establish a plan and ensure the necessary orders are in place if the student is take the enzymes when eating these types of foods.

• #126 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #127 Cystic Fibrosis | Show Me School Health

  https://showmeschoolhealth.org/resources/cystic-fibrosis/

  The school nurse should document that the UAPs knowledge, abilities, and skills have been assessed. […] The school nurse may also want to consider including the following goals in the students IHCP. The student will: Maintain optimal respiratory function and airway clearance by: Keep their lungs functioning as well as possible, Taking their medications, Avoiding friends when they are ill, Performing their ACT as recommended, Avoiding high risk behaviors such as smoking and vaping. […] Students with CF need to perform airway clearance therapy (ACT). ACTs are performed to assist the student in loosening and moving the thick, sticky secretions from the students lungs and airway and would be ordered by the health care provider. […] The school nurse must also plan for other potential emergencies such as lockdown, extreme weather events, evacuations, and shelter-in-place events. […] Students with CF may qualify for a Section 504 Plan since their health condition may impact a major life activity (breathing).

• #128 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #129 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Interventions for cystic fibrosis can involve medications (such as antibiotics, bronchodilators, and enzyme replacement therapy), lifestyle changes (such as avoiding contact with tobacco smoke and outdoor pollutants), non-pharmacological treatments (such as coughing and chest physiotherapy, use of a vibration platform, and dietary management), education and support, and physical and occupational therapies. […] Evaluation of the care plan is ongoing and should include ongoing assessment of the patients signs and symptoms. It should also include monitoring the patients progress toward achieving the established goals. The evaluation should include input from the patient and their family regarding the impact of treatment on their daily lives and their satisfaction with the care they receive.

• #130 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #131 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #132 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #133 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #134 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #135 Cystic Fibrosis Nursing Care Management: Study Guide

  https://nurseslabs.com/cystic-fibrosis/

  Goals are met as evidenced by: relief of immediate respiratory distress, maintenance of adequate oxygenation, freedom from infection, improvement of nutritional status, and relief of anxiety. […] Documentation for a child with CF includes: impact of condition on personal image and lifestyle, current or recent antibiotic therapy, plan of care, teaching plan, responses to interventions, teaching, and actions performed, attainment or progress towards desired outcomes, and modifications to plan of care.

• #136 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Interventions for cystic fibrosis can involve medications (such as antibiotics, bronchodilators, and enzyme replacement therapy), lifestyle changes (such as avoiding contact with tobacco smoke and outdoor pollutants), non-pharmacological treatments (such as coughing and chest physiotherapy, use of a vibration platform, and dietary management), education and support, and physical and occupational therapies. […] Evaluation of the care plan is ongoing and should include ongoing assessment of the patients signs and symptoms. It should also include monitoring the patients progress toward achieving the established goals. The evaluation should include input from the patient and their family regarding the impact of treatment on their daily lives and their satisfaction with the care they receive.

• #137 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Cystic Fibrosis is a life-threatening disease that affects the lungs and iviscera, and causes recurrent respiratory and digestive systems. It has no known cure. The goal of caring for people with cystic fibrosis is to keep them as healthy as possible and require the least amount of medical interventions. […] The nursing diagnosis for cystic fibrosis involves identifying risk factors such as airway obstruction, impaired gas exchange, or inadequate nutrition. It also includes establishing goals for improving health outcomes, such as reducing the frequency and severity of exacerbations, preventing pulmonary infections, and managing sleep disruption. […] The goal of a care plan is to identify measurable outcomes. Outcomes may include an improvement in lung function test results, increased exercise tolerance, an increased ability to cope with stress and depression, improved quality of life, and a decrease in hospitalizations.

• #138 Nursing Care Plan (NCP) for Cystic Fibrosis | Free NURSING.com Courses

  https://nursing.com/lesson/nursing-care-plan-for-cystic-fibrosis

  Monitor lung function through regular pulmonary function tests to assess the effectiveness of respiratory treatments. […] Assess weight gain and growth patterns, monitoring for improvements in nutritional status. […] Evaluate the patients adherence to the prescribed medication regimen. […] Assess the emotional well-being of the patient and family, considering the impact of CF on their daily lives. […] Evaluate the patients ability to independently perform airway clearance techniques.

• #139 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Cystic Fibrosis is a life-threatening disease that affects the lungs and iviscera, and causes recurrent respiratory and digestive systems. It has no known cure. The goal of caring for people with cystic fibrosis is to keep them as healthy as possible and require the least amount of medical interventions. […] The nursing diagnosis for cystic fibrosis involves identifying risk factors such as airway obstruction, impaired gas exchange, or inadequate nutrition. It also includes establishing goals for improving health outcomes, such as reducing the frequency and severity of exacerbations, preventing pulmonary infections, and managing sleep disruption. […] The goal of a care plan is to identify measurable outcomes. Outcomes may include an improvement in lung function test results, increased exercise tolerance, an increased ability to cope with stress and depression, improved quality of life, and a decrease in hospitalizations.

• #140 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Cystic Fibrosis is a life-threatening disease that affects the lungs and iviscera, and causes recurrent respiratory and digestive systems. It has no known cure. The goal of caring for people with cystic fibrosis is to keep them as healthy as possible and require the least amount of medical interventions. […] The nursing diagnosis for cystic fibrosis involves identifying risk factors such as airway obstruction, impaired gas exchange, or inadequate nutrition. It also includes establishing goals for improving health outcomes, such as reducing the frequency and severity of exacerbations, preventing pulmonary infections, and managing sleep disruption. […] The goal of a care plan is to identify measurable outcomes. Outcomes may include an improvement in lung function test results, increased exercise tolerance, an increased ability to cope with stress and depression, improved quality of life, and a decrease in hospitalizations.

• #141 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Cystic Fibrosis is a life-threatening disease that affects the lungs and iviscera, and causes recurrent respiratory and digestive systems. It has no known cure. The goal of caring for people with cystic fibrosis is to keep them as healthy as possible and require the least amount of medical interventions. […] The nursing diagnosis for cystic fibrosis involves identifying risk factors such as airway obstruction, impaired gas exchange, or inadequate nutrition. It also includes establishing goals for improving health outcomes, such as reducing the frequency and severity of exacerbations, preventing pulmonary infections, and managing sleep disruption. […] The goal of a care plan is to identify measurable outcomes. Outcomes may include an improvement in lung function test results, increased exercise tolerance, an increased ability to cope with stress and depression, improved quality of life, and a decrease in hospitalizations.

• #142 Cystic Fibrosis Nursing Diagnosis & Care Plan – NurseStudy.Net

  https://nursestudy.net/cystic-fibrosis-nursing-diagnosis/

  Plan activities with rest periods Rationale: Prevents excessive fatigue […] Encourage progressive exercise Rationale: Builds endurance and strength […] Monitor oxygen saturation during activity Rationale: Ensures adequate oxygenation […] The patient demonstrates improved activity tolerance […] Maintains adequate oxygenation during activities […] Participates in daily activities without excessive fatigue […] Deficient knowledge related to complex disease processes and management requirements as evidenced by questions about care and verbalization of concerns. […] Assess knowledge level Rationale: Identifies learning needs […] Provide disease education Rationale: Improves understanding and compliance […] Teach medication administration Rationale: Ensures proper treatment […] Demonstrate care techniques Rationale: Promotes skill development […] Patient verbalizes understanding of disease process. […] Demonstrates proper care techniques […] Shows improved compliance with treatment.

• #143 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Interventions for cystic fibrosis can involve medications (such as antibiotics, bronchodilators, and enzyme replacement therapy), lifestyle changes (such as avoiding contact with tobacco smoke and outdoor pollutants), non-pharmacological treatments (such as coughing and chest physiotherapy, use of a vibration platform, and dietary management), education and support, and physical and occupational therapies. […] Evaluation of the care plan is ongoing and should include ongoing assessment of the patients signs and symptoms. It should also include monitoring the patients progress toward achieving the established goals. The evaluation should include input from the patient and their family regarding the impact of treatment on their daily lives and their satisfaction with the care they receive.

• #144 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  This study revealed that nurses plan and implement interventions targeted at the adolescents’ needs in the several stages of life and disease, and also provide support to family caregivers, namely the parents. […] Results also show clear evidence on the nurse’s role as a caregiver, particularly in what concerns inhaled and intravenous medication administration, enteral and parenteral nutrition, ventilator weaning and oxygen administration. […] In this literature review, all studies refer to nursing interventions, mainly focused on communication processes, considered an important and efficient method to provide emotional and psychologic support, aiming at tailor-made care plans. […] Encouraging the involvement of family members in the therapeutic process and the support to the family as the most important promoter of the adolescent well-being is a key factor that will enable the adolescent to better adapt to the chronic disease.

• #145 Nursing care plan for cystic fibrosis

  https://nursipedia.com/nursing-care-plan-cystic-fibrosis/

  Caring for a patient with cystic fibrosis requires a multidisciplinary approach. Nurses play a crucial role in providing comprehensive care and ensuring that patients receive the most effective treatments available. A well-developed care plan is essential for ensuring that all of the patient’s needs are met. […] The goal of nursing care for cystic fibrosis is to keep the patient as healthy as possible and minimize the need for medical interventions. […] Interventions for cystic fibrosis can include medications, lifestyle modifications, non-pharmacological treatments, education and support, and physical and occupational therapies. […] The care plan is evaluated by ongoing assessment of the patient’s signs and symptoms and monitoring the patient’s progress towards achieving the established goals.

• #146 The changing face of cystic fibrosis

  https://www.myamericannurse.com/the-changing-face-of-cystic-fibrosis/

  Its no longer a childhood illness. […] Nurses should be acquainted with the underlying cause, treatments, and basic cystic fibrosis care guidelines. […] With the growing number of adults with CF and continued improvements in clinical care and prescribed therapies, nurses should be familiar with the underlying cause of CF, its treatments and basic care guidelines, and the changing face of the disease. […] When caring for patients with CF, nurses must be aware of drug-to-food and drug-to-drug interactions and treatment side effects. Individualized treatment plans are the standard of care to address specific genetic mutations. And as this patient population survives longer, nurses will encounter them in a variety of adult care settings. […] As more patients with CF are seen in adult care settings, nurses will need to learn about the disease and the model of care used to meet patient needs.

• #147 The changing face of cystic fibrosis

  https://www.myamericannurse.com/the-changing-face-of-cystic-fibrosis/

  Nurses in specialty areas such as otolaryngology, endocrinology, reproductive health, and gastroenterology may see an increased number of adults with CF and be asked to coordinate care with CF care teams. […] Because CF is no longer a pediatric disease, nurses in primary adult care and specialized fields are more likely to encounter patients with it. Nurses should partner with patients CF care teams and familiarize themselves with the CF model of care and special requirements, starting with clinical care guidelines.

• #148 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  The identification of educational needs is crucial for nursing, especially at the time of diagnosis, in genetic counselling, in the life cycle transition periods in pre and post pulmonary transplantation, hospitalization and return home, in daily life activities, re-entry in school and in the promotion of the quality of life of adolescents with cystic fibrosis and family caregivers. […] Emphasis should also be given to the nurses’ role in training these adolescents and their family members to pay special attention to feeding, nebulization, oxygen therapy, which will most likely result in benefits to the adolescent and avoid hospital readmissions. […] The nurse, as a health team member who interacts closely with the adolescent and family in the transition health-illness process, is able to establish a close relationship and offer emotional support, contributing to the autonomy of the adolescents and their family members.

• #149 Nursing interventions in monitoring the adolescent with Cystic Fibrosis: a literature review

  https://pmc.ncbi.nlm.nih.gov/articles/PMC5171783/

  Developing the potential of each individual with cystic fibrosis and advocate for the patient’s legal interests and protection is also one of the nurses’ competencies. […] The partnership of care and the identification of critical areas, such as the stigma associated with this disease, contribute to improve treatment compliance and enhance quality of life. […] The provision and management of care, the early identification of the adolescents needs, the interpersonal and therapeutic relationship established between nurses and adolescents/ families are important skills of nurses who provide care and support to this population.

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