Materiały źródłowe

• #1 Double Outlet Right Ventricle (DORV) | Rady Children’s Hospital

  https://www.rchsd.org/health-article/double-outlet-right-ventricle-dorv/

  DORV is due to an error in the way the heart forms very early in pregnancy. Why this happens is unknown. It isnt caused by anything a mother did or didnt do during her pregnancy. Doctors and scientists have not yet found a way to prevent DORV. […] Surgery is needed to correct DORV. Medicines might help the heart work better, but a baby with DORV cannot get better for long without surgery. […] In very rare cases, surgical repair isnt possible and a heart transplant may be recommended.

• #2 Double Outlet Right Ventricle (DORV) | Dayton Children’s Hospital

  https://www.childrensdayton.org/kidshealth/a/dorv

  DORV is due to an error in the way the heart forms very early in pregnancy. In most cases, this happens with no known cause, and isn’t due to anything a mother did or didn’t do during her pregnancy. Doctors and scientists have not yet found a way to prevent DORV. […] Surgery is needed to correct DORV. Medicines might help the heart work better, but a baby with DORV cannot get better for long without surgery. […] In very rare cases, surgical repair isn’t possible and a heart transplant may be recommended.

• #3 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Because researchers are still trying to understand DORVs cause, you cant prevent it. You shouldnt blame yourself, though. You didnt make this happen. […] Without surgery, a baby with double outlet right ventricle will eventually develop: Cyanosis. Heart failure. Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. Anyone whos had surgery for DORV needs lifelong care from a cardiologist or provider who specializes in taking care of your heart.

• #4 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Genetic counseling and testing is recommended for all women pregnant with a baby with DORV. […] Surgery is required to correct double outlet right ventricle, enabling blood to flow normally out of the heart to the body and lungs. […] The timing and type of surgery depends on each baby’s defect, other heart abnormalities, and overall health. If symptoms are severe, the surgery may be performed the first few days after birth. In complex cases, a series of surgeries may be required. […] Babies born with DORV will need to continue to see a heart specialist throughout their lives, transitioning at adulthood to a cardiologist who specializes in the treatment of adults with congenital heart defects.

• #5 Double Outlet Right Ventricle (DORV) | Rady Children’s Hospital

  https://www.rchsd.org/health-article/double-outlet-right-ventricle-dorv/

  DORV is due to an error in the way the heart forms very early in pregnancy. Why this happens is unknown. It isnt caused by anything a mother did or didnt do during her pregnancy. Doctors and scientists have not yet found a way to prevent DORV. […] Surgery is needed to correct DORV. Medicines might help the heart work better, but a baby with DORV cannot get better for long without surgery. […] In very rare cases, surgical repair isnt possible and a heart transplant may be recommended.

• #6 Double-Outlet Right Ventricle – DORV

  https://www.isuog.org/clinical-resources/patient-information-series/patient-information-pregnancy-conditions/heart/double-outlet-right-ventricle-dorv.html

  DORV is often an abnormality that arises without a clear cause. […] Poorly controlled diabetes mellitus in early pregnancy can be associated with an increased chance of DORV. […] If you have Diabetes Mellitus, your blood sugar should be well-controlled before planning to get pregnant.

• #7 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Genetic counseling and testing is recommended for all women pregnant with a baby with DORV. […] Surgery is required to correct double outlet right ventricle, enabling blood to flow normally out of the heart to the body and lungs. […] The timing and type of surgery depends on each baby’s defect, other heart abnormalities, and overall health. If symptoms are severe, the surgery may be performed the first few days after birth. In complex cases, a series of surgeries may be required. […] Babies born with DORV will need to continue to see a heart specialist throughout their lives, transitioning at adulthood to a cardiologist who specializes in the treatment of adults with congenital heart defects.

• #8 Double Outlet Right Ventricle | Mount Sinai – New York

  https://www.mountsinai.org/locations/childrens-heart/conditions/double-outlet-right-ventricle

  If your child has a diagnosis of double outlet right ventricle (DORV), you will want to know as much as possible about the problem—and the solution. And you want to know as quickly as possible. […] Our Fetal Heart Program specialists can diagnose double outlet right ventricle before your baby is born. When we detect the condition during pregnancy, our doctors will monitor mother and baby throughout the pregnancy. Your dedicated team of specialists will explain how we can help you and will develop a plan for your baby’s birth and afterward. […] To treat DORV, we may need to surgically close the ventricular septal defect (VSD) and correct blood flow—from the left ventricle into the aorta and from the right ventricle into the pulmonary artery. The approach your child’s surgeon uses depends on the specific anatomy of your child’s DORV. […] Patients with DORV require lifelong follow-up care, and the Children’s Heart Center is here for your child.

• #9 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Because researchers are still trying to understand DORVs cause, you cant prevent it. You shouldnt blame yourself, though. You didnt make this happen. […] Without surgery, a baby with double outlet right ventricle will eventually develop: Cyanosis. Heart failure. Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. Anyone whos had surgery for DORV needs lifelong care from a cardiologist or provider who specializes in taking care of your heart.

• #10

  https://journals.lww.com/cmj/fulltext/2017/02200/surgical_treatment_of_double_outlet_right.6.aspx

  Double outlet right ventricle (DORV) is a group of complex congenital heart abnormalities. Preoperative pulmonary hypertension (PH) is considered an important risk factor for early death during the surgical treatment of DORV. […] Preoperative PH was concerned as an important risk factor for early deaths in the surgical treatment of DORV. […] Therefore, once the diagnosis is confirmed, surgical treatment should be considered. […] It is generally considered that these patients often develop significant congestive heart failure due to a large left-to-right shunt, and surgical repair should be carried out in the first several months of life. […] Overall, infants and children in this study had a significant reduction in PH after surgery. However, the decline was not significant for a few infants 1 year old, which may be related to hypoplastic development of the pulmonary vascular bed.

• #11 Double Outlet Right Ventricle With Transposition Treatment & Management: Medical Care, Surgical Care, Consultations

  https://emedicine.medscape.com/article/896082-treatment

  Medical management to control congestive heart failure (CHF) and improve the patient’s condition prior to surgery should be instituted. […] In addition, observe subacute bacterial endocarditis prophylaxis. […] Lifelong antibiotic prophylaxis is necessary prior to any potentially contaminated procedure, especially dental work.

• #12 Double Outlet Right Ventricle | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/double-outlet-right-ventricle

  DORV requires open heart surgery. Medication may also be necessary early on to help the heart function better before and after surgical intervention. […] Your Cardiac Center team at Children’s Hospital of Philadelphia (CHOP) will explain your child’s heart defect to you in detail. […] Follow-up care for double outlet right ventricle depends on the type of surgical procedure that was performed, and whether additional surgeries are expected to be needed throughout the child’s life. Regardless, children who were born with double outlet right ventricle must continue to see a pediatric cardiologist regularly. […] Children with complex congenital heart defects who have had open heart surgery as infants are at a higher risk for neurodevelopmental issues when compared to children without congenital heart defects. CHOP’s Cardiac Kids Development Follow-up Program provides evaluation, screening and clinical care for children with complex congenital heart disease who are at risk for neurodevelopmental problems.

• #13 Double Outlet Right Ventricle | Loma Linda University Children’s Health

  https://lluch.org/conditions/double-outlet-right-ventricle

  DORV can be treated with surgery. Surgery can correct blood flow so that it moves the right way from the left ventricle to the aorta and from the right ventricle to the pulmonary artery. Surgery is also needed to fix the defect in the ventricular wall. […] Some children with DORV also need medicine. That may especially be the case if they haven’t yet had surgery and they have symptoms of heart failure. Treatment will vary based on the type of DORV and the severity of symptoms. […] Children with heart abnormalities like DORV are also at higher risk for infection of the heart valves. To prevent it, your child’s healthcare provider might prescribe antibiotics before and after certain medical and dental procedures.

• #14

  https://journals.lww.com/cmj/fulltext/2017/02200/surgical_treatment_of_double_outlet_right.6.aspx

  Double outlet right ventricle (DORV) is a group of complex congenital heart abnormalities. Preoperative pulmonary hypertension (PH) is considered an important risk factor for early death during the surgical treatment of DORV. […] Preoperative PH was concerned as an important risk factor for early deaths in the surgical treatment of DORV. […] Therefore, once the diagnosis is confirmed, surgical treatment should be considered. […] It is generally considered that these patients often develop significant congestive heart failure due to a large left-to-right shunt, and surgical repair should be carried out in the first several months of life. […] Overall, infants and children in this study had a significant reduction in PH after surgery. However, the decline was not significant for a few infants 1 year old, which may be related to hypoplastic development of the pulmonary vascular bed.

• #15 Double outlet right ventricle

  https://adamcertificationdemo.adam.com/content.aspx?productid=142&pid=1&gid=007328

  Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The aorta connects to the right ventricle (RV, the chamber of the heart that pumps oxygen-poor blood to the lungs), instead of to the left ventricle (LV, the chamber that normally pumps oxygen-rich blood to the body). […] Treatment requires surgery to close the hole in the heart and direct blood from the left ventricle into the aorta. Surgery may also be needed to move the pulmonary artery or aorta. […] Children with this heart condition may need to take antibiotics before surgeries or dental treatments. This prevents infections in the heart.

• #16 Double Outlet Right Ventricle | Loma Linda University Children’s Health

  https://lluch.org/conditions/double-outlet-right-ventricle

  DORV can be treated with surgery. Surgery can correct blood flow so that it moves the right way from the left ventricle to the aorta and from the right ventricle to the pulmonary artery. Surgery is also needed to fix the defect in the ventricular wall. […] Some children with DORV also need medicine. That may especially be the case if they haven’t yet had surgery and they have symptoms of heart failure. Treatment will vary based on the type of DORV and the severity of symptoms. […] Children with heart abnormalities like DORV are also at higher risk for infection of the heart valves. To prevent it, your child’s healthcare provider might prescribe antibiotics before and after certain medical and dental procedures.

• #17

  https://link.springer.com/article/10.1007/s11936-005-0022-2

  In the current era of superb surgical results for congenital heart disease, several management options are available for patients born with double outlet right ventricle (DORV). […] The surgical repair of DORV is tailored to address the variety of abnormalities associated with this lesion. […] For patients with subaortic or doubly committed VSDs, without right ventricular outflow tract obstruction, the usual repair is an intraventricular tunnel from the VSD to the aorta. […] If right ventricular outflow tract obstruction exists, then augmentation of the right ventricular outflow tract or conduit placement from the right ventricle to the pulmonary artery is necessary. […] For the Taussig-Bing anomaly (subpulmonary VSD) an arterial switch operation is indicated with tunneling of the VSD to the neoaorta.

• #18

  https://link.springer.com/article/10.1007/s11936-005-0022-2

  For patients with a remote VSD, complex atrioventricular valve abnormalities, or unbalanced ventricles, a staged palliative approach is warranted. […] Outcomes are determined by the surgery performed. […] Patients who require conduit placement from right ventricle to pulmonary artery will need subsequent surgery for replacement of the conduit. […] Complex intraventricular tunnels are at risk for developing subaortic obstruction. […] Patients who had arterial switch operations have thus far had excellent results. […] However, these patients may be at risk for development of neoaortic valve regurgitation requiring subsequent reoperation. […] Complex biventricular intracardiac repairs have been associated with a higher risk of reoperation. […] In the past 10 to 15 years, patients undergoing Fontan operations have had improved early and late survival. […] However, long-term problems after the Fontan operation include arrhythmia and development of protein-losing enteropathy.

• #19

  https://journals.lww.com/cmj/fulltext/2017/02200/surgical_treatment_of_double_outlet_right.6.aspx

  The suture technique used in intracardiac channel repair of VSD type DORV should be sufficient to prevent residual shunt formation. […] Mustard or Senning surgical techniques are generally safe because of their relative simplicity. […] The postoperative management of these patients is very important. Routine use of inhaled nitric oxide and prostaglandins is helpful.

• #20 Double Outlet Right Ventricle With Transposition Treatment & Management: Medical Care, Surgical Care, Consultations

  https://emedicine.medscape.com/article/896082-treatment

  Medical management to control congestive heart failure (CHF) and improve the patient’s condition prior to surgery should be instituted. […] In addition, observe subacute bacterial endocarditis prophylaxis. […] Lifelong antibiotic prophylaxis is necessary prior to any potentially contaminated procedure, especially dental work.

• #21 Double outlet right ventricle

  https://adamcertificationdemo.adam.com/content.aspx?productid=142&pid=1&gid=007328

  Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The aorta connects to the right ventricle (RV, the chamber of the heart that pumps oxygen-poor blood to the lungs), instead of to the left ventricle (LV, the chamber that normally pumps oxygen-rich blood to the body). […] Treatment requires surgery to close the hole in the heart and direct blood from the left ventricle into the aorta. Surgery may also be needed to move the pulmonary artery or aorta. […] Children with this heart condition may need to take antibiotics before surgeries or dental treatments. This prevents infections in the heart.

• #22 Double Outlet Right Ventricle | Loma Linda University Children’s Health

  https://lluch.org/conditions/double-outlet-right-ventricle

  DORV can be treated with surgery. Surgery can correct blood flow so that it moves the right way from the left ventricle to the aorta and from the right ventricle to the pulmonary artery. Surgery is also needed to fix the defect in the ventricular wall. […] Some children with DORV also need medicine. That may especially be the case if they haven’t yet had surgery and they have symptoms of heart failure. Treatment will vary based on the type of DORV and the severity of symptoms. […] Children with heart abnormalities like DORV are also at higher risk for infection of the heart valves. To prevent it, your child’s healthcare provider might prescribe antibiotics before and after certain medical and dental procedures.

• #23

  https://www.pted.org/?id=doubleoutlet4

  Most patients, regardless of repair, will require life-long medication to guard against endocarditis (cardiac inflammation) if cyanotic. […] Life-long medical monitoring, including the prescription of antibiotics to guard against endocarditis (infection of the heart’s internal lining), will be necessary for all single ventricle patients. […] All patients after a Fontan repair require anticoagulation therapy with at least aspirin or Coumadin.

• #24 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Because researchers are still trying to understand DORVs cause, you cant prevent it. You shouldnt blame yourself, though. You didnt make this happen. […] Without surgery, a baby with double outlet right ventricle will eventually develop: Cyanosis. Heart failure. Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. Anyone whos had surgery for DORV needs lifelong care from a cardiologist or provider who specializes in taking care of your heart.

• #25 Double Outlet Right Ventricle | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/double-outlet-right-ventricle

  DORV requires open heart surgery. Medication may also be necessary early on to help the heart function better before and after surgical intervention. […] Your Cardiac Center team at Children’s Hospital of Philadelphia (CHOP) will explain your child’s heart defect to you in detail. […] Follow-up care for double outlet right ventricle depends on the type of surgical procedure that was performed, and whether additional surgeries are expected to be needed throughout the child’s life. Regardless, children who were born with double outlet right ventricle must continue to see a pediatric cardiologist regularly. […] Children with complex congenital heart defects who have had open heart surgery as infants are at a higher risk for neurodevelopmental issues when compared to children without congenital heart defects. CHOP’s Cardiac Kids Development Follow-up Program provides evaluation, screening and clinical care for children with complex congenital heart disease who are at risk for neurodevelopmental problems.

• #26 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Genetic counseling and testing is recommended for all women pregnant with a baby with DORV. […] Surgery is required to correct double outlet right ventricle, enabling blood to flow normally out of the heart to the body and lungs. […] The timing and type of surgery depends on each baby’s defect, other heart abnormalities, and overall health. If symptoms are severe, the surgery may be performed the first few days after birth. In complex cases, a series of surgeries may be required. […] Babies born with DORV will need to continue to see a heart specialist throughout their lives, transitioning at adulthood to a cardiologist who specializes in the treatment of adults with congenital heart defects.

• #27 Double Outlet Right Ventricle | Mount Sinai – New York

  https://www.mountsinai.org/locations/childrens-heart/conditions/double-outlet-right-ventricle

  If your child has a diagnosis of double outlet right ventricle (DORV), you will want to know as much as possible about the problem—and the solution. And you want to know as quickly as possible. […] Our Fetal Heart Program specialists can diagnose double outlet right ventricle before your baby is born. When we detect the condition during pregnancy, our doctors will monitor mother and baby throughout the pregnancy. Your dedicated team of specialists will explain how we can help you and will develop a plan for your baby’s birth and afterward. […] To treat DORV, we may need to surgically close the ventricular septal defect (VSD) and correct blood flow—from the left ventricle into the aorta and from the right ventricle into the pulmonary artery. The approach your child’s surgeon uses depends on the specific anatomy of your child’s DORV. […] Patients with DORV require lifelong follow-up care, and the Children’s Heart Center is here for your child.

• #28 Double Outlet Right Ventricle | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/double-outlet-right-ventricle

  DORV requires open heart surgery. Medication may also be necessary early on to help the heart function better before and after surgical intervention. […] Your Cardiac Center team at Children’s Hospital of Philadelphia (CHOP) will explain your child’s heart defect to you in detail. […] Follow-up care for double outlet right ventricle depends on the type of surgical procedure that was performed, and whether additional surgeries are expected to be needed throughout the child’s life. Regardless, children who were born with double outlet right ventricle must continue to see a pediatric cardiologist regularly. […] Children with complex congenital heart defects who have had open heart surgery as infants are at a higher risk for neurodevelopmental issues when compared to children without congenital heart defects. CHOP’s Cardiac Kids Development Follow-up Program provides evaluation, screening and clinical care for children with complex congenital heart disease who are at risk for neurodevelopmental problems.

• #29

  https://link.springer.com/article/10.1007/s11936-005-0022-2

  For patients with a remote VSD, complex atrioventricular valve abnormalities, or unbalanced ventricles, a staged palliative approach is warranted. […] Outcomes are determined by the surgery performed. […] Patients who require conduit placement from right ventricle to pulmonary artery will need subsequent surgery for replacement of the conduit. […] Complex intraventricular tunnels are at risk for developing subaortic obstruction. […] Patients who had arterial switch operations have thus far had excellent results. […] However, these patients may be at risk for development of neoaortic valve regurgitation requiring subsequent reoperation. […] Complex biventricular intracardiac repairs have been associated with a higher risk of reoperation. […] In the past 10 to 15 years, patients undergoing Fontan operations have had improved early and late survival. […] However, long-term problems after the Fontan operation include arrhythmia and development of protein-losing enteropathy.

• #30

  https://link.springer.com/article/10.1007/s11936-005-0022-2

  For patients with a remote VSD, complex atrioventricular valve abnormalities, or unbalanced ventricles, a staged palliative approach is warranted. […] Outcomes are determined by the surgery performed. […] Patients who require conduit placement from right ventricle to pulmonary artery will need subsequent surgery for replacement of the conduit. […] Complex intraventricular tunnels are at risk for developing subaortic obstruction. […] Patients who had arterial switch operations have thus far had excellent results. […] However, these patients may be at risk for development of neoaortic valve regurgitation requiring subsequent reoperation. […] Complex biventricular intracardiac repairs have been associated with a higher risk of reoperation. […] In the past 10 to 15 years, patients undergoing Fontan operations have had improved early and late survival. […] However, long-term problems after the Fontan operation include arrhythmia and development of protein-losing enteropathy.

• #31 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Because researchers are still trying to understand DORVs cause, you cant prevent it. You shouldnt blame yourself, though. You didnt make this happen. […] Without surgery, a baby with double outlet right ventricle will eventually develop: Cyanosis. Heart failure. Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. Anyone whos had surgery for DORV needs lifelong care from a cardiologist or provider who specializes in taking care of your heart.

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