Materiały źródłowe

• #1 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Tricuspid atresia is a congenital heart defect, occurring in two out of every 10,000 live births. Relatively rare, it accounts for about 1 to 2 percent of all cases of congenital heart disease. […] While very serious, tricuspid atresia is treatable surgically, and surgical advances have greatly improved outcomes. […] Specific treatments for tricuspid atresia depend on the associated cardiac conditions and other variables. Most newborn babies with the condition are admitted to the intensive care unit (ICU) or special care nursery. Initially, your child may be placed on oxygen or (less commonly) a ventilator to help with breathing and may be given IV (intravenous) medications to help the heart and lungs function more efficiently. […] Once your child is stabilized, your baby’s treatments will probably include:

• #2 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #3 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #4 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #5 About Tricuspid Atresia | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tricuspid-atresia.html

  Surgical repairs for tricuspid atresia aren’t a cure. […] A baby with tricuspid atresia may need surgery or other procedures soon after birth. […] Surgical treatment for tricuspid atresia depends on its severity and presence of other heart defects. Soon after birth, one or more surgeries may be needed. The surgeries will help increase blood flow to the lungs and bypass the poorly functioning right side of the heart. […] Other surgeries or procedures may be needed later. These surgeries, described below, do not cure tricuspid atresia, but they help restore heart function. […] Septostomy may be done within the first few days or weeks of a baby’s life. The procedure creates or enlarges the atrial septal defect, the hole between the right and left upper chambers (atria). This allows oxygen-poor blood to mix with oxygen-rich blood, so that more oxygen-rich blood can get to the body.

• #6 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #7 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Tricuspid atresia is a congenital heart defect, occurring in two out of every 10,000 live births. Relatively rare, it accounts for about 1 to 2 percent of all cases of congenital heart disease. […] While very serious, tricuspid atresia is treatable surgically, and surgical advances have greatly improved outcomes. […] Specific treatments for tricuspid atresia depend on the associated cardiac conditions and other variables. Most newborn babies with the condition are admitted to the intensive care unit (ICU) or special care nursery. Initially, your child may be placed on oxygen or (less commonly) a ventilator to help with breathing and may be given IV (intravenous) medications to help the heart and lungs function more efficiently. […] Once your child is stabilized, your baby’s treatments will probably include:

• #8 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #9 Tricuspid Atresia | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/tricuspid-atresia

  If your baby is born with tricuspid atresia, they will be admitted to the Evelyn and Daniel M. Tabas Cardiac Intensive Care Unit (CICU), where they will receive round-the-clock attention from a team of dedicated cardiac critical care medicine specialists. Your baby may require oxygen and a medication called prostaglandin, to keep enough oxygen in their blood. […] Prostaglandin is an IV (intravenous) medication that keeps the connection between the pulmonary artery and the aorta open. This connection, called the patent ductus arteriosus (PDA), is open in the fetus, and closes soon after birth. When the PDA closes, some babies with tricuspid atresia turn blue. An infusion of prostaglandin is a lifesaving intervention that can re-open the PDA. Not all babies with tricuspid atresia require prostaglandin.

• #10 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The initial management of the condition focuses on stabilizing the patient. The initiation of prostaglandin soon after birth is imperative in cyanotic patients with severe or critical PS or a very small VSD, relying on a ductal-dependent pulmonary blood supply. Patients presenting later in infancy with heart failure and pulmonary over-circulation may require diuretics as part of the indicated treatment. […] Due to the presence of only one functional ventricle (the left ventricle), individuals with tricuspid atresia undergo staged single ventricle palliation to ensure sufficient pulmonary and systemic blood flow, ultimately leading to the separation of these circulatory systems. The selection of the surgical approach for the initial stage of palliation depends on factors such as the anatomy of the great vessels, the presence or absence of outflow tract obstruction, and the size of any existing VSD.

• #11 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The diagnosis of tricuspid atresia with too little blood flow to the lungs or to the body needs immediate medical treatment. In a newborn baby (less than 1-2 weeks old), a medication called PGE can be given through an IV (intravenous line) to reopen the connection (ductus arteriosus) between the pulmonary artery and aorta. This improves blood flow to the lungs or body. […] Children with tricuspid atresia and too little pulmonary blood flow will need surgery to create a connection between the arteries to the body and the arteries to the lungs. This type of surgery is called a modified Blalock-Taussig-Thomas (BTT) shunt. It involves the placement of a small tube between the artery to the arm (subclavian artery) and the arteries to the lungs (pulmonary artery). Sometimes a cardiac catheterization intervention is done to place a stent in the ductus arteriosus (PDA) instead of the surgical shunt.

• #12 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #13 Tricuspid Atresia Medication: Antiarrhythmics, inotropic agents, Diuretics

  https://emedicine.medscape.com/article/158359-medication

  Digitalis and diuretics are used to control the congestive heart failure present in patients with tricuspid atresia. […] Consider digitalis to maintain sinus rhythm and improve cardiac contractility. […] Diuretics are often administered to treat and prevent pulmonary edema. […] Improve ventricular contractility and maintain normal sinus rhythm. […] Decrease circulating pulmonary blood volume.

• #14 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The initial management of the condition focuses on stabilizing the patient. The initiation of prostaglandin soon after birth is imperative in cyanotic patients with severe or critical PS or a very small VSD, relying on a ductal-dependent pulmonary blood supply. Patients presenting later in infancy with heart failure and pulmonary over-circulation may require diuretics as part of the indicated treatment. […] Due to the presence of only one functional ventricle (the left ventricle), individuals with tricuspid atresia undergo staged single ventricle palliation to ensure sufficient pulmonary and systemic blood flow, ultimately leading to the separation of these circulatory systems. The selection of the surgical approach for the initial stage of palliation depends on factors such as the anatomy of the great vessels, the presence or absence of outflow tract obstruction, and the size of any existing VSD.

• #15 Tricuspid Atresia Medication: Antiarrhythmics, inotropic agents, Diuretics

  https://emedicine.medscape.com/article/158359-medication

  Digitalis and diuretics are used to control the congestive heart failure present in patients with tricuspid atresia. […] Consider digitalis to maintain sinus rhythm and improve cardiac contractility. […] Diuretics are often administered to treat and prevent pulmonary edema. […] Improve ventricular contractility and maintain normal sinus rhythm. […] Decrease circulating pulmonary blood volume.

• #16 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  There’s no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] If your baby has tricuspid atresia, consider getting care at a medical center with surgeons and other health care providers who have experience with complex congenital heart disease. […] Medications for tricuspid atresia may be given to: Strengthen the heart muscle, Lower blood pressure, Remove excess fluid from the body. […] Supplemental oxygen might be given to help the baby breathe better. […] Before heart surgery, a baby with tricuspid atresia may be given the hormone prostaglandin to help widen and keep open the ductus arteriosus. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done.

• #17 Tricuspid atresia | Congenital Heart Defect (CHD) | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/tricuspid-atresia

  Tricuspid atresia treatment options will be determined by your child’s physician based on: […] Your child will most likely be admitted to the cardiac intensive care unit (CICU) or special care nursery once symptoms are noted. Initially, your child may be placed on oxygen, and possibly even on a ventilator, to assist his/her breathing. Intravenous (IV) medications may be given to help the heart and lungs function more efficiently. […] A cardiac catheterization procedure can be used as a diagnostic procedure, as well as initial treatment procedure for some heart defects. A cardiac catheterization procedure will usually be performed to evaluate the defect(s) and the amount of blood that is mixing. […] As part of the cardiac catheterization, a procedure called a balloon atrial septostomy may be performed to improve mixing oxygen-rich (red) blood and oxygen-poor (blue) blood.

• #18 Tricuspid Atresia Treatment & Management: Medical Care, Surgical Care, Diet and Activity

  https://emedicine.medscape.com/article/158359-treatment

  The following three considerations guide the treatment of infants with tricuspid atresia: […] The treatment of these children must be coordinated with a pediatric cardiac surgeon, pediatric cardiologist, neonatologist, and pediatric pulmonologist/intensivist. […] Promptly treat infants with severe hypoxemia with prostaglandin E infusions in order to maintain patency of the ductus arteriosus and improve pulmonary blood flow. […] The intelligent application of palliative procedures to control the amount of pulmonary blood flow in this lesion improves the survival of infants with tricuspid atresia. […] Most patients with tricuspid atresia require some form of surgical treatment during the first year of life. […] In patients with severe congestive heart failure indicative of increased pulmonary blood flow, pulmonary artery banding may be required to decrease the blood flow to the lungs and to assist with treatment of the accompanying congestive heart failure.

• #19 Tricuspid atresia | Congenital Heart Defect (CHD) | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/tricuspid-atresia

  Tricuspid atresia treatment options will be determined by your child’s physician based on: […] Your child will most likely be admitted to the cardiac intensive care unit (CICU) or special care nursery once symptoms are noted. Initially, your child may be placed on oxygen, and possibly even on a ventilator, to assist his/her breathing. Intravenous (IV) medications may be given to help the heart and lungs function more efficiently. […] A cardiac catheterization procedure can be used as a diagnostic procedure, as well as initial treatment procedure for some heart defects. A cardiac catheterization procedure will usually be performed to evaluate the defect(s) and the amount of blood that is mixing. […] As part of the cardiac catheterization, a procedure called a balloon atrial septostomy may be performed to improve mixing oxygen-rich (red) blood and oxygen-poor (blue) blood.

• #20 About Tricuspid Atresia | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tricuspid-atresia.html

  Surgical repairs for tricuspid atresia aren’t a cure. […] A baby with tricuspid atresia may need surgery or other procedures soon after birth. […] Surgical treatment for tricuspid atresia depends on its severity and presence of other heart defects. Soon after birth, one or more surgeries may be needed. The surgeries will help increase blood flow to the lungs and bypass the poorly functioning right side of the heart. […] Other surgeries or procedures may be needed later. These surgeries, described below, do not cure tricuspid atresia, but they help restore heart function. […] Septostomy may be done within the first few days or weeks of a baby’s life. The procedure creates or enlarges the atrial septal defect, the hole between the right and left upper chambers (atria). This allows oxygen-poor blood to mix with oxygen-rich blood, so that more oxygen-rich blood can get to the body.

• #21 Tricuspid Atresia | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/tricuspid-atresia

  To repair many types of single ventricle defects, including tricuspid atresia, surgeons perform a series of open-heart procedures over a period of years. This is called staged reconstruction. […] Babies who need prostaglandin to keep their oxygen levels stable will need surgery shortly after birth. The first surgery involves placing a shunt, which is a tube that connects a branch of the aorta to the pulmonary artery, taking over the job of the PDA. This surgery is called the Blalock-Taussig-Thomas (or BTT) shunt. […] Instead of having a surgical stunt, some babies may have a ductal stunt placed. This means putting a small tube (stent) into the ductus arteriosus, the blood vessel that connects the pulmonary artery to the aorta. […] The second operation, called the Glenn operation, usually happens within six months of a child’s birth. […] The third operation, called the Fontan, usually happens when a child is 18 months to 3 years old. […] Your Cardiac Center team will explain staged reconstruction to you in greater detail based on your child’s individual anatomy.

• #22 Tricuspid Atresia

  https://library.ouhealth.com/Library/Wellness/WeightControl/90,P01819

  Your child will most likely be in the intensive care unit (ICU). Early medical treatment may include: […] Medicines may be given to help the heart and lungs work better. Prostaglandin E1 may be given to keep the ductus arteriosus open. […] In some cases, cardiac cath may be used in the early period. If pulmonary stenosis is present, a catheter with a balloon at the tip can be inflated to widen the valve and let enough blood flow through. […] A special catheter with a balloon in the tip is used to create or enlarge an opening in the wall between the left and right atria (atrial septum). This helps with blood flow from the right side of the heart to the left side of the heart. […] Three surgeries, in stages, may be done. They include: […] This surgery is done on newborns. It varies, depending on the exact defect your child has. A connection (shunt) is created to let blood from the aorta reach the lungs and pick up oxygen.

• #23 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Since tricuspid atresia with an underdeveloped right ventricle is considered a single ventricle defect (where the defect results in just one fully functioning ventricle), it’s usually treated using single ventricle palliation — a staged series of three operations performed between the first few days or months and the first few years of life. […] The first stage is to optimize the blood flow to the lungs, whether it’s too much or too little. […] If the blood flow is too little, a Blalock-Taussig shunt is usually performed. […] If it’s too much, the pulmonary artery may be banded to control blood flow. […] The second operation, often performed when a child is between about 4 and 6 months old, reduces the left ventricle’s workload and sets the stage for the Fontan procedure to come. […] This final operation in the sequence, done in the first few years of life, is performed for treatment of children with various types of single ventricle defects, including tricuspid atresia. […] In some instances, your baby’s single ventricle heart can be converted into two functioning ventricles (biventricular circulation).

• #24 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Since tricuspid atresia with an underdeveloped right ventricle is considered a single ventricle defect (where the defect results in just one fully functioning ventricle), it’s usually treated using single ventricle palliation — a staged series of three operations performed between the first few days or months and the first few years of life. […] The first stage is to optimize the blood flow to the lungs, whether it’s too much or too little. […] If the blood flow is too little, a Blalock-Taussig shunt is usually performed. […] If it’s too much, the pulmonary artery may be banded to control blood flow. […] The second operation, often performed when a child is between about 4 and 6 months old, reduces the left ventricle’s workload and sets the stage for the Fontan procedure to come. […] This final operation in the sequence, done in the first few years of life, is performed for treatment of children with various types of single ventricle defects, including tricuspid atresia. […] In some instances, your baby’s single ventricle heart can be converted into two functioning ventricles (biventricular circulation).

• #25 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  For patients with pulmonary obstruction, the initial stage involves ensuring sufficient pulmonary blood flow through a systemic-to-pulmonary artery shunt, commonly achieved with a modified Blalock-Taussig (BT) shunt, also referred to as a BT-Thomas shunt. This involves creating a connection between the right subclavian and pulmonary artery, typically utilizing a polytetrafluoroethylene tubular graft. […] For patients with unobstructed pulmonary blood flow (type IC), the initial stage may involve the placement of a pulmonary artery (PA) band to regulate excessive blood flow to the pulmonary vascular bed. In a subset of cases, the VSD may be sufficiently small to naturally limit pulmonary blood flow, resulting in a balanced circulation. Therefore, pulmonary artery banding is unnecessary for these patients as they have balanced circulation and proceed to the second stage of palliation, as detailed below.

• #26 About Tricuspid Atresia | Congenital Heart Defects (CHDs) | CDC

  https://www.cdc.gov/heart-defects/about/tricuspid-atresia.html

  If the baby has other heart defects along with tricuspid atresia, there may be too much blood flowing to the lungs. Thus, not enough blood can go out to the rest of the body. […] This surgery usually is done within the first 2 weeks of a baby’s life. Surgeons create a bypass (shunt) from the aorta to the main pulmonary artery, allowing blood to get to the lungs. […] This usually is performed when an infant is 4 to 6 months of age. This procedure creates a direct connection between the main pulmonary artery and the superior vena cava. […] This procedure usually is done around 2 years of age. Doctors connect the main pulmonary artery and the inferior vena cava. After surgery, oxygen-rich and oxygen-poor blood no longer mix in the heart and an infant’s skin will no longer look bluish.

• #27 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  If there is too much pulmonary blood flow (tricuspid atresia with a large ventricular septal defect), blood flow to the lungs will need to be limited. This is done to protect the lungs from becoming damaged. This can be done by placing a band around the pulmonary artery surgically or placing flow restrictors in the pulmonary arteries by a cardiac catheterization procedure so that blood flow to the lungs is limited but controlled. […] Finally, if the problem is not enough blood flow through the aorta (tricuspid atresia with ventricular septal defect and transposition of the great arteries), blood from the normal-size left ventricle will need to be routed to the aorta. The aorta will need to be reconstructed. Pulmonary blood flow can be established by placement of a modified BTT shunt. […] Whatever surgery is needed in the newborn period, children can expect to have further heart surgery by the age of 3-6 months.

• #28 Tricuspid Atresia Repair | Norton Children’s

  https://nortonchildrens.com/services/cardiology/conditions/treatments/surgical/tricuspid-atresia-repair/

  If a child has too much blood flow to the lungs (tricuspid atresia with a large ventricular septal defect), the blood flow will need to be reduced to protect the lungs from damage. This is done by surgically placing a band around the pulmonary artery so that blood flow to the lungs is controlled. […] If the child has inadequate blood flow through the aorta (tricuspid atresia with ventricular septal defect and transposition of the great arteries), blood from the normal-size left ventricle will need to be routed to the aorta. This usually means reconstructing the aorta. This is called the Norwood procedure. Placing a modified Blalock-Taussig shunt can then create pulmonary blood flow. […] No matter which surgery is performed, children with tricuspid atresia will need more heart surgeries: Bidirectional Glenn procedure: This surgery is done when the child is 3 to 6 months old.

• #29 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The operation at 3-6 months is called a bidirectional Glenn. The superior vena cava is removed from the heart and connected directly to the pulmonary artery. The BTT shunt is removed. This allows blood from the upper body to flow directly to the lungs to pick up oxygen without having to be pumped by the heart. It also prevents blood that has oxygen from returning to the lungs. It keeps the heart from doing unnecessary work. After this surgery there is still blood returning from the body through the inferior vena cava going directly back to the body without first passing through the lungs. Because of this, some level of cyanosis will be present. […] Between the ages of 2 and 5 years, children with tricuspid atresia will be ready for the third surgery. This surgery is called the Fontan procedure. It involves connection of the inferior vena cava to the pulmonary artery. This forces all blood returning from the body to pass through the lungs and pick up oxygen before being pumped to the body. This allows a more normal color in the skin and lips due to a more normal oxygen saturation in the blood.

• #30 Tricuspid Valve Atresia | Norton Children’s Louisville, Ky.

  https://nortonchildrens.com/services/cardiology/conditions/congenital-heart-disease/tricuspid-atresia/

  No matter which surgery is performed, children with tricuspid atresia will need more heart surgeries: Bidirectional Glenn procedure: This surgery is done when the child is 3 to 6 months old. The superior vena cava, a vein carrying deoxygenated blood into the heart, is detached from the heart and connected directly to the pulmonary artery. […] Fontan procedure: The third surgery to improve blood circulation is usually done when the child is between ages 2 and 4. This procedure involves connecting the inferior vena cava directly to the pulmonary artery, forcing all blood returning from the body to pass through the lungs and pick up oxygen before being pumped back out to the body. […] The results for the three-stage surgical treatment for tricuspid atresia are generally good. Expected survival rates for children who complete all three stages of surgery are 75% to 95%, depending on the factors unique to each child and the care they receive.

• #31 Tricuspid Atresia – Adult Congenital Heart Disease | UCLA Health

  https://www.uclahealth.org/medical-services/heart/achd/conditions-treatments/tricuspid-atresia

  Not every patient with tricuspid atresia is a candidate for further surgical intervention, and some children with this heart defect may grow up with continued cyanosis, requiring specialized long-term cardiology care for their cyanotic congenital heart disease. For those that qualify for further surgery, the next operation that is routinely done in the current era of pediatric congenital heart surgery, is a bidirectional Glenn shunt, and is often performed at approximately 6-12 months of age. This consists of directly connecting the vessel draining oxygen depleted blood from the upper body to the right pulmonary artery. After this operation, the blue blood from the upper body goes to the lungs without passing through the heart, which provides the child with a more direct route of picking up oxygen from the lungs.

• #32 Tricuspid Atresia | Dayton Children’s Hospital

  https://www.childrensdayton.org/kidshealth/a/tricuspid-atresia

  Treatment for tricuspid atresia combines medicine, surgery, and cardiac catheterization to improve the flow of blood to the lungs. Replacing the tricuspid valve does not help because the right ventricle is not large enough to pump blood well. […] A medicine called prostaglandin E1 helps keep the ductus arteriosus (often called „the ductus” or PDA for patent ductus arteriosus) open. The ductus arteriosus is a normal blood vessel that connects two major arteries the aorta and the pulmonary artery that carry blood away from the heart. Keeping the ductus open in babies with tricuspid atresia improves the flow of blood to the lungs. […] These surgical steps (called the single ventricle pathway) can improve blood flow to the lungs in a baby with tricuspid atresia: At age 2 weeks or less: A Blalock-Taussig-Thomas (BTT) shunt or ductal stent redirects some of the left ventricle’s output from the body to the lungs. OR If the blood flow to the lungs is too high, as can happen with a large VSD, a band around the pulmonary artery lessens the flow to prevent lung damage. At age 4-6 months: The Glenn procedure allows blood returning from the upper part of the body to flow directly to the lungs. The BTT shunt or ductal stent is removed at the same time. At age 1.5-3 years: The Fontan procedure channels blood from the lower half of the body to the lungs so the heart pumps oxygen-rich blood to the body only. Blood returning from the body flows to the lungs before passing through the heart. […] Cardiac catheterization can make or enlarge openings in the wall between the two atria and between the two ventricles. It also can be used to place a stent (mesh tube) in the ductus to keep it open.

• #33 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The operation at 3-6 months is called a bidirectional Glenn. The superior vena cava is removed from the heart and connected directly to the pulmonary artery. The BTT shunt is removed. This allows blood from the upper body to flow directly to the lungs to pick up oxygen without having to be pumped by the heart. It also prevents blood that has oxygen from returning to the lungs. It keeps the heart from doing unnecessary work. After this surgery there is still blood returning from the body through the inferior vena cava going directly back to the body without first passing through the lungs. Because of this, some level of cyanosis will be present. […] Between the ages of 2 and 5 years, children with tricuspid atresia will be ready for the third surgery. This surgery is called the Fontan procedure. It involves connection of the inferior vena cava to the pulmonary artery. This forces all blood returning from the body to pass through the lungs and pick up oxygen before being pumped to the body. This allows a more normal color in the skin and lips due to a more normal oxygen saturation in the blood.

• #34 Tricuspid Atresia > Fact Sheets > Yale Medicine

  https://www.yalemedicine.org/conditions/tricuspid-atresia

  Stage 2: Bidirectional Glenn (BDG) Procedure. When the baby is 4 to 6 months old, doctors perform another procedure, known as the bidirectional Glenn shunt. […] Stage 3: Fontan procedure. When a patient is usually around 3 years old (though sometimes can be offered as early as 1.5 years), doctors perform a Fontan procedure to further improve blood flow throughout the body. […] If tricuspid atresia is left untreated, patients usually die within the first year of life. But patients with tricuspid atresia who undergo all three surgical procedures experience improvement in their symptoms.

• #35 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The second stage for type I and II lesions involves cavo-pulmonary anastomosis, where the superior vena cava connects to the right pulmonary artery, achieved through either the bidirectional Glenn or hemi-Fontan procedure. This modification facilitates passive blood flow from the upper body into the pulmonary vessels. This surgery is typically performed at around 6 months. […] The third stage is the Fontan procedure, which was first described in 1971 for tricuspid atresia. The original Fontan involved end-to-end anastomosis between the right atrial appendage and the proximal end of the right pulmonary artery, but the procedure has evolved significantly since then. In the current era, it involves either an extra-cardiac or intra-atrial non-valved conduit connecting the inferior vena cava to the pulmonary arteries, and this conduit may be fenestrated. Fenestration serves as a „pop-off” valve during the adjustment of the lungs to the increased blood flow from the lower body. The Fontan procedure directs total systemic venous return passively into the pulmonary vessels and is typically performed when the patient is between the ages of 2 and 3. Patients experiencing progressive ventricular dysfunction may eventually necessitate heart transplantation.

• #36 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The second stage for type I and II lesions involves cavo-pulmonary anastomosis, where the superior vena cava connects to the right pulmonary artery, achieved through either the bidirectional Glenn or hemi-Fontan procedure. This modification facilitates passive blood flow from the upper body into the pulmonary vessels. This surgery is typically performed at around 6 months. […] The third stage is the Fontan procedure, which was first described in 1971 for tricuspid atresia. The original Fontan involved end-to-end anastomosis between the right atrial appendage and the proximal end of the right pulmonary artery, but the procedure has evolved significantly since then. In the current era, it involves either an extra-cardiac or intra-atrial non-valved conduit connecting the inferior vena cava to the pulmonary arteries, and this conduit may be fenestrated. Fenestration serves as a „pop-off” valve during the adjustment of the lungs to the increased blood flow from the lower body. The Fontan procedure directs total systemic venous return passively into the pulmonary vessels and is typically performed when the patient is between the ages of 2 and 3. Patients experiencing progressive ventricular dysfunction may eventually necessitate heart transplantation.

• #37 Tricuspid Atresia – Adult Congenital Heart Disease | UCLA Health

  https://www.uclahealth.org/medical-services/heart/achd/conditions-treatments/tricuspid-atresia

  The final operation is known as the Fontan procedure, usually performed at 3-4 years of age. In this operation, oxygen depleted venous blood from the lower part of the body is connected to the pulmonary artery either via a graft through the right atrium (lateral tunnel Fontan) or via a tube graft outside the right atrium (extracardiac Fontan). The end result is that all blue blood now returns directly to the lungs, and the single left ventricle pumps only oxygenated blood to the body.

• #38 Tricuspid Valve Atresia | Norton Children’s Louisville, Ky.

  https://nortonchildrens.com/services/cardiology/conditions/congenital-heart-disease/tricuspid-atresia/

  No matter which surgery is performed, children with tricuspid atresia will need more heart surgeries: Bidirectional Glenn procedure: This surgery is done when the child is 3 to 6 months old. The superior vena cava, a vein carrying deoxygenated blood into the heart, is detached from the heart and connected directly to the pulmonary artery. […] Fontan procedure: The third surgery to improve blood circulation is usually done when the child is between ages 2 and 4. This procedure involves connecting the inferior vena cava directly to the pulmonary artery, forcing all blood returning from the body to pass through the lungs and pick up oxygen before being pumped back out to the body. […] The results for the three-stage surgical treatment for tricuspid atresia are generally good. Expected survival rates for children who complete all three stages of surgery are 75% to 95%, depending on the factors unique to each child and the care they receive.

• #39 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The second stage for type I and II lesions involves cavo-pulmonary anastomosis, where the superior vena cava connects to the right pulmonary artery, achieved through either the bidirectional Glenn or hemi-Fontan procedure. This modification facilitates passive blood flow from the upper body into the pulmonary vessels. This surgery is typically performed at around 6 months. […] The third stage is the Fontan procedure, which was first described in 1971 for tricuspid atresia. The original Fontan involved end-to-end anastomosis between the right atrial appendage and the proximal end of the right pulmonary artery, but the procedure has evolved significantly since then. In the current era, it involves either an extra-cardiac or intra-atrial non-valved conduit connecting the inferior vena cava to the pulmonary arteries, and this conduit may be fenestrated. Fenestration serves as a „pop-off” valve during the adjustment of the lungs to the increased blood flow from the lower body. The Fontan procedure directs total systemic venous return passively into the pulmonary vessels and is typically performed when the patient is between the ages of 2 and 3. Patients experiencing progressive ventricular dysfunction may eventually necessitate heart transplantation.

• #40 Tricuspid Atresia Repair | Norton Children’s

  https://nortonchildrens.com/services/cardiology/conditions/treatments/surgical/tricuspid-atresia-repair/

  If a child has too much blood flow to the lungs (tricuspid atresia with a large ventricular septal defect), the blood flow will need to be reduced to protect the lungs from damage. This is done by surgically placing a band around the pulmonary artery so that blood flow to the lungs is controlled. […] If the child has inadequate blood flow through the aorta (tricuspid atresia with ventricular septal defect and transposition of the great arteries), blood from the normal-size left ventricle will need to be routed to the aorta. This usually means reconstructing the aorta. This is called the Norwood procedure. Placing a modified Blalock-Taussig shunt can then create pulmonary blood flow. […] No matter which surgery is performed, children with tricuspid atresia will need more heart surgeries: Bidirectional Glenn procedure: This surgery is done when the child is 3 to 6 months old.

• #41 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Since tricuspid atresia with an underdeveloped right ventricle is considered a single ventricle defect (where the defect results in just one fully functioning ventricle), it’s usually treated using single ventricle palliation — a staged series of three operations performed between the first few days or months and the first few years of life. […] The first stage is to optimize the blood flow to the lungs, whether it’s too much or too little. […] If the blood flow is too little, a Blalock-Taussig shunt is usually performed. […] If it’s too much, the pulmonary artery may be banded to control blood flow. […] The second operation, often performed when a child is between about 4 and 6 months old, reduces the left ventricle’s workload and sets the stage for the Fontan procedure to come. […] This final operation in the sequence, done in the first few years of life, is performed for treatment of children with various types of single ventricle defects, including tricuspid atresia. […] In some instances, your baby’s single ventricle heart can be converted into two functioning ventricles (biventricular circulation).

• #42 Tricuspid Atresia | Treatment & Management | Point of Care

  https://www.statpearls.com/point-of-care/30595

  The second stage for type I and II lesions involves cavo-pulmonary anastomosis, where the superior vena cava connects to the right pulmonary artery, achieved through either the bidirectional Glenn or hemi-Fontan procedure. This modification facilitates passive blood flow from the upper body into the pulmonary vessels. This surgery is typically performed at around 6 months. […] The third stage is the Fontan procedure, which was first described in 1971 for tricuspid atresia. The original Fontan involved end-to-end anastomosis between the right atrial appendage and the proximal end of the right pulmonary artery, but the procedure has evolved significantly since then. In the current era, it involves either an extra-cardiac or intra-atrial non-valved conduit connecting the inferior vena cava to the pulmonary arteries, and this conduit may be fenestrated. Fenestration serves as a „pop-off” valve during the adjustment of the lungs to the increased blood flow from the lower body. The Fontan procedure directs total systemic venous return passively into the pulmonary vessels and is typically performed when the patient is between the ages of 2 and 3. Patients experiencing progressive ventricular dysfunction may eventually necessitate heart transplantation.

• #43 Tricuspid Atresia | Little Hearts Matter

  https://www.lhm.org.uk/tricuspid-atresia/

  The aim of surgical treatment is to re-route the blood through the right side of the heart, bypassing the blockages on the left side. This surgery is offered in three stages over three or more years and involves extremely high-risk, open-heart surgery. […] Heart transplantation is one of the possible treatments for single ventricle heart disease, but it is not offered as a first treatment within the United Kingdom for the following reasons; Very few donor hearts small enough for a baby are available in the United Kingdom and babies with a single ventricle heart would not survive long enough for a donor to become available. […] The MCT (Medium Chain Triglycerides) diet is a special diet which is sometimes required by children for a short period of time in hospital after heart or chest surgery or for a short period of time at home. […] A very important part of the treatment of complex congenital heart disease is the medical support given to the heart and circulation. This support will be altered as the needs of each child and young adult change as they undergo surgery and grow.

• #44 Tricuspid atresia | Congenital Heart Defect (CHD) | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/tricuspid-atresia

  An intravenous (IV) medication called prostaglandin E1 is given to keep the ductus arteriosus from closing. […] A series of operations are performed in the first two years of life that will re-route blood so that enough oxygen is added to the bloodstream to meet the child’s needs. […] Each operation is performed under general anesthesia. Types of operations include the following: […] After tricuspid atresia surgery, infants will return to the cardiac intensive care unit (CICU) to be closely monitored during the recovery period. […] Your child may need other equipment not mentioned here to provide support while in the CICU, or afterwards. […] Pain medications, such as acetaminophen or ibuprofen, may be recommended to keep your child comfortable. Your child’s physician will discuss pain control before your child is discharged from the hospital.

• #45 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Most babies with tricuspid atresia will need many heart surgeries over their lifetime. Since the right ventricle is missing, they will need single ventricle surgeries. This means that the heart can never be fully repaired. Most surgeries are successful, but your child will need cardiology care for life. […] When the surgeries happen depends on the child’s heart defect. Most children will need surgery the first week of life, the second surgery at about 6 months, and the third surgery at 3 years old. The second is called the Glenn surgery and the third is called the Fontan surgery. […] After surgery, your baby will go to the Cardiothoracic Intensive Care Unit (CTICU). They may be on a breathing machine and have many tubes, wires, and equipment to keep them stable and make sure they are okay. Members of their health care team may make changes to your baby’s medicines and breathing machine often. This will happen the most in the first 24 to 48 hours after surgery.

• #46 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #47 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #48 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #49 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #50 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #51 Tricuspid atresia | Congenital Heart Defect (CHD) | Children’s Wisconsin

  https://childrenswi.org/medical-care/herma-heart/conditions/tricuspid-atresia

  An intravenous (IV) medication called prostaglandin E1 is given to keep the ductus arteriosus from closing. […] A series of operations are performed in the first two years of life that will re-route blood so that enough oxygen is added to the bloodstream to meet the child’s needs. […] Each operation is performed under general anesthesia. Types of operations include the following: […] After tricuspid atresia surgery, infants will return to the cardiac intensive care unit (CICU) to be closely monitored during the recovery period. […] Your child may need other equipment not mentioned here to provide support while in the CICU, or afterwards. […] Pain medications, such as acetaminophen or ibuprofen, may be recommended to keep your child comfortable. Your child’s physician will discuss pain control before your child is discharged from the hospital.

• #52 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #53 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #54 Tricuspid Atresia | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/tricuspid-atresia

  Other treatments your baby will probably get after surgery are: Antibiotic medicine to prevent infection, Fluids and nutrition through an IV or PICC line, Heart medicines by IV or by mouth, Chest drainage tube, Oxygen, Pain medicines, A tube in the nose to the stomach (nasogastric [NG] tube) to keep the stomach empty, Blood transfusions, when needed. […] When your baby gets to the CTICU at Nationwide Children’s Hospital, they will have many tests. These tests include an echocardiogram and an EKG. These tests will help the team make a plan for your baby at the Heart Center Case Management Conference. This plan includes choices about surgeries, procedures, and timing.

• #55 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #56 Tricuspid atresia | Health Library | Memorial Health System

  https://www.mhsystem.org/health-library/con-20316967/

  Learn how this congenital heart defect blocks blood flow from the heart to the lungs. Treatment involves multiple surgeries. […] Tricuspid atresia is treated with multiple surgeries. Most babies with tricuspid atresia who have surgery live well into adulthood, though follow-up surgeries are often needed. […] Theres no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a childrens doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. Many children with congenital heart defects, such as tricuspid atresia, grow up to lead full lives. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #57 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #58 Tricuspid Atresia Treatment & Management: Medical Care, Surgical Care, Diet and Activity

  https://emedicine.medscape.com/article/158359-treatment

  Recurrence of the cyanosis, progressive polycythemia, decreasing exercise tolerance, shunt failure, or increasing pulmonary obstruction are indications for re-evaluation and consideration of a second operative procedure. […] A Fontan procedure is undertaken if the criteria are met; otherwise, a second palliative procedure should be performed. […] The Fontan operation excludes the right ventricle through the formation of a right atrial-to-pulmonary artery connection or an extracardiac cavopulmonary anastomosis using a synthetic graft. […] For patients who have undergone a palliative procedure, arrange careful follow-up to monitor pulmonary blood flow. […] For patients who have had the Fontan procedure, maintain follow-up care to ensure a stable cardiac rhythm.

• #59 Tricuspid atresia | Beacon Health System

  https://www.beaconhealthsystem.org/library/diseases-and-conditions/tricuspid-atresia?content_id=CON-20316967

  The short- and intermediate-term outlook for babies who have a Fontan procedure is generally promising. But regular checkups are necessary to monitor for complications, including heart failure. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions.

• #60 Children’s Heart Federation | Tricuspid Atresia

  https://chfed.org.uk/how-we-help/information-service/heart-conditions/tricuspid-atresia/

  As soon as the diagnosis is made, the baby is moved to a paediatric cardiac unit, and medicine is given to keep the Ductus Arteriosus open. […] The baby will need surgery when a few weeks or months old depending on how he or she is coping. This could mean taking an artery which normally carries blood to the arm and diverting it during an operation to the pulmonary arteries so that a larger blood supply will pick up oxygen from the lungs (a Blalock-Taussig or BT shunt). […] Further surgery will need to be carried out to improve the amount of blood picking up oxygen from the lungs. […] These are open heart surgeries the heart will need to be stopped and opened to repair it. […] The aim of the operations is to increase the amount of blood picking up oxygen from the lungs. […] Some children will need to continue on diuretic medicines to help them get rid of excess fluid. […] In some cases an anticoagulant medicine, such as aspirin or warfarin, will be prescribed. […] The length of time in hospital can be several weeks and a longer period may be needed in an intensive care or high dependency unit while the heart and lungs adjust to the different pressures.

• #61 Children’s Heart Federation | Tricuspid Atresia

  https://chfed.org.uk/how-we-help/information-service/heart-conditions/tricuspid-atresia/

  As soon as the diagnosis is made, the baby is moved to a paediatric cardiac unit, and medicine is given to keep the Ductus Arteriosus open. […] The baby will need surgery when a few weeks or months old depending on how he or she is coping. This could mean taking an artery which normally carries blood to the arm and diverting it during an operation to the pulmonary arteries so that a larger blood supply will pick up oxygen from the lungs (a Blalock-Taussig or BT shunt). […] Further surgery will need to be carried out to improve the amount of blood picking up oxygen from the lungs. […] These are open heart surgeries the heart will need to be stopped and opened to repair it. […] The aim of the operations is to increase the amount of blood picking up oxygen from the lungs. […] Some children will need to continue on diuretic medicines to help them get rid of excess fluid. […] In some cases an anticoagulant medicine, such as aspirin or warfarin, will be prescribed. […] The length of time in hospital can be several weeks and a longer period may be needed in an intensive care or high dependency unit while the heart and lungs adjust to the different pressures.

• #62 Children’s Heart Federation | Tricuspid Atresia

  https://chfed.org.uk/how-we-help/information-service/heart-conditions/tricuspid-atresia/

  As soon as the diagnosis is made, the baby is moved to a paediatric cardiac unit, and medicine is given to keep the Ductus Arteriosus open. […] The baby will need surgery when a few weeks or months old depending on how he or she is coping. This could mean taking an artery which normally carries blood to the arm and diverting it during an operation to the pulmonary arteries so that a larger blood supply will pick up oxygen from the lungs (a Blalock-Taussig or BT shunt). […] Further surgery will need to be carried out to improve the amount of blood picking up oxygen from the lungs. […] These are open heart surgeries the heart will need to be stopped and opened to repair it. […] The aim of the operations is to increase the amount of blood picking up oxygen from the lungs. […] Some children will need to continue on diuretic medicines to help them get rid of excess fluid. […] In some cases an anticoagulant medicine, such as aspirin or warfarin, will be prescribed. […] The length of time in hospital can be several weeks and a longer period may be needed in an intensive care or high dependency unit while the heart and lungs adjust to the different pressures.

• #63 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #64 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #65 Tricuspid Atresia Repair | Norton Children’s

  https://nortonchildrens.com/services/cardiology/conditions/treatments/surgical/tricuspid-atresia-repair/

  Fontan procedure: The third surgery to improve blood circulation is usually done when the child is between ages 2 and 4. […] The results for the three-stage tricuspid atresia repair surgeries are generally good. Expected survival rates for children who complete all three stages of surgery are 75% to 95%, depending on the factors unique to each child and the care they receive. […] Long-term quality of life following the Fontan operation is usually good. Currently, the oldest patients who have had this procedure are age 30 and older. However, complications can occur, including heart rhythm issues that require medication or pacemaker placement.

• #66 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #67 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #68

  https://www.pted.org/?id=tricuspidatresia5

  Tricuspid Atresia is one of the so-called Single Ventricle congenital heart diseases. […] Adult patients with these defects will usually have had a Fontan Operation. […] If these symptoms are severe, the Fontan Operation will be performed, but only if certain conditions are met: pulmonary artery pressure is acceptably low the pulmonary arteries are sufficiently well formed there is no pulmonary vascular obstructive disease (PVOD) the systemic ventricle is functioning adequately. […] The long term prognosis after the Fontan for single ventricle patients is better than for other treatments, and improvements of surgical technique continue to be made. […] Patients that had early forms of the Fontan repair are at risk for worsening heart failure, arrhythmias, and stroke.

• #69

  https://www.pted.org/?id=tricuspidatresia5

  Tricuspid Atresia is one of the so-called Single Ventricle congenital heart diseases. […] Adult patients with these defects will usually have had a Fontan Operation. […] If these symptoms are severe, the Fontan Operation will be performed, but only if certain conditions are met: pulmonary artery pressure is acceptably low the pulmonary arteries are sufficiently well formed there is no pulmonary vascular obstructive disease (PVOD) the systemic ventricle is functioning adequately. […] The long term prognosis after the Fontan for single ventricle patients is better than for other treatments, and improvements of surgical technique continue to be made. […] Patients that had early forms of the Fontan repair are at risk for worsening heart failure, arrhythmias, and stroke.

• #70 Orphanet: Tricuspid atresia

  https://www.orpha.net/en/disease/detail/1209

  The management of neonates with tricuspid atresia depends on the pulmonary blood flow. If pulmonary blood flow is high, pulmonary banding will be indicated to protect the pulmonary vascular bed. If it is reduced, prostaglandin E1 may be needed to maintain the permeability of the arterial duct before a surgical Blalock-Taussig-Thomas systemic-to-pulmonary anastomosis is performed. Rashkind maneuver may be needed if the interatrial shunt is restrictive. The second surgical stage will consist of a partial cavopulmonary connection (superior caval vein to pulmonary artery anastomosis) between 4 and 6 months of age, followed by the Fontan procedure (total cavopulmonary connection, fenestrated or not) between 2 and 4 years of age. […] Fontan procedure is a palliative surgery which does not restore a biventricular circulation. Current pooled survival estimates at 5, 10 and 15 years are 88.4%, 85.7% and 84.1% respectively. Long-term complications include left ventricular dysfunction, atrial arrhythmias, cardiac conduction disorders, thromboembolism, cirrhosis and hepatocellular carcinoma, and protein-losing enteropathy. Many of these patients will ultimately require cardiac transplantation.

• #71 Orphanet: Tricuspid atresia

  https://www.orpha.net/en/disease/detail/1209

  The management of neonates with tricuspid atresia depends on the pulmonary blood flow. If pulmonary blood flow is high, pulmonary banding will be indicated to protect the pulmonary vascular bed. If it is reduced, prostaglandin E1 may be needed to maintain the permeability of the arterial duct before a surgical Blalock-Taussig-Thomas systemic-to-pulmonary anastomosis is performed. Rashkind maneuver may be needed if the interatrial shunt is restrictive. The second surgical stage will consist of a partial cavopulmonary connection (superior caval vein to pulmonary artery anastomosis) between 4 and 6 months of age, followed by the Fontan procedure (total cavopulmonary connection, fenestrated or not) between 2 and 4 years of age. […] Fontan procedure is a palliative surgery which does not restore a biventricular circulation. Current pooled survival estimates at 5, 10 and 15 years are 88.4%, 85.7% and 84.1% respectively. Long-term complications include left ventricular dysfunction, atrial arrhythmias, cardiac conduction disorders, thromboembolism, cirrhosis and hepatocellular carcinoma, and protein-losing enteropathy. Many of these patients will ultimately require cardiac transplantation.

• #72 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #73 Orphanet: Tricuspid atresia

  https://www.orpha.net/en/disease/detail/1209

  The management of neonates with tricuspid atresia depends on the pulmonary blood flow. If pulmonary blood flow is high, pulmonary banding will be indicated to protect the pulmonary vascular bed. If it is reduced, prostaglandin E1 may be needed to maintain the permeability of the arterial duct before a surgical Blalock-Taussig-Thomas systemic-to-pulmonary anastomosis is performed. Rashkind maneuver may be needed if the interatrial shunt is restrictive. The second surgical stage will consist of a partial cavopulmonary connection (superior caval vein to pulmonary artery anastomosis) between 4 and 6 months of age, followed by the Fontan procedure (total cavopulmonary connection, fenestrated or not) between 2 and 4 years of age. […] Fontan procedure is a palliative surgery which does not restore a biventricular circulation. Current pooled survival estimates at 5, 10 and 15 years are 88.4%, 85.7% and 84.1% respectively. Long-term complications include left ventricular dysfunction, atrial arrhythmias, cardiac conduction disorders, thromboembolism, cirrhosis and hepatocellular carcinoma, and protein-losing enteropathy. Many of these patients will ultimately require cardiac transplantation.

• #74 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The results of this staged approach for children with tricuspid atresia are good. The expected survival through all three stages is 75-95% depending on the exact defects and surgery for any given person. […] The long-term quality of life following the Fontan operation is good. The oldest patients are currently in their 30s. However, several complications may occur. These include heart rhythm problems needing medication or placement of a pacemaker. Patients may also have lung problems leading to a decrease in oxygen in the blood. Digestive problems caused by loss of protein in the stool may be a concern. This may lead to swelling and water retention. For some patients, heart and lung transplantation may be needed later in life.

• #75 Tricuspid Atresia Repair | Norton Children’s

  https://nortonchildrens.com/services/cardiology/conditions/treatments/surgical/tricuspid-atresia-repair/

  Fontan procedure: The third surgery to improve blood circulation is usually done when the child is between ages 2 and 4. […] The results for the three-stage tricuspid atresia repair surgeries are generally good. Expected survival rates for children who complete all three stages of surgery are 75% to 95%, depending on the factors unique to each child and the care they receive. […] Long-term quality of life following the Fontan operation is usually good. Currently, the oldest patients who have had this procedure are age 30 and older. However, complications can occur, including heart rhythm issues that require medication or pacemaker placement.

• #76 Tricuspid atresia Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/tricuspid-atresia

  Once the diagnosis is made, the baby will often be admitted to the neonatal intensive care unit (NICU). A medicine called prostaglandin E1 may be used to keep the ductus arteriosis open (patent) so that blood can circulate to the lungs. […] Generally, patients with this condition require surgery. If the heart is unable to pump enough blood out to the lungs and rest of the body, the first surgery most often takes place within the first few days of life. In this procedure, an artificial shunt is inserted to keep blood flowing to the lungs. In some cases, this first surgery is not needed. […] Afterward, the baby goes home in most cases. The child will need to take one or more daily medicines and be closely followed by a pediatric cardiologist. This doctor will decide when the second stage of surgery should be done.

• #77 Tricuspid atresia Information | Mount Sinai – New York

  https://www.mountsinai.org/health-library/diseases-conditions/tricuspid-atresia

  Once the diagnosis is made, the baby will often be admitted to the neonatal intensive care unit (NICU). A medicine called prostaglandin E1 may be used to keep the ductus arteriosis open (patent) so that blood can circulate to the lungs. […] Generally, patients with this condition require surgery. If the heart is unable to pump enough blood out to the lungs and rest of the body, the first surgery most often takes place within the first few days of life. In this procedure, an artificial shunt is inserted to keep blood flowing to the lungs. In some cases, this first surgery is not needed. […] Afterward, the baby goes home in most cases. The child will need to take one or more daily medicines and be closely followed by a pediatric cardiologist. This doctor will decide when the second stage of surgery should be done.

• #78 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #79 Tricuspid Atresia – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/tricuspid-atresia

  In infants with excess pulmonary blood flow and signs of heart failure, a pulmonary artery band may be placed to limit pulmonary blood flow. […] The Fontan procedure involves diverting the inferior vena cava flow directly to the pulmonary artery using either a baffle created within the right atrium (lateral tunnel) or an extracardiac conduit that completely bypasses the right atrium. […] Endocarditis prophylaxis is recommended preoperatively and for at least 6 months after each surgical intervention and for as long as the patient remains cyanotic or has a residual defect adjacent to a surgical patch or prosthetic material. […] Relieve severe cyanosis during the newborn period by giving prostaglandin E1 infusion to keep the ductus arteriosus open. […] Definitive treatment requires staged operations.

• #80 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #81

  https://www.pted.org/?id=tricuspidatresia5

  Tricuspid Atresia is one of the so-called Single Ventricle congenital heart diseases. […] Adult patients with these defects will usually have had a Fontan Operation. […] If these symptoms are severe, the Fontan Operation will be performed, but only if certain conditions are met: pulmonary artery pressure is acceptably low the pulmonary arteries are sufficiently well formed there is no pulmonary vascular obstructive disease (PVOD) the systemic ventricle is functioning adequately. […] The long term prognosis after the Fontan for single ventricle patients is better than for other treatments, and improvements of surgical technique continue to be made. […] Patients that had early forms of the Fontan repair are at risk for worsening heart failure, arrhythmias, and stroke.

• #82 Orphanet: Tricuspid atresia

  https://www.orpha.net/en/disease/detail/1209

  The management of neonates with tricuspid atresia depends on the pulmonary blood flow. If pulmonary blood flow is high, pulmonary banding will be indicated to protect the pulmonary vascular bed. If it is reduced, prostaglandin E1 may be needed to maintain the permeability of the arterial duct before a surgical Blalock-Taussig-Thomas systemic-to-pulmonary anastomosis is performed. Rashkind maneuver may be needed if the interatrial shunt is restrictive. The second surgical stage will consist of a partial cavopulmonary connection (superior caval vein to pulmonary artery anastomosis) between 4 and 6 months of age, followed by the Fontan procedure (total cavopulmonary connection, fenestrated or not) between 2 and 4 years of age. […] Fontan procedure is a palliative surgery which does not restore a biventricular circulation. Current pooled survival estimates at 5, 10 and 15 years are 88.4%, 85.7% and 84.1% respectively. Long-term complications include left ventricular dysfunction, atrial arrhythmias, cardiac conduction disorders, thromboembolism, cirrhosis and hepatocellular carcinoma, and protein-losing enteropathy. Many of these patients will ultimately require cardiac transplantation.

• #83

  https://link.springer.com/article/10.1007/s11936-000-0046-6

  Untreated, the prognosis for patients with tricuspid atresia (TA) is poor. Recent advances in medical and surgical therapy, particularly the application of Fontan principle, have markedly improved the long-term outlook for children with this condition. […] Palliative procedures to normalize the pulmonary blood flow and to relieve interatrial or interventricular obstruction should be undertaken promptly. […] Staged total cavopulmonary connection to bypass the right atrium and right ventricle by an initial bidirectional Glenn procedure and followed by extracardiac conduit diversion of inferior vena caval flow into the pulmonary arteries appears to be the current procedure of choice in the surgical management of TA. […] Total cavopulmonary diversion appears to be superior to conventional Fontan-Kreutzer operations, but long-term follow-up results are needed to confirm this impression.

• #84 Tricuspid Atresia – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=tricuspid-atresia-90-P01819

  Your child will most likely be in the intensive care unit (ICU). Early medical treatment may include: […] Medicines may be given to help the heart and lungs work better. Prostaglandin E1 may be given to keep the ductus arteriosus open. […] In some cases, cardiac cath may be used in the early period. If pulmonary stenosis is present, a catheter with a balloon at the tip can be inflated to widen the valve and let enough blood flow through. This may allow the child to only need 2 surgical stages, rather than 3. […] A special catheter with a balloon in the tip is used to create or enlarge an opening in the wall between the left and right atria (atrial septum). This helps with the flow of blood from the right side of the heart to the left side of the heart. […] Three surgeries, in stages, may be done. They include:

• #85 Tricuspid Atresia | Symptoms, Diagnosis & Treatment

  https://www.cincinnatichildrens.org/health/t/tricuspid-atresia

  The diagnosis of tricuspid atresia with too little blood flow to the lungs or to the body needs immediate medical treatment. In a newborn baby (less than 1-2 weeks old), a medication called PGE can be given through an IV (intravenous line) to reopen the connection (ductus arteriosus) between the pulmonary artery and aorta. This improves blood flow to the lungs or body. […] Children with tricuspid atresia and too little pulmonary blood flow will need surgery to create a connection between the arteries to the body and the arteries to the lungs. This type of surgery is called a modified Blalock-Taussig-Thomas (BTT) shunt. It involves the placement of a small tube between the artery to the arm (subclavian artery) and the arteries to the lungs (pulmonary artery). Sometimes a cardiac catheterization intervention is done to place a stent in the ductus arteriosus (PDA) instead of the surgical shunt.

• #86 Tricuspid Atresia Repair | Norton Children’s

  https://nortonchildrens.com/services/cardiology/conditions/treatments/surgical/tricuspid-atresia-repair/

  The tricuspid atresia repair procedure chosen by the cardiothoracic surgeons at Norton Children’s Heart Institute will depend on variations around the heart’s structure — how the child’s heart has developed despite the defect. […] Tricuspid atresia repair treatment will be based on the child’s unique needs. The treatment usually includes three surgeries that take place at various ages. […] A child that has too little blood flow to the lungs or body will need immediate treatment. For a newborn (less than 1 to 2 weeks old), a medicine called prostaglandin can be given through an IV to reopen the connection between the pulmonary artery and aorta (ductus arteriosus) and improve blood flow. […] A child with too little blood flow to the lungs will need surgery to create a connection between the arteries to the body, and the arteries to the lungs. This surgery is called a modified Blalock-Taussig shunt.

• #87 Tricuspid atresia – Diagnosis & treatment – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/tricuspid-atresia/diagnosis-treatment/drc-20368416#!

  Surgeries or procedures for tricuspid atresia include open-heart surgery and minimally invasive heart surgery. The type of heart surgery depends on the specific congenital heart defect. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a children’s doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #88 Tricuspid Atresia Treatment & Management: Medical Care, Surgical Care, Diet and Activity

  https://emedicine.medscape.com/article/158359-treatment

  The following three considerations guide the treatment of infants with tricuspid atresia: […] The treatment of these children must be coordinated with a pediatric cardiac surgeon, pediatric cardiologist, neonatologist, and pediatric pulmonologist/intensivist. […] Promptly treat infants with severe hypoxemia with prostaglandin E infusions in order to maintain patency of the ductus arteriosus and improve pulmonary blood flow. […] The intelligent application of palliative procedures to control the amount of pulmonary blood flow in this lesion improves the survival of infants with tricuspid atresia. […] Most patients with tricuspid atresia require some form of surgical treatment during the first year of life. […] In patients with severe congestive heart failure indicative of increased pulmonary blood flow, pulmonary artery banding may be required to decrease the blood flow to the lungs and to assist with treatment of the accompanying congestive heart failure.

• #89 Tricuspid Atresia | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/tricuspid-atresia

  Tricuspid atresia is a congenital heart defect, occurring in two out of every 10,000 live births. Relatively rare, it accounts for about 1 to 2 percent of all cases of congenital heart disease. […] While very serious, tricuspid atresia is treatable surgically, and surgical advances have greatly improved outcomes. […] Specific treatments for tricuspid atresia depend on the associated cardiac conditions and other variables. Most newborn babies with the condition are admitted to the intensive care unit (ICU) or special care nursery. Initially, your child may be placed on oxygen or (less commonly) a ventilator to help with breathing and may be given IV (intravenous) medications to help the heart and lungs function more efficiently. […] Once your child is stabilized, your baby’s treatments will probably include:

• #90 Tricuspid atresia | Health Library | Memorial Health System

  https://www.mhsystem.org/health-library/con-20316967/

  Learn how this congenital heart defect blocks blood flow from the heart to the lungs. Treatment involves multiple surgeries. […] Tricuspid atresia is treated with multiple surgeries. Most babies with tricuspid atresia who have surgery live well into adulthood, though follow-up surgeries are often needed. […] Theres no way to replace a tricuspid valve in tricuspid atresia. If your child has tricuspid atresia, several surgeries are often done to improve blood flow through the heart and to the lungs. Medications are used to manage symptoms. […] A baby with tricuspid atresia often needs several heart surgeries or procedures. Some of them are temporary fixes to quickly improve blood flow before a more permanent procedure can be done. […] After treatment, babies with tricuspid atresia need regular health checkups, ideally with a childrens doctor trained in congenital heart conditions. This care provider is called a pediatric congenital cardiologist. Many children with congenital heart defects, such as tricuspid atresia, grow up to lead full lives. […] Adults treated for tricuspid atresia also need lifelong checkups, preferably with a doctor trained in adult congenital heart conditions. This care provider is called an adult congenital cardiologist.

• #91 Tricuspid Atresia

  https://library.ouhealth.com/Library/Wellness/WeightControl/90,P01819

  This surgery may be done on babies ages 2 to 6 months. A new connection (shunt) replaces the first shunt. This shunt connects the large blood vessel from the top of the body to the heart (superior vena cava) to the pulmonary artery. This allows blood to get to the lungs for oxygen. […] This surgery may be done from ages 2 to 3. A second connection (shunt) is made. It allows blood from the large blood vessel from the lower part of the body to the heart to flow to the pulmonary artery. This surgery varies depending on the exact defect, as well as other factors. […] Your child will need medicines and a series of surgeries to allow oxygen-rich (red) blood to be pumped to the body. […] Your child will need to be followed by a specialist in congenital heart conditions throughout their life.

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