Materiały źródłowe

• #1 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #2 Double Outlet Right Ventricle | The Texas Heart Institute®

  https://www.texasheart.org/heart-health/heart-information-center/topics/double-outlet-right-ventricle/

  Double outlet right ventricle (DORV) is a rare form of congenital heart disease. […] Infants born with DORV usually have a ventricular septal defect (VSD). […] Where the VSD is located will determine the signs and symptoms of DORV. The most common signs and symptoms of DORV may not appear for days or weeks after birth. […] Shortness of breath […] Heart murmur […] Sweating […] Extreme tiredness […] Fast or difficult breathing […] A bluish color to the skin (cyanosis) […] No interest in feeding […] Loss of weight or no weight gain.

• #3 Double Outlet Right Ventricle (DORV) | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/dorv

  Common symptoms of double outlet right ventricle (DORV) in babies include: Rapid breathing, Rapid heartbeat, Sweating, Disinterest in feeding or tiring while feeding, Poor weight gain, Blue color of the skin, lips, and nail beds (cyanosis), Heart murmur (detected by doctor) […] In older children, symptoms may include: Fatigue, Shortness of breath.

• #4 Double Outlet Right Ventricle (DORV) | Connecticut Children’s

  https://www.connecticutchildrens.org/specialties-conditions/cardiology/conditions/double-outlet-right-ventricle-dorv

  DORV is often detected before birth, or in the first few days after a baby is born. Symptoms include: […] Bluish or grayish lips, skin and nails […] Fast breathing […] Sweating or clammy skin […] Trouble feeding […] Poor weight gain […] Extreme sleepiness.

• #5 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #6 Double-outlet right ventricle – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/double-outlet-right-ventricle/cdc-20389537

  In double-outlet right ventricle, the lower right heart chamber, called the right ventricle, has two openings for blood to exit instead of one. Some blood goes to the body instead of just the lungs. There also is a hole between the two lower heart chambers. The hole is called a ventricular septal defect. […] Babies with double-outlet right ventricle also have a hole between the lower heart chambers. The lower heart chambers are called the ventricles. The hole is called a ventricular septal defect. The hole causes oxygen-rich blood to mix with oxygen-poor blood. Babies with this hole may not get enough oxygen in the bloodstream. Their skin may appear gray or blue. […] Symptoms of double-outlet right ventricle may include: Pale gray or blue lips, tongue, or fingernails. Depending on skin color, these changes may be harder or easier to see. Rapid breathing. Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #7 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #8 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Newborns with DORV typically show signs of the condition within a few days of birth. […] While the signs and symptoms can vary for each baby, in general they may include: Rapid breathing or difficulty breathing, Heart murmur, Rapid heartbeat, Sweating, Extreme tiredness, A blue tint to the skin, lips or nails (cyanosis), due to lack of oxygen in the blood, No interest in feeding, Weight loss or poor weight gain. […] In babies with DORV, the heart has to work harder than normal to pump enough oxygenated blood out into the body, which can cause the heart to become enlarged. Too much blood may also be pumped to the baby’s lungs. […] Without treatment, risks include high blood pressure and heart failure.

• #9 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #10 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #11 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #12 Double outlet right ventricle | Lima Memorial Health System

  https://www.limamemorial.org/health-library/hie%20multimedia-textonly/1/007328

  Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The symptoms and severity of the problem will depend on the type of DORV. […] Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing.

• #13 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #14 Double outlet right ventricle | Lima Memorial Health System

  https://www.limamemorial.org/health-library/hie%20multimedia-textonly/1/007328

  Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The symptoms and severity of the problem will depend on the type of DORV. […] Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing.

• #15 Double Outlet Right Ventricle (DORV) | Boston Children’s Hospital

  https://www.childrenshospital.org/conditions/dorv

  Common symptoms of double outlet right ventricle (DORV) in babies include: Rapid breathing, Rapid heartbeat, Sweating, Disinterest in feeding or tiring while feeding, Poor weight gain, Blue color of the skin, lips, and nail beds (cyanosis), Heart murmur (detected by doctor) […] In older children, symptoms may include: Fatigue, Shortness of breath.

• #16 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Newborns with DORV typically show signs of the condition within a few days of birth. […] While the signs and symptoms can vary for each baby, in general they may include: Rapid breathing or difficulty breathing, Heart murmur, Rapid heartbeat, Sweating, Extreme tiredness, A blue tint to the skin, lips or nails (cyanosis), due to lack of oxygen in the blood, No interest in feeding, Weight loss or poor weight gain. […] In babies with DORV, the heart has to work harder than normal to pump enough oxygenated blood out into the body, which can cause the heart to become enlarged. Too much blood may also be pumped to the baby’s lungs. […] Without treatment, risks include high blood pressure and heart failure.

• #17 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #18 Double-outlet right ventricle – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/double-outlet-right-ventricle/cdc-20389537

  In double-outlet right ventricle, the lower right heart chamber, called the right ventricle, has two openings for blood to exit instead of one. Some blood goes to the body instead of just the lungs. There also is a hole between the two lower heart chambers. The hole is called a ventricular septal defect. […] Babies with double-outlet right ventricle also have a hole between the lower heart chambers. The lower heart chambers are called the ventricles. The hole is called a ventricular septal defect. The hole causes oxygen-rich blood to mix with oxygen-poor blood. Babies with this hole may not get enough oxygen in the bloodstream. Their skin may appear gray or blue. […] Symptoms of double-outlet right ventricle may include: Pale gray or blue lips, tongue, or fingernails. Depending on skin color, these changes may be harder or easier to see. Rapid breathing. Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #19 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #20 Double Outlet Right Ventricle Treatment: Symptoms & Causes Explained – The Kingsley Clinic

  https://thekingsleyclinic.com/resources/double-outlet-right-ventricle-treatment-symptoms-causes-explained/

  Cyanosis is observed in approximately 70-90% of patients with Double Outlet Right Ventricle (DORV). It is often one of the earliest and most noticeable symptoms, particularly in newborns and infants. […] Difficulty breathing, or dyspnea, is reported in about 60-80% of DORV patients, particularly during infancy and early childhood. […] Poor feeding is present in approximately 50-70% of infants with DORV. […] Fatigue is observed in nearly 60-80% of individuals with DORV, particularly during infancy and childhood. […] A rapid heartbeat, or tachycardia, is seen in around 50-70% of DORV patients. […] Clubbing of the fingers occurs in approximately 30-50% of patients with chronic cyanosis due to DORV. […] A heart murmur is detected in nearly 100% of DORV cases during a physical exam. […] Failure to thrive is reported in about 40-60% of infants with DORV. […] Excessive sweating, or diaphoresis, is seen in approximately 50-70% of DORV patients, particularly during feeding or physical activity. […] Irritability is observed in about 40-60% of infants and young children with DORV.

• #21 Double Outlet Right Ventricle Surgery: Background, Problem, Relevant Anatomy

  https://emedicine.medscape.com/article/904397-overview

  Double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. […] The clinical presentation can vary from one of profound cyanosis to that of fulminant congestive heart failure. As a result, management and surgical repair of the defect are based on correcting the specific combination of anatomic defects with their radically different pathophysiologies. […] The severity or lack of pulmonary stenosis largely determines the spectrum of symptoms and the patient’s age at the time of clinical presentation. In general, most patients present during the neonatal period. Patients with severe pulmonary stenosis have cyanosis, and those with uncontrolled pulmonary blood flow present with congestive heart failure.

• #22 Double Outlet Right Ventricle – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/double-outlet-right-ventricle

  The clinical manifestations of DORV range from severe cyanosis (with the Taussig-Bing anomaly or any VSD type with pulmonary stenosis) to congestive heart failure and pulmonary hypertension (with a subaortic VSD and no pulmonary outflow obstruction). […] Physical examination may reveal a single loud second heart sound (S2) with pulmonary hypertension, a systolic ejection murmur at the base due to pulmonary stenosis, cyanosis with clubbing, and, if a coarctation is present, decreased femoral pulses. […] During the newborn period, prostaglandins may be needed for severe cyanosis if critical pulmonary stenosis is present. If pulmonary blood flow is greatly increased, heart failure treatment is required. However, surgical intervention is invariably required.

• #23 Double Outlet Right Ventricle (DORV) (for Parents) – Humana – Kentucky

  https://kidshealth.org/HumanaKentucky/en/parents/dorv.html

  Babies born with DORV almost always show signs of the problem within a few days of birth. […] Within a few days of birth, a newborn with DORV usually will show these signs: breathing fast or hard, pale or bluish skin (cyanosis), sweating, poor feeding with little weight gain, excessive sleepiness. […] The position and size of the VSD and the positions of the pulmonary artery and aorta are different for each baby. So some babies with DORV have more severe symptoms than others.

• #24 Double outlet right ventricle (DORV) | Norton Children’s Louisville, Ky.

  https://nortonchildrens.com/services/cardiology/conditions/congenital-heart-disease/double-outlet-right-ventricle/

  Double outlet right ventricle (DORV) is a congenital heart defect that causes the aorta to be connected to the heart in the wrong place. […] Babies born with DORV almost always show signs of the issue within a few days of birth. Surgery is needed to correct it. […] In a baby with DORV, oxygen-rich blood from the lungs returns to the left ventricle but can’t leave through the aorta as it does in a healthy heart. The blood is forced through the hole — the ventricular septal defect — where it mixes with the oxygen-poor blood returning from the body in the right ventricle. […] The position and size of the VSD and the positions of the pulmonary artery and aorta are different for each baby. Some babies with DORV have more severe symptoms than others. […] Within a few days of birth, a newborn with DORV usually will show these signs: Breathing fast or hard, Pale or bluish skin, Sweating, Poor feeding with little weight gain, Sleepiness.

• #25 Double outlet right ventricle – UF Health

  https://ufhealth.org/conditions-and-treatments/double-outlet-right-ventricle

  Double outlet right ventricle (DORV) is a congenital heart disease in which the aorta and pulmonary artery rise from the right ventricle. This configuration allows oxygen-poor blood, to be carried throughout the body. The body is not able to get enough oxygen, causing the heart to work harder to try to bring more oxygen-rich blood to the body. […] Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips, Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring, Sweating, Swollen legs or abdomen, Trouble breathing. […] The symptoms and severity of the problem will depend on the type of DORV. The presence of pulmonary valve stenosis also affects the condition.

• #26 Double Outlet Right Ventricle (DORV) – Diagnosis and Treatment

  https://angolodeldottorino.it/en/Medicine/Cardiology/Congenital_Heart_Diseases/Double_Outlet_Right_Ventricle.php

  Symptoms vary depending on the anatomical type of DORV: […] Newborns with pulmonary stenosis: early cyanosis and signs of hypoxemia. […] Newborns with increased pulmonary blood flow: signs of heart failure, tachypnea, and excessive sweating. […] Heart murmur: present in most patients, with variable intensity. […] The prognosis depends on the anatomical configuration and the success of surgical correction. Without treatment, survival is limited. With proper surgical intervention, long-term quality of life is generally good. Major complications include valvular dysfunction, residual stenosis, and arrhythmias.

• #27 Double outlet right ventricle

  https://adamcertificationdemo.adam.com/content.aspx?productid=142&pid=1&gid=007328

  Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing. […] Treatment requires surgery to close the hole in the heart and direct blood from the left ventricle into the aorta. Surgery may also be needed to move the pulmonary artery or aorta. […] How well the baby does depends on: The size and location of the VSD, The size of the pumping chambers, The location of the aorta and pulmonary artery, The presence of other complications (such as coarctation of the aorta and mitral valve problems), Your baby’s overall health at the time of diagnosis, Whether lung damage has occurred from too much blood flowing to the lungs for a long period of time.

• #28 Double Outlet Right Ventricle (DORV): Overview, Symptoms and Treatment | Nationwide Children’s Hospital

  https://www.nationwidechildrens.org/conditions/double-outlet-right-ventricle

  Double outlet right ventricle, or DORV, is a heart condition present at birth. The bodys main artery and the lung artery do not connect to the usual areas in the heart. […] DORV frequently will have additional heart defects and is very unique to each child. […] Most of these surgeries are a complete repair. This means that the blood flow is back to normal and the hole in the bottom chambers (VSD) is closed. When surgery happens depends on your childs unique DORV. It can happen anywhere from newborn to 1 year of age. Some babies will need more than one surgery. […] Some heart conditions are more severe and can cause problems right away. At the delivery hospital, a doctor who specializes in working with sick infants (neonatologist) will manage the care of your baby. They will watch your babys breathing and heart rate and look for other problems. […] Your cardiologist will follow up with your babys heart needs even after they are discharged from the hospital.

• #29 Double Outlet Right Ventricle – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/double-outlet-right-ventricle

  The clinical manifestations of DORV range from severe cyanosis (with the Taussig-Bing anomaly or any VSD type with pulmonary stenosis) to congestive heart failure and pulmonary hypertension (with a subaortic VSD and no pulmonary outflow obstruction). […] Physical examination may reveal a single loud second heart sound (S2) with pulmonary hypertension, a systolic ejection murmur at the base due to pulmonary stenosis, cyanosis with clubbing, and, if a coarctation is present, decreased femoral pulses. […] During the newborn period, prostaglandins may be needed for severe cyanosis if critical pulmonary stenosis is present. If pulmonary blood flow is greatly increased, heart failure treatment is required. However, surgical intervention is invariably required.

• #30 Double Outlet Right Ventricle Surgery: Background, Problem, Relevant Anatomy

  https://emedicine.medscape.com/article/904397-overview

  Double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. […] The clinical presentation can vary from one of profound cyanosis to that of fulminant congestive heart failure. As a result, management and surgical repair of the defect are based on correcting the specific combination of anatomic defects with their radically different pathophysiologies. […] The severity or lack of pulmonary stenosis largely determines the spectrum of symptoms and the patient’s age at the time of clinical presentation. In general, most patients present during the neonatal period. Patients with severe pulmonary stenosis have cyanosis, and those with uncontrolled pulmonary blood flow present with congestive heart failure.

• #31 Double Outlet Right Ventricle (DORV) – Diagnosis and Treatment

  https://angolodeldottorino.it/en/Medicine/Cardiology/Congenital_Heart_Diseases/Double_Outlet_Right_Ventricle.php

  Symptoms vary depending on the anatomical type of DORV: […] Newborns with pulmonary stenosis: early cyanosis and signs of hypoxemia. […] Newborns with increased pulmonary blood flow: signs of heart failure, tachypnea, and excessive sweating. […] Heart murmur: present in most patients, with variable intensity. […] The prognosis depends on the anatomical configuration and the success of surgical correction. Without treatment, survival is limited. With proper surgical intervention, long-term quality of life is generally good. Major complications include valvular dysfunction, residual stenosis, and arrhythmias.

• #32

  https://www.pted.org/?id=doubleoutlet2

  The symptoms associated with Double Outlet Right Ventricle depend on the position of the Ventricular Septal Defect (VSD) and the degree of pulmonary valve stenosis (narrowing or obstruction of the valve opening). With at least moderate pulmonary stenosis, desaturated blood enters the aorta and cyanosis is present (right to left shunt). If an insufficient amount of blood is pumped to the lungs (because of significant pulmonary stenosis), the infant will have difficulty adding weight and may show blueness (cyanosis). On the other hand, if too much blood is pumped to the lungs, heart failure may result. […] 1) Both the Aorta and Pulmonary Artery exit from the right ventricle 2) Ventricular Septal Defect (VSD)

• #33 Double Outlet Right Ventricle – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/double-outlet-right-ventricle

  The clinical manifestations of DORV range from severe cyanosis (with the Taussig-Bing anomaly or any VSD type with pulmonary stenosis) to congestive heart failure and pulmonary hypertension (with a subaortic VSD and no pulmonary outflow obstruction). […] Physical examination may reveal a single loud second heart sound (S2) with pulmonary hypertension, a systolic ejection murmur at the base due to pulmonary stenosis, cyanosis with clubbing, and, if a coarctation is present, decreased femoral pulses. […] During the newborn period, prostaglandins may be needed for severe cyanosis if critical pulmonary stenosis is present. If pulmonary blood flow is greatly increased, heart failure treatment is required. However, surgical intervention is invariably required.

• #34 Double Outlet Right Ventricle (DORV) – Diagnosis and Treatment

  https://angolodeldottorino.it/en/Medicine/Cardiology/Congenital_Heart_Diseases/Double_Outlet_Right_Ventricle.php

  Symptoms vary depending on the anatomical type of DORV: […] Newborns with pulmonary stenosis: early cyanosis and signs of hypoxemia. […] Newborns with increased pulmonary blood flow: signs of heart failure, tachypnea, and excessive sweating. […] Heart murmur: present in most patients, with variable intensity. […] The prognosis depends on the anatomical configuration and the success of surgical correction. Without treatment, survival is limited. With proper surgical intervention, long-term quality of life is generally good. Major complications include valvular dysfunction, residual stenosis, and arrhythmias.

• #35 Double Outlet Right Ventricle – Pediatrics – Merck Manual Professional Edition

  https://www.merckmanuals.com/professional/pediatrics/congenital-cardiovascular-anomalies/double-outlet-right-ventricle

  The clinical manifestations of DORV range from severe cyanosis (with the Taussig-Bing anomaly or any VSD type with pulmonary stenosis) to congestive heart failure and pulmonary hypertension (with a subaortic VSD and no pulmonary outflow obstruction). […] Physical examination may reveal a single loud second heart sound (S2) with pulmonary hypertension, a systolic ejection murmur at the base due to pulmonary stenosis, cyanosis with clubbing, and, if a coarctation is present, decreased femoral pulses. […] During the newborn period, prostaglandins may be needed for severe cyanosis if critical pulmonary stenosis is present. If pulmonary blood flow is greatly increased, heart failure treatment is required. However, surgical intervention is invariably required.

• #36 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #37 Double Outlet Right Ventricle in Children – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=double-outlet-right-ventricle-in-children-160-113

  Symptoms may vary depending on the exact heart abnormalities involved. Symptoms are often present at birth. But they may not appear until later. They can include: […] Surgery may greatly ease or stop these symptoms. That is even more likely if the surgery happens very early in life. […] DORV can cause serious complications. These include heart failure, high blood pressure in the lungs, and death. […] Most children with DORV go on to lead normal and active lives. But they will always need special follow-up care with cardiologists. Some may need follow-up surgery as adults.

• #38 Double-outlet right ventricle – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/double-outlet-right-ventricle/cdc-20389537

  In double-outlet right ventricle, the lower right heart chamber, called the right ventricle, has two openings for blood to exit instead of one. Some blood goes to the body instead of just the lungs. There also is a hole between the two lower heart chambers. The hole is called a ventricular septal defect. […] Babies with double-outlet right ventricle also have a hole between the lower heart chambers. The lower heart chambers are called the ventricles. The hole is called a ventricular septal defect. The hole causes oxygen-rich blood to mix with oxygen-poor blood. Babies with this hole may not get enough oxygen in the bloodstream. Their skin may appear gray or blue. […] Symptoms of double-outlet right ventricle may include: Pale gray or blue lips, tongue, or fingernails. Depending on skin color, these changes may be harder or easier to see. Rapid breathing. Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #39 Double Outlet Right Ventricle (DORV) (for Parents) | Nemours KidsHealth

  https://kidshealth.org/en/parents/dorv.html

  Babies born with DORV almost always show signs of the problem within a few days of birth. […] Within a few days of birth, a newborn with DORV usually will show these signs: breathing fast or hard, pale or bluish skin (cyanosis), sweating, poor feeding with little weight gain, excessive sleepiness. […] The position and size of the VSD and the positions of the pulmonary artery and aorta are different for each baby. So some babies with DORV have more severe symptoms than others. […] Extra pressure from blood going to the lungs of babies with DORV can damage the lungs’ blood vessels and lead to heart failure.

• #40 Partners in Care | Double Outlet Right Ventricle treatment at the…

  https://partnersincare.health/conditions/double-outlet-right-ventricle

  While some forms of DORV result in too much blood flow to the lungs, which causes damage to the heart and lungs and, over time, can cause heart failure, other forms of DORV result in not enough blood flow to the lungs. […] Some children with DOVR may have an evenly balanced amount of blood flowing to the lungs and body and may not experience symptoms at all. […] Symptoms of DORV may include: Difficulty feeding, Fast breathing, Fatigue, Poor weight gain, Sweating during feeds, Skin that appears pale or blue in color (cyanosis).

• #41 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Newborns with DORV typically show signs of the condition within a few days of birth. […] While the signs and symptoms can vary for each baby, in general they may include: Rapid breathing or difficulty breathing, Heart murmur, Rapid heartbeat, Sweating, Extreme tiredness, A blue tint to the skin, lips or nails (cyanosis), due to lack of oxygen in the blood, No interest in feeding, Weight loss or poor weight gain. […] In babies with DORV, the heart has to work harder than normal to pump enough oxygenated blood out into the body, which can cause the heart to become enlarged. Too much blood may also be pumped to the baby’s lungs. […] Without treatment, risks include high blood pressure and heart failure.

• #42

  https://www.pted.org/?id=doubleoutlet2

  The symptoms associated with Double Outlet Right Ventricle depend on the position of the Ventricular Septal Defect (VSD) and the degree of pulmonary valve stenosis (narrowing or obstruction of the valve opening). With at least moderate pulmonary stenosis, desaturated blood enters the aorta and cyanosis is present (right to left shunt). If an insufficient amount of blood is pumped to the lungs (because of significant pulmonary stenosis), the infant will have difficulty adding weight and may show blueness (cyanosis). On the other hand, if too much blood is pumped to the lungs, heart failure may result. […] 1) Both the Aorta and Pulmonary Artery exit from the right ventricle 2) Ventricular Septal Defect (VSD)

• #43 Double Outlet Right Ventricle – Children’s Health Issues – Merck Manual Consumer Version

  https://www.merckmanuals.com/home/children-s-health-issues/birth-defects-of-the-heart/double-outlet-right-ventricle

  Symptoms depend on the specific anatomy and location of the ventricular defect and associated abnormalities. […] Infants may have rapid breathing, poor feeding, easy tiring, and/or bluish color of the lips, nail beds, and skin (cyanosis). […] If too much blood flows through the pulmonary artery to the lungs, heart failure may develop.

• #44 Double Outlet Right Ventricle – Sheikh Shakhbout Medical City

  https://ssmc.ae/doctors-specialities/double-outlet-right-ventricle/

  Double Outlet Right Ventricle (DORV) is a congenital heart defect characterized by both the aorta and pulmonary artery arising predominantly from the right ventricle. […] Clinical manifestations of DORV can range from mild to severe, including: […] Cyanosis: A bluish tint to the skin due to low oxygen levels. […] Heart Failure: Symptoms such as fatigue, difficulty breathing, and poor growth in infants. […] Murmurs: Heart murmurs may be detected during physical examinations due to abnormal blood flow. […] Early intervention through surgical repair can significantly improve outcomes for affected individuals.

• #45 What Is Double Outlet Right Ventricle?

  https://www.icliniq.com/articles/heart-circulatory-health/double-outlet-right-ventricle

  The signs and symptoms of Double outlet right ventricle include: […] Signs of DORV include: […] Symptoms of DORV include: […] Complications that arise from DORV include: […] DORV may cause heart failure, a disease in which the heart fails to pump blood properly, causing symptoms such as fatigue, difficulty breathing, and fluid retention. […] Untreated DORV may result in elevated blood pressure in the lungs. Long-term pulmonary hypertension may permanently damage lung tissues, affecting their capacity to function. […] In severe cases or if left untreated, DORV can pose life-threatening risks. Inadequate oxygenation and impaired blood flow can have detrimental effects on the body that may result in death or irreversible damage. […] Surgery is important for nearly all cases of Double Outlet Right Ventricle (DORV), as children affected with this congenital heart defect encounter difficulties in properly pumping blood throughout the body, leading to severe symptoms such as breathing issues and inadequate weight gain. […] The prognosis for patients with DORV has significantly improved over time due to developments in medical and surgical interventions. Timely diagnosis and appropriate treatment significantly enhance the chances of a favorable outcome.

• #46 Double Outlet Right Ventricle Surgery: Background, Problem, Relevant Anatomy

  https://emedicine.medscape.com/article/904397-overview

  Double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. […] The clinical presentation can vary from one of profound cyanosis to that of fulminant congestive heart failure. As a result, management and surgical repair of the defect are based on correcting the specific combination of anatomic defects with their radically different pathophysiologies. […] The severity or lack of pulmonary stenosis largely determines the spectrum of symptoms and the patient’s age at the time of clinical presentation. In general, most patients present during the neonatal period. Patients with severe pulmonary stenosis have cyanosis, and those with uncontrolled pulmonary blood flow present with congestive heart failure.

• #47 Double Outlet Right Ventricle (DORV) (for Parents) | Nemours KidsHealth

  https://kidshealth.org/en/parents/dorv.html

  Babies born with DORV almost always show signs of the problem within a few days of birth. […] Within a few days of birth, a newborn with DORV usually will show these signs: breathing fast or hard, pale or bluish skin (cyanosis), sweating, poor feeding with little weight gain, excessive sleepiness. […] The position and size of the VSD and the positions of the pulmonary artery and aorta are different for each baby. So some babies with DORV have more severe symptoms than others. […] Extra pressure from blood going to the lungs of babies with DORV can damage the lungs’ blood vessels and lead to heart failure.

• #48 Double Outlet Right Ventricle (DORV) | Texas Children’s

  https://www.texaschildrens.org/content/conditions/double-outlet-right-ventricle-dorv

  Double outlet right ventricle (DORV) is a congenital heart defect, meaning it is present at birth. It occurs when the heart doesn’t form properly during fetal development. In most cases, the cause is unknown. […] Newborns with DORV typically show signs of the condition within a few days of birth. […] While the signs and symptoms can vary for each baby, in general they may include: Rapid breathing or difficulty breathing, Heart murmur, Rapid heartbeat, Sweating, Extreme tiredness, A blue tint to the skin, lips or nails (cyanosis), due to lack of oxygen in the blood, No interest in feeding, Weight loss or poor weight gain. […] In babies with DORV, the heart has to work harder than normal to pump enough oxygenated blood out into the body, which can cause the heart to become enlarged. Too much blood may also be pumped to the baby’s lungs. […] Without treatment, risks include high blood pressure and heart failure.

• #49 What Is Double Outlet Right Ventricle?

  https://www.icliniq.com/articles/heart-circulatory-health/double-outlet-right-ventricle

  The signs and symptoms of Double outlet right ventricle include: […] Signs of DORV include: […] Symptoms of DORV include: […] Complications that arise from DORV include: […] DORV may cause heart failure, a disease in which the heart fails to pump blood properly, causing symptoms such as fatigue, difficulty breathing, and fluid retention. […] Untreated DORV may result in elevated blood pressure in the lungs. Long-term pulmonary hypertension may permanently damage lung tissues, affecting their capacity to function. […] In severe cases or if left untreated, DORV can pose life-threatening risks. Inadequate oxygenation and impaired blood flow can have detrimental effects on the body that may result in death or irreversible damage. […] Surgery is important for nearly all cases of Double Outlet Right Ventricle (DORV), as children affected with this congenital heart defect encounter difficulties in properly pumping blood throughout the body, leading to severe symptoms such as breathing issues and inadequate weight gain. […] The prognosis for patients with DORV has significantly improved over time due to developments in medical and surgical interventions. Timely diagnosis and appropriate treatment significantly enhance the chances of a favorable outcome.

• #50 Double Outlet Right Ventricle in Children | UMass Memorial Health

  https://www.harringtonhospital.org/health-library/double-outlet-right-ventricle-in-children

  Double outlet right ventricle (DORV) is a type of congenital heart malformation. This means it is present from birth. In this condition, the heart and the main blood vessels leaving the heart do not develop the right way. This can cause symptoms in your child. […] Symptoms may vary depending on the exact heart abnormalities involved. Symptoms are often present at birth. But they may not appear until later. They can include: […] Surgery may greatly ease or stop these symptoms. That is even more likely if the surgery happens very early in life. […] DORV can cause serious complications. These include heart failure, high blood pressure in the lungs, and death. […] Many children with DORV can lead full and active lives. But they need lifelong follow-up care.

• #51 Double-outlet right ventricle – Overview – Mayo Clinic

  https://www.mayoclinic.org/diseases-conditions/double-outlet-right-ventricle/cdc-20389537

  In double-outlet right ventricle, the lower right heart chamber, called the right ventricle, has two openings for blood to exit instead of one. Some blood goes to the body instead of just the lungs. There also is a hole between the two lower heart chambers. The hole is called a ventricular septal defect. […] Babies with double-outlet right ventricle also have a hole between the lower heart chambers. The lower heart chambers are called the ventricles. The hole is called a ventricular septal defect. The hole causes oxygen-rich blood to mix with oxygen-poor blood. Babies with this hole may not get enough oxygen in the bloodstream. Their skin may appear gray or blue. […] Symptoms of double-outlet right ventricle may include: Pale gray or blue lips, tongue, or fingernails. Depending on skin color, these changes may be harder or easier to see. Rapid breathing. Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #52 Double-outlet right ventricle | Beacon Health System

  https://www.beaconhealthsystem.org/library/diseases-and-conditions/double-outlet-right-ventricle?content_id=CON-20359709

  In double-outlet right ventricle, the lower right heart chamber, called the right ventricle, has two openings for blood to exit instead of one. Some blood goes to the body instead of just the lungs. […] Babies with double-outlet right ventricle also have a hole between the lower heart chambers. The hole causes oxygen-rich blood to mix with oxygen-poor blood. Babies with this hole may not get enough oxygen in the bloodstream. Their skin may appear gray or blue. […] Symptoms of double-outlet right ventricle may include: Pale gray or blue lips, tongue, or fingernails. Rapid breathing. Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #53 Double outlet right ventricle | Lima Memorial Health System

  https://www.limamemorial.org/health-library/hie%20multimedia-textonly/1/007328

  Double outlet right ventricle (DORV) is a heart disease that is present from birth (congenital). The symptoms and severity of the problem will depend on the type of DORV. […] Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing.

• #54 Double-outlet right ventricle | Health Library | Memorial Health System

  https://www.mhsystem.org/health-library/con-20359709/

  Double-outlet right ventricle Symptoms may include: Pale gray or blue lips, tongue, or fingernails. Depending on skin color, these changes may be harder or easier to see. […] Rapid breathing. […] Problems with feeding, growth and weight gain. […] Complications of double-outlet right ventricle include poor growth and heart failure.

• #55 Double Outlet Right Ventricle | Children’s Hospital of Philadelphia

  https://www.chop.edu/conditions-diseases/double-outlet-right-ventricle

  Double outlet right ventricle symptoms vary depending on how much oxygenated blood is reaching the body. In most cases, children will have symptoms in the first days or weeks of life, including: […] Over time, this uncontrolled flow can damage the lungs and heart, and heart failure symptoms can result (similar to what happens with a simple VSD). […] However, in some cases, problems with the heart’s valves, heart rhythm or the baffle may occur, and additional surgeries or catheterization procedures may be required.

• #56 Double Outlet Right Ventricle in Children – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=double-outlet-right-ventricle-in-children-160-113

  Symptoms may vary depending on the exact heart abnormalities involved. Symptoms are often present at birth. But they may not appear until later. They can include: […] Surgery may greatly ease or stop these symptoms. That is even more likely if the surgery happens very early in life. […] DORV can cause serious complications. These include heart failure, high blood pressure in the lungs, and death. […] Most children with DORV go on to lead normal and active lives. But they will always need special follow-up care with cardiologists. Some may need follow-up surgery as adults.

• #57 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #58 Double Outlet Right Ventricle (DORV) – Diagnosis and Treatment

  https://angolodeldottorino.it/en/Medicine/Cardiology/Congenital_Heart_Diseases/Double_Outlet_Right_Ventricle.php

  Symptoms vary depending on the anatomical type of DORV: […] Newborns with pulmonary stenosis: early cyanosis and signs of hypoxemia. […] Newborns with increased pulmonary blood flow: signs of heart failure, tachypnea, and excessive sweating. […] Heart murmur: present in most patients, with variable intensity. […] The prognosis depends on the anatomical configuration and the success of surgical correction. Without treatment, survival is limited. With proper surgical intervention, long-term quality of life is generally good. Major complications include valvular dysfunction, residual stenosis, and arrhythmias.

• #59 Double Outlet Right Ventricle (DORV) – Diagnosis and Treatment

  https://angolodeldottorino.it/en/Medicine/Cardiology/Congenital_Heart_Diseases/Double_Outlet_Right_Ventricle.php

  Symptoms vary depending on the anatomical type of DORV: […] Newborns with pulmonary stenosis: early cyanosis and signs of hypoxemia. […] Newborns with increased pulmonary blood flow: signs of heart failure, tachypnea, and excessive sweating. […] Heart murmur: present in most patients, with variable intensity. […] The prognosis depends on the anatomical configuration and the success of surgical correction. Without treatment, survival is limited. With proper surgical intervention, long-term quality of life is generally good. Major complications include valvular dysfunction, residual stenosis, and arrhythmias.

• #60 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #61 Orphanet: Double outlet right ventricle

  https://www.orpha.net/en/disease/detail/3426

  A rare cono-truncal anomaly in which both the aorta and pulmonary artery originate, either entirely or predominantly, from the morphologic right ventricle. […] Double outlet right ventricle (DORV) accounts for about 2-3% of all congenital heart defects, with a birth prevalence rate of 1/ 10,000. […] Symptoms are generally observed during the first days or weeks of life. Cyanosis is the most frequent sign. Tachypnea or breathlessness, poor feeding and slow weight gain are also common. Tachycardia and/or heart murmur may also be observed. […] Without treatment, prognosis is poor due to severe cyanosis, congestive heart failure or pulmonary hypertension. With biventricular repair, patients have, on average, a normal life expectancy, with possible risk or re-operation. All patients that have received surgery for a DORV require life-long surveillance by a cardiologist. Univentricular palliation requires a very close follow up.

• #62 What Is Double Outlet Right Ventricle?

  https://www.icliniq.com/articles/heart-circulatory-health/double-outlet-right-ventricle

  The signs and symptoms of Double outlet right ventricle include: […] Signs of DORV include: […] Symptoms of DORV include: […] Complications that arise from DORV include: […] DORV may cause heart failure, a disease in which the heart fails to pump blood properly, causing symptoms such as fatigue, difficulty breathing, and fluid retention. […] Untreated DORV may result in elevated blood pressure in the lungs. Long-term pulmonary hypertension may permanently damage lung tissues, affecting their capacity to function. […] In severe cases or if left untreated, DORV can pose life-threatening risks. Inadequate oxygenation and impaired blood flow can have detrimental effects on the body that may result in death or irreversible damage. […] Surgery is important for nearly all cases of Double Outlet Right Ventricle (DORV), as children affected with this congenital heart defect encounter difficulties in properly pumping blood throughout the body, leading to severe symptoms such as breathing issues and inadequate weight gain. […] The prognosis for patients with DORV has significantly improved over time due to developments in medical and surgical interventions. Timely diagnosis and appropriate treatment significantly enhance the chances of a favorable outcome.

• #63 Double Outlet Right Ventricle (DORV)

  https://my.clevelandclinic.org/health/diseases/14733-double-outlet-right-ventricle

  Double outlet right ventricle symptoms usually appear during the first days or weeks after birth. They include: […] Cyanosis (blue or purple skin, lips or nails). […] Difficulty breathing, such as tachypnea (fast breathing) or shortness of breath. […] Difficulty eating or gaining weight. […] Heart murmur (extra sound in the heartbeat, which a healthcare provider can hear with a stethoscope). […] Tachycardia (heart rate faster than 100 beats a minute). […] Sweating a lot, such as while eating. […] Unusual sleepiness or seeming out of it. […] Without surgery, a baby with double outlet right ventricle will eventually develop: […] Cyanosis. […] Heart failure. […] Pulmonary hypertension (high blood pressure in the lungs). […] With surgery, most babies who have double outlet right ventricle live to be adults. […] Even after a surgical repair for double outlet right ventricle, a baby can have abnormal heart rhythms. […] Some people can develop heart failure years later.

• #64 What Is Double Outlet Right Ventricle?

  https://www.icliniq.com/articles/heart-circulatory-health/double-outlet-right-ventricle

  The signs and symptoms of Double outlet right ventricle include: […] Signs of DORV include: […] Symptoms of DORV include: […] Complications that arise from DORV include: […] DORV may cause heart failure, a disease in which the heart fails to pump blood properly, causing symptoms such as fatigue, difficulty breathing, and fluid retention. […] Untreated DORV may result in elevated blood pressure in the lungs. Long-term pulmonary hypertension may permanently damage lung tissues, affecting their capacity to function. […] In severe cases or if left untreated, DORV can pose life-threatening risks. Inadequate oxygenation and impaired blood flow can have detrimental effects on the body that may result in death or irreversible damage. […] Surgery is important for nearly all cases of Double Outlet Right Ventricle (DORV), as children affected with this congenital heart defect encounter difficulties in properly pumping blood throughout the body, leading to severe symptoms such as breathing issues and inadequate weight gain. […] The prognosis for patients with DORV has significantly improved over time due to developments in medical and surgical interventions. Timely diagnosis and appropriate treatment significantly enhance the chances of a favorable outcome.

• #65 Double Outlet Right Ventricle Surgery for Children – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=double-outlet-right-ventricle-surgery-for-children-161-106

  Surgery is needed for almost all cases of DORV. Children with DORV have trouble pumping blood through the body. That can lead to serious symptoms, such as breathing problems or not gaining weight. It can also cause serious complications. These include heart failure and high blood pressure in the vessels of the lungs. DORV surgery lets blood flow out to the body and lungs normally. […] Over time, symptoms will happen in a child with uncorrected DORV.

• #66 Double outlet right ventricle (S,D,L) with subaortic ventricular septal defect and pulmonary stenosis. Report of six cases – PubMed

  https://pubmed.ncbi.nlm.nih.gov/1109246/

  The clinical features were those of cyanosis, clubbing and accentuation of the second heart sound in the pulmonary area (related to aortic valve closure). […] There was a systolic ejection murmur along the upper left sternal border, related to pulmonary outflow tract stenosis. […] Relatively early surgical correction is suggested to minimize the progression of pulmonary infundibular stenosis and to avoid acquired atresia.

• #67 Orphanet: Double outlet right ventricle

  https://www.orpha.net/en/disease/detail/3426

  A rare cono-truncal anomaly in which both the aorta and pulmonary artery originate, either entirely or predominantly, from the morphologic right ventricle. […] Double outlet right ventricle (DORV) accounts for about 2-3% of all congenital heart defects, with a birth prevalence rate of 1/ 10,000. […] Symptoms are generally observed during the first days or weeks of life. Cyanosis is the most frequent sign. Tachypnea or breathlessness, poor feeding and slow weight gain are also common. Tachycardia and/or heart murmur may also be observed. […] Without treatment, prognosis is poor due to severe cyanosis, congestive heart failure or pulmonary hypertension. With biventricular repair, patients have, on average, a normal life expectancy, with possible risk or re-operation. All patients that have received surgery for a DORV require life-long surveillance by a cardiologist. Univentricular palliation requires a very close follow up.

• #68 Double outlet right ventricle

  https://adamcertificationdemo.adam.com/content.aspx?productid=142&pid=1&gid=007328

  Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing. […] Treatment requires surgery to close the hole in the heart and direct blood from the left ventricle into the aorta. Surgery may also be needed to move the pulmonary artery or aorta. […] How well the baby does depends on: The size and location of the VSD, The size of the pumping chambers, The location of the aorta and pulmonary artery, The presence of other complications (such as coarctation of the aorta and mitral valve problems), Your baby’s overall health at the time of diagnosis, Whether lung damage has occurred from too much blood flowing to the lungs for a long period of time.

• #69 Double outlet right ventricle (DORV) | Norton Children’s Louisville, Ky.

  https://nortonchildrens.com/services/cardiology/conditions/congenital-heart-disease/double-outlet-right-ventricle/

  Surgery is needed to correct DORV. Medicines might help the heart work better, but a baby with DORV cannot get better for long without surgery. […] Infants who have a repaired DORV will need to see a pediatric cardiologist throughout childhood, adolescence and adulthood. When the child becomes an adult, an adult congenital heart defect specialist can continue to provide care.

• #70 Double Outlet Right Ventricle | Mount Sinai – New York

  https://www.mountsinai.org/locations/childrens-heart/conditions/double-outlet-right-ventricle

  If your child has a diagnosis of double outlet right ventricle (DORV), you will want to know as much as possible about the problem—and the solution. And you want to know as quickly as possible. […] There are many variations of DORV. Your child’s symptoms and treatment will depend on how the position of the arteries along with the VSD and other possible abnormalities. […] Your child’s DORV symptoms depend on the specific anatomy of the heart and may include: Blue-or purple-tinted lips, skin, and nails from low oxygen levels (cyanosis); Heart murmur; Difficult feeding; Poor weight gain; Rapid or shallow breathing; Sweating, especially when eating. […] Patients with DORV require lifelong follow-up care, and the Children’s Heart Center is here for your child.

• #71 Double Outlet Right Ventricle in Children – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=double-outlet-right-ventricle-in-children-160-113

  Symptoms may vary depending on the exact heart abnormalities involved. Symptoms are often present at birth. But they may not appear until later. They can include: […] Surgery may greatly ease or stop these symptoms. That is even more likely if the surgery happens very early in life. […] DORV can cause serious complications. These include heart failure, high blood pressure in the lungs, and death. […] Most children with DORV go on to lead normal and active lives. But they will always need special follow-up care with cardiologists. Some may need follow-up surgery as adults.

• #72 Double Outlet Right Ventricle

  https://healthlibrary.wjmc.org/library/diseasesconditions/adult/Infectious/3,90590

  Double outlet right ventricle (DORV) is a rare heart malformation. Its when the heart and the main vessels leaving the heart dont develop the way they should. The problem is present from birth (congenital). […] The symptoms of DORV may vary based on the exact heart problem involved. Symptoms are often present at birth. They can include: Bluish color (cyanosis) of the skin, lips, or nails, or pale skin; Fast breathing or problems breathing; Tiring easily, especially when feeding; Failure to gain weight normally; Swelling in the legs or belly (abdomen); Sleepiness or unresponsiveness. […] Most children with DORV go on to lead normal and active lives. But they will need to see a heart specialist regularly. Some may need more surgery as adults.

• #73 An Introduction To Double Outlet Right Ventricle (DORV) – Travocure

  http://travocure.com/an-introduction-to-double-outlet-right-ventricle-dorv/

  The symptoms of DORV can vary depending on the specific anatomy of the heart and the degree of blood mixing between the two circulatory systems. Common symptoms may include: […] Cyanosis: Babies with DORV often have bluish skin and lips due to inadequate oxygen supply to the body. […] Rapid Breathing and Fatigue: Infants may exhibit rapid breathing and tire easily during feeding or physical activity. […] Poor Growth: Some infants with DORV may experience slow growth and weight gain due to the increased effort required to pump blood. […] Heart Murmur: A heart murmur, an abnormal sound that a turbulent blood flow produces, is often present and undergoes detection during a physical examination. […] Thanks to developments in medical and surgical procedures, the prognosis for people with DORV has greatly improved recently. For a positive outcome, early diagnosis and adequate treatment are essential. Many children with DORV can live healthy lives and develop normally with the right treatment. However, periodic procedures and lifetime cardiac monitoring is extremely essential. […] Many children with DORV can live happy lives and reach their full potential with continuing care and supervision.

• #74 Double Outlet Right Ventricle in Children | UMass Memorial Health

  https://www.harringtonhospital.org/health-library/double-outlet-right-ventricle-in-children

  Double outlet right ventricle (DORV) is a type of congenital heart malformation. This means it is present from birth. In this condition, the heart and the main blood vessels leaving the heart do not develop the right way. This can cause symptoms in your child. […] Symptoms may vary depending on the exact heart abnormalities involved. Symptoms are often present at birth. But they may not appear until later. They can include: […] Surgery may greatly ease or stop these symptoms. That is even more likely if the surgery happens very early in life. […] DORV can cause serious complications. These include heart failure, high blood pressure in the lungs, and death. […] Many children with DORV can lead full and active lives. But they need lifelong follow-up care.

• #75 Double outlet right ventricle

  https://adamcertificationdemo.adam.com/content.aspx?productid=142&pid=1&gid=007328

  Signs of DORV may include: Enlarged heart, Heart murmur, Rapid breathing, Rapid heartbeat. […] Symptoms of DORV may include: Poor feeding from becoming tired easily, Bluish color of the skin and lips (cyanosis), Clubbing (thickening of the nail beds) of toes and fingers (late sign), Failure to gain weight and grow, Pale coloring (pallor), Sweating, Swollen legs or abdomen, Trouble breathing. […] Treatment requires surgery to close the hole in the heart and direct blood from the left ventricle into the aorta. Surgery may also be needed to move the pulmonary artery or aorta. […] How well the baby does depends on: The size and location of the VSD, The size of the pumping chambers, The location of the aorta and pulmonary artery, The presence of other complications (such as coarctation of the aorta and mitral valve problems), Your baby’s overall health at the time of diagnosis, Whether lung damage has occurred from too much blood flowing to the lungs for a long period of time.

• #76 Double Outlet Right Ventricle (DORV) | Dayton, Ohio

  http://fetaltonewborn.org/double-outlet-right-ventricle-dorv/

  Babies who have DORV may show these symptoms: Tiring easily, especially when feeding […] Bluish color of the skin and lips […] Clubbing (thickening of the nail beds) of the fingers and toes […] Poor growth or poor weight gain […] Pale skin […] Sweating […] Difficulty breathing […] Rapid breathing […] Rapid heartbeat. How well your baby does after surgery will depend on: The size and location of the VSD […] The function of your babys ventricles […] The status of the pulmonary valve […] Whether or not your baby has other heart conditions […] Your babys overall health at the time of diagnosis […] Whether or not lung damage has occurred from too much blood flowing to the lungs.

• #77 What Is Double Outlet Right Ventricle?

  https://www.icliniq.com/articles/heart-circulatory-health/double-outlet-right-ventricle

  The signs and symptoms of Double outlet right ventricle include: […] Signs of DORV include: […] Symptoms of DORV include: […] Complications that arise from DORV include: […] DORV may cause heart failure, a disease in which the heart fails to pump blood properly, causing symptoms such as fatigue, difficulty breathing, and fluid retention. […] Untreated DORV may result in elevated blood pressure in the lungs. Long-term pulmonary hypertension may permanently damage lung tissues, affecting their capacity to function. […] In severe cases or if left untreated, DORV can pose life-threatening risks. Inadequate oxygenation and impaired blood flow can have detrimental effects on the body that may result in death or irreversible damage. […] Surgery is important for nearly all cases of Double Outlet Right Ventricle (DORV), as children affected with this congenital heart defect encounter difficulties in properly pumping blood throughout the body, leading to severe symptoms such as breathing issues and inadequate weight gain. […] The prognosis for patients with DORV has significantly improved over time due to developments in medical and surgical interventions. Timely diagnosis and appropriate treatment significantly enhance the chances of a favorable outcome.

• #78 Double Outlet Right Ventricle Surgery for Children – Stanford Medicine Children’s Health

  https://www.stanfordchildrens.org/en/topic/default?id=double-outlet-right-ventricle-surgery-for-children-161-106

  Surgery is needed for almost all cases of DORV. Children with DORV have trouble pumping blood through the body. That can lead to serious symptoms, such as breathing problems or not gaining weight. It can also cause serious complications. These include heart failure and high blood pressure in the vessels of the lungs. DORV surgery lets blood flow out to the body and lungs normally. […] Over time, symptoms will happen in a child with uncorrected DORV.

• #79 Double outlet right ventricle (DORV) | Norton Children’s Louisville, Ky.

  https://nortonchildrens.com/services/cardiology/conditions/congenital-heart-disease/double-outlet-right-ventricle/

  Surgery is needed to correct DORV. Medicines might help the heart work better, but a baby with DORV cannot get better for long without surgery. […] Infants who have a repaired DORV will need to see a pediatric cardiologist throughout childhood, adolescence and adulthood. When the child becomes an adult, an adult congenital heart defect specialist can continue to provide care.

• #80 Orphanet: Double outlet right ventricle

  https://www.orpha.net/en/disease/detail/3426

  A rare cono-truncal anomaly in which both the aorta and pulmonary artery originate, either entirely or predominantly, from the morphologic right ventricle. […] Double outlet right ventricle (DORV) accounts for about 2-3% of all congenital heart defects, with a birth prevalence rate of 1/ 10,000. […] Symptoms are generally observed during the first days or weeks of life. Cyanosis is the most frequent sign. Tachypnea or breathlessness, poor feeding and slow weight gain are also common. Tachycardia and/or heart murmur may also be observed. […] Without treatment, prognosis is poor due to severe cyanosis, congestive heart failure or pulmonary hypertension. With biventricular repair, patients have, on average, a normal life expectancy, with possible risk or re-operation. All patients that have received surgery for a DORV require life-long surveillance by a cardiologist. Univentricular palliation requires a very close follow up.

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