Pniowiec tętniczy – Charakterystyka, pielęgnacja i opieka

Pniowiec tętniczy
Charakterystyka, pielęgnacja i opieka

Pniowiec tętniczy (truncus arteriosus) to rzadka wrodzona wada serca charakteryzująca się brakiem rozdzielenia aorty i tętnicy płucnej, skutkująca obecnością pojedynczego pnia tętniczego z ubytkiem przegrody międzykomorowej (VSD). Nieleczony prowadzi do niewydolności serca w ciągu pierwszych 7 dni życia, manifestując się sinicą, objawami niewydolności serca i nadciśnienia płucnego. Przedoperacyjne leczenie farmakologiczne obejmuje digoksynę (monitorowanie tętna koniuszkowego, przerwanie podania przy tętni <90-110 u/min u niemowląt), diuretyki, inhibitory ACE oraz dożylne podawanie prostaglandyny w celu utrzymania drożności przewodu tętniczego. Wsparcie żywieniowe obejmuje wysokoenergetyczne mieszanki mleczne, karmienie sondą donosową lub żywienie pozajelitowe, z koniecznością ścisłej kontroli bilansu płynów i poziomu potasu (istotne ze względu na ryzyko toksyczności digoksyny).

Charakterystyka pniowca tętniczego (truncus arteriosus)

Pniowiec tętniczy (łac. truncus arteriosus) to rzadka wrodzona wada serca, w której nie dochodzi do prawidłowego rozdzielenia dwóch głównych naczyń krwionośnych odchodzących od serca – aorty i tętnicy płucnej. Zamiast dwóch oddzielnych naczyń, występuje jedno duże wspólne naczynie (pień tętniczy), które wychodzi z obu komór przez pojedynczą zastawkę pniową. Dodatkowo u prawie wszystkich dzieci z pniowcem tętniczym występuje ubytek przegrody międzykomorowej (VSD), który umożliwia mieszanie się krwi bogatej w tlen z krwią ubogą w tlen.¹²

Nieleczony pniowiec tętniczy prowadzi do niewydolności serca w ciągu pierwszych 7 dni życia. Jest to stan zagrażający życiu, który wymaga natychmiastowej interwencji chirurgicznej. U niemowląt z pniowcem tętniczym często obserwuje się sinicę (niebieskawą barwę skóry) spowodowaną niedotlenieniem organizmu oraz objawy niewydolności serca i nadciśnienia płucnego.³⁴⁵

Przygotowanie do zabiegu chirurgicznego

Leczenie medyczne przed zabiegiem chirurgicznym zależy od stanu klinicznego noworodka. Większość noworodków z pniowcem tętniczym wykazuje objawy zastoinowej niewydolności serca i wymaga leczenia farmakologicznego przed operacją.⁶

Farmakoterapia przedoperacyjna

Przed zabiegiem chirurgicznym często stosuje się następujące leki:⁷⁸⁹

Digoksyna – powoduje, że serce kurczy się silniej, ale wolniej. Rola pielęgniarki obejmuje pomiar tętna koniuszkowego przez pełną minutę. Należy wstrzymać podanie leku, jeśli tętno koniuszkowe jest mniejsze niż 60 u dorosłych, mniejsze niż 70 u dzieci, mniejsze niż 90-110 u niemowląt.¹⁰
Diuretyki – pomagają pozbyć się nadmiaru płynów z organizmu i zmniejszyć obciążenie serca.
Inhibitory ACE – zmniejszają obciążenie następcze serca.
Prostaglandyna podawana dożylnie – często stosowana u pacjentów z pniowcem tętniczym przy przyjęciu, ponieważ różnicowa diagnoza obejmuje liczne anomalie z przepływem krwi do układu płucnego lub systemowego zależnym od przewodu tętniczego.¹¹

W niektórych przypadkach mogą być wskazane inne leki przedoperacyjne, w zależności od konkretnych okoliczności, takie jak leki zmniejszające obciążenie następcze, leki inotropowe lub leki przeciwarytmiczne.¹²

Wsparcie żywieniowe

Niemowlęta z pniowcem tętniczym często mają problemy z karmieniem i przyrostem masy ciała. Przed operacją mogą potrzebować:¹³¹⁴

Wysokoenergetycznych mieszanek mlecznych dla zapewnienia odpowiedniego przyrostu masy ciała
Karmienia przez sondę donosową
W niektórych przypadkach żywienia pozajelitowego przez dostęp dożylny

Należy dokładnie monitorować pobieranie i wydalanie płynów, aby ocenić funkcję nerek, która musi być prawidłowa dla bezpiecznego stosowania leków, takich jak digoksyna. Hipokaliemia zwiększa ryzyko toksyczności digoksyny, dlatego poziom potasu powinien być ściśle kontrolowany.¹⁵

Leczenie chirurgiczne pniowca tętniczego

Zabieg chirurgiczny jest niezbędny w leczeniu pniowca tętniczego i powinien być przeprowadzony w ciągu pierwszych 2 tygodni życia dziecka, aby zapobiec uszkodzeniu naczyń płucnych i rozwojowi nieodwracalnego nadciśnienia płucnego.¹⁶¹⁷

Zabieg Rastelli

Najczęściej wykonywany zabieg chirurgiczny to naprawa metodą Rastelli, która tworzy dwie oddzielne drogi dla krwi opuszczającej serce dziecka. Procedura obejmuje:¹⁸¹⁹

Zamknięcie ubytku przegrody międzykomorowej (VSD) za pomocą łaty
Oddzielenie tętnic płucnych od wspólnego pnia tętniczego
Utworzenie nowej aorty z istniejącego naczynia (pnia tętniczego)
Utworzenie nowej zastawki aortalnej z istniejącej zastawki pniowej
Umieszczenie sztucznego przewodu (konduit) z zastawką w celu utworzenia nowej tętnicy płucnej łączącej prawą komorę z tętnicami płucnymi

Po zabiegu chirurgicznym pacjent będzie wymagał kolejnych operacji w przyszłości, ponieważ wraz z rozwojem dziecka konduit nie rośnie i konieczna będzie jego wymiana. Zazwyczaj kolejna operacja jest potrzebna w ciągu 3-10 lat po pierwszym zabiegu.²⁰²¹

Opieka pooperacyjna

Pobyt na oddziale intensywnej terapii

Po zabiegu chirurgicznym niemowlę zostaje przeniesione na oddział intensywnej terapii kardiologicznej (CICU), gdzie otrzymuje całodobową opiekę od zespołu specjalistów w dziedzinie intensywnej terapii kardiologicznej.²²²³

W okresie pooperacyjnym stosuje się:²⁴²⁵

Wentylację mechaniczną
Specjalne systemy monitorowania parametrów życiowych
Leki dożylne, w tym leki inotropowe wspierające pracę serca
Leki przeciwbólowe i zmniejszające lęk
Drenaż klatki piersiowej

Zespół medyczny koncentruje się na utrzymaniu odpowiedniego rzutu serca i zarządzaniu skutkami rezydualnych wad, niedomykalności zastawki pniowej, arytmii lub nadciśnienia płucnego.²⁶

Etap zdrowienia

Stopniowo, w miarę poprawy stanu niemowlęcia, zmniejsza się wsparcie wentylacyjne i inotropowe, a pacjenta przestawia się na podawanie leków doustnych. Rozpoczyna się także proces nauki karmienia.²⁷

Czas pobytu w szpitalu po operacji wynosi od jednego do trzech tygodni w większości przypadków. Przed wypisem ze szpitala zespół medyczny przekaże rodzicom instrukcje dotyczące:²⁸²⁹

Podawania leków
Ograniczeń aktywności
Terminów wizyt kontrolnych
Kontroli bólu – mogą być zalecane leki przeciwbólowe, takie jak paracetamol lub ibuprofen

Wyzwania żywieniowe

Niemowlęta po operacji pniowca tętniczego mogą mieć zwiększone potrzeby kaloryczne i trudności z karmieniem. Wsparcie żywieniowe może obejmować:³⁰³¹

Mieszanki o wysokiej zawartości kalorii przez kilka tygodni lub miesięcy po operacji
Karmienie przez sondę do czasu, aż dziecko będzie w stanie efektywnie jeść
Codzienne ważenie niemowlęcia w celu monitorowania przyrostu masy ciała

Farmakoterapia pooperacyjna

Po zabiegu chirurgicznym niemowlęta często są wypisywane z lekami kardiologicznymi, które mogą być stopniowo odstawiane w ciągu kolejnych miesięcy. Farmakoterapia może obejmować:³²³³

Leki stosowane w opiece domowej

Digoksyna – zwiększa kurczliwość mięśnia sercowego. Rola pielęgniarki obejmuje edukację rodziców w zakresie monitorowania częstości akcji serca i objawów toksyczności digoksyny.
Diuretyki – pomagają kontrolować retencję płynów i zmniejszają obciążenie serca.
Inhibitory ACE – zmniejszają obciążenie następcze serca i pomagają w remodelingu serca.
Leki przeciwbólowe – podawane w celu zapewnienia komfortu dziecku w okresie pooperacyjnym.

Kluczowe jest ścisłe monitorowanie parametrów życiowych, nawodnienia i równowagi elektrolitowej, szczególnie poziomu potasu przy stosowaniu digoksyny.³⁴

Opieka długoterminowa i dalsze postępowanie

Dziecko z pniowcem tętniczym będzie wymagało dożywotniej opieki kardiologicznej. Pediatryczni kardiolodzy opiekują się pacjentami z pniowcem tętniczym do czasu, gdy są młodymi dorosłymi, koordynując opiekę z lekarzem podstawowej opieki zdrowotnej.³⁵³⁶

Regularne wizyty kontrolne

Regularne wizyty kontrolne u kardiologa są niezbędne dla monitorowania stanu zdrowia i wczesnego wykrywania potencjalnych problemów. Podczas tych wizyt wykonywane są:³⁷³⁸

Elektrokardiogramy (EKG)
Monitory Holtera
Testy wysiłkowe
Echokardiogramy
W razie potrzeby cewnikowanie serca

Potencjalne późne powikłania

U pacjentów po korekcji pniowca tętniczego mogą wystąpić późne powikłania, takie jak:³⁹⁴⁰

Zwężenie konduitu lub tętnicy płucnej wymagające wymiany
Niedomykalność zastawki aortalnej (pniowej)
Zaburzenia rytmu serca (arytmie)
U pacjentów z towarzyszącym przerwaniem łuku aorty – nawrót zwężenia łuku i ucisk oskrzeli

Niedomykalność zastawki pniowej, która może postępować nawet jeśli nie była ciężka przed zabiegiem, może stać się istotną przyczyną utrzymującego się niepowodzenia w przybieraniu na wadze, a naprawa lub wymiana zastawki może być wskazana.⁴¹

Profilaktyka infekcyjnego zapalenia wsierdzia

Pacjenci z pniowcem tętniczym wymagają profilaktyki antybiotykowej przed niektórymi zabiegami stomatologicznymi i chirurgicznymi w celu zapobiegania infekcyjnemu zapaleniu wsierdzia.⁴²⁴³

Ograniczenia aktywności

Dzieci po operacji pniowca tętniczego mogą mieć pewne ograniczenia aktywności fizycznej. Należy skonsultować się z kardiologiem dziecięcym w sprawie bezpiecznych form aktywności i sportu dla dziecka.⁴⁴⁴⁵

Przejście do opieki dla dorosłych

Gdy pacjent osiągnie dorosłość, konieczne będzie przejście pod opiekę kardiologa specjalizującego się w wadach wrodzonych serca u dorosłych. Zapewnienie ciągłości opieki jest kluczowe dla długoterminowego zdrowia i jakości życia.⁴⁶⁴⁷

Wsparcie dla rodzin

Opieka nad dzieckiem z poważną wadą serca, taką jak pniowiec tętniczy, może być wyzwaniem. Istotne jest zapewnienie wsparcia dla całej rodziny:⁴⁸⁴⁹

Edukacja rodziców na temat stanu dziecka, leczenia i długoterminowych wyników
Wsparcie psychologiczne i grupy wsparcia dla rodzin
Szkolenie w zakresie resuscytacji krążeniowo-oddechowej (CPR) przed wypisem ze szpitala
W niektórych przypadkach – usługi domowej opieki pielęgniarskiej, które mogą pomóc zapewnić dzieciom wracającym do zdrowia po pniowcu tętniczym opiekę i uwagę, na jaką zasługują

Ważne jest, aby rodziny miały otwartą komunikację z zespołem medycznym i zadawały pytania w razie wątpliwości.⁵⁰

Wyniki i rokowania

Operacja naprawy pniowca tętniczego jest zazwyczaj skuteczna, szczególnie jeśli zabieg zostanie przeprowadzony przed ukończeniem przez dziecko pierwszego miesiąca życia. Wyniki w obecnej erze są doskonałe dla niepowikłanego pniowca tętniczego i nieco gorsze dla tych z towarzyszącymi złożonymi anomaliami.⁵¹⁵²

Po chirurgicznej korekcji pniowca tętniczego ponad 80% pacjentów dożywa wieku dorosłego. Większość pacjentów dobrze funkcjonuje, szczególnie dzięki ulepszonym technikom chirurgicznym i większej liczbie opcji naprawy i wymiany zastawek aortalnych i płucnych.⁵³⁵⁴

Bez leczenia chirurgicznego pniowiec tętniczy jest stanem zagrażającym życiu, a większość niemowląt nie przeżyłaby pierwszego roku życia. Z odpowiednią opieką i regularnym monitorowaniem przez kardiologa, większość dzieci po operacji pniowca tętniczego będzie wiodło zdrowe życie.⁵⁵⁵⁶

Kolejne rozdziały

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Materiały źródłowe

#1 Truncus Arteriosus | American Heart Association
https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/truncus-arteriosus
Truncus arteriosus occurs when the two large arteries carrying blood away from the heart donât form properly and one large artery is present instead. This artery (the truncus) sits over a large opening or hole in the wall between the two pumping chambers (ventricular septal defect). With only one artery, there is no specific path to the lungs for oxygen before returning to the heart to deliver oxygen to the body. […] Surgery is needed to close the ventricular septal defect (VSD) and separate blood flow to the body from blood flow to the lungs. This is usually done early in infancy to prevent high blood pressure from damaging the lung arteries. A patch is used to close the ventricular defect. The pulmonary arteries are then disconnected from the single great vessel (the truncus) and a tube (a conduit or tunnel) is placed from the right ventricle to the pulmonary arteries. This is sometimes called a Rastelli repair.
#2 Truncus Arteriosus | Children’s Hospital Colorado
https://www.childrenscolorado.org/conditions-and-advice/conditions-and-symptoms/conditions/truncus-arteriosus/
Truncus arteriosus is a rare type of congenital birth defect in which the two major arteries of the heart (the aorta and the pulmonary artery) fail to separate during development. Instead, there is only one large vessel coming from the heart. […] If your child has been diagnosed with truncus arteriosus, he or she will need heart surgery to repair it. […] Surgery is recommended within the first few weeks of life if the condition is detected immediately after birth. During the procedure, a pediatric cardiac surgeon will close the holes within the heart and separate the pulmonary and truncal arteries. […] After truncus arteriosus treatment, children will spend 2 to 3 weeks in the hospital and have follow-up appointments with a cardiologist.
#3 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#4 About Truncus Arteriosus | Congenital Heart Defects (CHDs) | CDC
https://www.cdc.gov/heart-defects/about/truncus-arteriosus.html
People with truncus arteriosus should schedule routine checkups with a heart doctor to stay as healthy as possible. […] Infants with truncus arteriosus usually are in distress in the first few days of life. […] Infants with truncus arteriosus can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. […] Some babies and children will need medicines to help strengthen the heart muscle, lower their blood pressure, and help the body get rid of extra fluid. […] To make sure babies have a healthy weight gain, a special high-calorie formula might be prescribed. […] Surgery is needed to repair the heart and blood vessels. […] A person born with truncus arteriosus will need regular follow-up visits with a cardiologist (a heart doctor).
#5 Truncus Arteriosus NCLEX Questions
https://www.registerednursern.com/truncus-arteriosus-nclex-questions/
The answers are B and C. This infant has only one artery that is arising out of the right and left ventricle. Deoxygenated and oxygenated blood is mixing in the ventricles, entering the truncus arteriosus, and going to both the lungs and systemic circulation. Consequently, more blood is flowing to the lungs than the systemic circulation (the body) because resistance in lower to the lungs than the body. Hence, it is easier to pump blood to the lungs than to body (blood flow to the body requires a lot of pressure when compared to the lungs). Its important to note that the blood that is entering the body is a mixture of deoxygenated and oxygenated blood (leading to cyanosis). Now because there is more blood flow going to the lungs, this leads to damage to the arteries that feed the lungs, and this leads to pulmonary hypertension. The pulmonary hypertension increases the resistance the heart must pump against to get the blood to the lungs. Therefore, the heart becomes very weak from having to pump so hard against the resistance to the lungs, and this leads to heart failure. Many infants with a severe case of truncus arteriosus will develop heart failure within the first 7 days of life.
#6 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Medical care before surgical repair depends on the neonate’s clinical presentation. […] Most neonates with truncus arteriosus display evidence of congestive heart failure and are usually treated with digitalis and diuretic medicines. […] Intravenous prostaglandin is often administered in patients with truncus arteriosus upon presentation because the differential diagnosis includes numerous anomalies with duct-dependent systemic or pulmonary blood flow. […] Other preoperative medications are not generally indicated, although specific circumstances may dictate afterload reducing agents, inotropic medications, or antiarrhythmics. […] Full-term and premature newborns with truncus arteriosus may be at increased risk for necrotizing enterocolitis, either preoperatively or postoperatively, and appropriate evaluation should be undertaken in any newborn exhibiting signs or symptoms of necrotizing enterocolitis.
#7 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#8 Truncus Arteriosus NCLEX Questions
https://www.registerednursern.com/truncus-arteriosus-nclex-questions/
The answer is D. A normal digoxin level is 0.5-2 ng/mL (the patients digoxin level is normal in this scenario). Therefore, the nurse should ADMINISTER the dose as ordered..AFTER checking the apical pulse. […] The answers are B, C, and D. Digoxin, ACE inhibitors, and Diuretics may be ordered to help with heart function and prevent complications associated with heart failure in an infant prior to surgery.
#9 Truncus Arteriosus > Fact Sheets > Yale Medicine
https://www.yalemedicine.org/conditions/truncus-arteriosus
Truncus arteriosus is a congenital heart defect that prevents the heart from sending enough oxygen-rich blood throughout the body. This occurs because blood vessels within a fetus’s heart did not develop normally during pregnancy. The condition causes heart failure, and, without treatment, babies may die within the first year of life. […] Babies born with truncus arteriosus usually experience heart failure within the first few weeks of life. However, when the condition is surgically corrected during infancy, more than 80% of patients live to adulthood. Most patients do quite well, especially with improving surgical techniques and more options for aortic and pulmonic valve repairs and replacements. Follow-up cardiology care is lifelong for these patients. […] Doctors surgically correct truncus arteriosus within the first few months of a baby’s life. A newborn may need medication (diuretics, digoxin, and ACE inhibitors) to manage the symptoms of heart failure before surgery.
#10 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#11 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Medical care before surgical repair depends on the neonate’s clinical presentation. […] Most neonates with truncus arteriosus display evidence of congestive heart failure and are usually treated with digitalis and diuretic medicines. […] Intravenous prostaglandin is often administered in patients with truncus arteriosus upon presentation because the differential diagnosis includes numerous anomalies with duct-dependent systemic or pulmonary blood flow. […] Other preoperative medications are not generally indicated, although specific circumstances may dictate afterload reducing agents, inotropic medications, or antiarrhythmics. […] Full-term and premature newborns with truncus arteriosus may be at increased risk for necrotizing enterocolitis, either preoperatively or postoperatively, and appropriate evaluation should be undertaken in any newborn exhibiting signs or symptoms of necrotizing enterocolitis.
#12 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Medical care before surgical repair depends on the neonate’s clinical presentation. […] Most neonates with truncus arteriosus display evidence of congestive heart failure and are usually treated with digitalis and diuretic medicines. […] Intravenous prostaglandin is often administered in patients with truncus arteriosus upon presentation because the differential diagnosis includes numerous anomalies with duct-dependent systemic or pulmonary blood flow. […] Other preoperative medications are not generally indicated, although specific circumstances may dictate afterload reducing agents, inotropic medications, or antiarrhythmics. […] Full-term and premature newborns with truncus arteriosus may be at increased risk for necrotizing enterocolitis, either preoperatively or postoperatively, and appropriate evaluation should be undertaken in any newborn exhibiting signs or symptoms of necrotizing enterocolitis.
#13 About Truncus Arteriosus | Congenital Heart Defects (CHDs) | CDC
https://www.cdc.gov/heart-defects/about/truncus-arteriosus.html
People with truncus arteriosus should schedule routine checkups with a heart doctor to stay as healthy as possible. […] Infants with truncus arteriosus usually are in distress in the first few days of life. […] Infants with truncus arteriosus can have a bluish looking skin color, called cyanosis, because their blood doesn’t carry enough oxygen. […] Some babies and children will need medicines to help strengthen the heart muscle, lower their blood pressure, and help the body get rid of extra fluid. […] To make sure babies have a healthy weight gain, a special high-calorie formula might be prescribed. […] Surgery is needed to repair the heart and blood vessels. […] A person born with truncus arteriosus will need regular follow-up visits with a cardiologist (a heart doctor).
#14 Truncus Arteriosus | Boston Children’s Hospital
https://www.childrenshospital.org/conditions/truncus-arteriosus
Truncus arteriosus must be treated through surgery. While your baby is waiting for surgery, he or she may need to take medications to reduce fluid in the lungs and have high-calorie feedings to build strength. […] Care for truncus lasts a lifetime. We specialize in the neonatal full repair but also specialize in the follow-up care which can include: […] Sometimes, the truncal valve can leak and it needs to be repaired or replaced at some point in the future.
#15 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#16 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
Truncus arteriosus repair (within first 2 weeks of life): VSD is closed with a patch, there is separating of the pulmonary arteries from the truncus arteriosus and they are connected to the right ventricle using a valved conduit. […] Educate: conduit may narrow overtime or the child may outgrow it and will need more procedures in the future, and prophylactic antibiotics may be needed to prevent bacterial endocarditis.
#17 Truncus Arteriosus
https://www.rwjbh.org/treatment-care/heart-and-vascular-care/diseases-conditions/congenital-heart-disease/truncus-arteriosus/
If not treated immediately, life-threatening consequences can occur. […] Surgery to repair truncus arteriosus is generally successful, especially if the repair occurs before your baby is one month old. […] Truncus arteriosus is most often fatal without early intervention. Therefore, intervention is critical. […] Some of treatment options include: […] Truncus arteriosus Treatment Care offered at these locations in your neighborhood.
#18 Truncus Arteriosus: Symptoms & Treatment
https://my.clevelandclinic.org/health/diseases/14785-truncus-arteriosus
Babies with truncus arteriosus need heart surgery within the first weeks of life. The most common procedure is called a Rastelli repair, which creates two separate paths for blood to leave your babys heart. […] Your babys surgeon will: Use a patch to close the hole in your babys heart (VSD) […] Create a new aorta using the existing blood vessel (truncus) […] Create a new aortic valve using the existing truncal valve […] Place an artificial tube (conduit) and artificial valve to create a new pulmonary artery and valve. […] Your childs surgeon will tell you more about future surgeries and what theyll involve. Your child will likely need another surgery within three to 10 years after their first one, and possibly more after that. […] Follow the appointment schedule your childs care team provides. Your child will need routine appointments with a heart specialist (pediatric cardiologist). […] This ongoing care is very important. Your childs providers will: Run tests, including imaging tests and cardiac catheterizations, to see how your childs heart is functioning […] Perform additional surgeries, as needed, to address issues with the conduit or valves.
#19 Truncus Arteriosus | American Heart Association
https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/truncus-arteriosus
Truncus arteriosus occurs when the two large arteries carrying blood away from the heart donât form properly and one large artery is present instead. This artery (the truncus) sits over a large opening or hole in the wall between the two pumping chambers (ventricular septal defect). With only one artery, there is no specific path to the lungs for oxygen before returning to the heart to deliver oxygen to the body. […] Surgery is needed to close the ventricular septal defect (VSD) and separate blood flow to the body from blood flow to the lungs. This is usually done early in infancy to prevent high blood pressure from damaging the lung arteries. A patch is used to close the ventricular defect. The pulmonary arteries are then disconnected from the single great vessel (the truncus) and a tube (a conduit or tunnel) is placed from the right ventricle to the pulmonary arteries. This is sometimes called a Rastelli repair.
#20 Truncus Arteriosus: Symptoms & Treatment
https://my.clevelandclinic.org/health/diseases/14785-truncus-arteriosus
Babies with truncus arteriosus need heart surgery within the first weeks of life. The most common procedure is called a Rastelli repair, which creates two separate paths for blood to leave your babys heart. […] Your babys surgeon will: Use a patch to close the hole in your babys heart (VSD) […] Create a new aorta using the existing blood vessel (truncus) […] Create a new aortic valve using the existing truncal valve […] Place an artificial tube (conduit) and artificial valve to create a new pulmonary artery and valve. […] Your childs surgeon will tell you more about future surgeries and what theyll involve. Your child will likely need another surgery within three to 10 years after their first one, and possibly more after that. […] Follow the appointment schedule your childs care team provides. Your child will need routine appointments with a heart specialist (pediatric cardiologist). […] This ongoing care is very important. Your childs providers will: Run tests, including imaging tests and cardiac catheterizations, to see how your childs heart is functioning […] Perform additional surgeries, as needed, to address issues with the conduit or valves.
#21 Truncus Arteriosus | Children’s Hospital of Philadelphia
https://www.chop.edu/conditions-diseases/truncus-arteriosus
Sometimes children with truncus arteriosus experience heart problems later in life, including irregular heartbeat (arrhythmia), a restricted conduit or pulmonary artery, or a leaky aortic valve. Medicine, surgery and/or cardiac catheterization may be required. […] We will help patients who have had truncus arteriosus treatment transition care to an adult cardiologist.
#22 Truncus Arteriosus | Children’s Hospital of Philadelphia
https://www.chop.edu/conditions-diseases/truncus-arteriosus
Open heart surgery is required to treat truncus arteriosus, usually before the baby is 2 months old. More than one operation may be required. […] Following surgery, your child will initially recover in the Evelyn and Daniel M. Tabas Cardiac Intensive Care Unit (CICU), where he will receive round-the-clock attention from a team of dedicated cardiac critical care medicine specialists. As his condition improves, he will be moved to the Cardiac Care Unit. […] A child who has had surgical repair of truncus arteriosus will require lifelong care by a cardiologist. […] Our pediatric cardiologists follow patients with truncus arteriosus until they are young adults, coordinating care with the primary care physician. Patients will need to carefully follow doctors’ advice, including staying on any medications prescribed and, in some cases, limiting certain types of exercise.
#23 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Administer routine postoperative care, initially in the cardiac intensive care unit, following correction of truncus arteriosus. […] Support patients with mechanical ventilation, inotropic medications, and sedation as necessary. […] Focus the remainder of the inpatient stay on providing sufficient enteral nutrition, parental education, and elucidation of the maintenance pharmacologic regimen (if any) that is adopted. […] Postoperative care after repair of truncus arteriosus requires attention to issues that are common to patients with complex congenital heart disease (eg, support of cardiac output) and prevention or management of arrhythmias and end-organ dysfunction. […] Management issues include maintenance of intravascular volume and ventricular filling, inotropic support, and acid-base and electrolyte homeostasis.
#24 Truncus arteriosus | Causes, symptoms, diagnosis | Children’s Wisconsin
https://childrenswi.org/medical-care/herma-heart/conditions/truncus-arteriosus
Children will spend time in the intensive care unit (ICU) after a truncus repair. […] While your child is in the ICU, special equipment will be used to help him/her recover, and may include the following: […] Your child will be kept as comfortable as possible with several different medications; some which relieve pain, and some which relieve anxiety. The staff will also be asking for your input as to how best to soothe and comfort your child. […] After being discharged from the ICU, your child will recuperate in another hospital unit for a few days before going home. You will learn how to care for your child at home before your child is discharged. Your child may need to take medications for a while at home, and these will be explained to you. The staff will give you instructions regarding medications, activity limitations, and follow-up appointments before your child is discharged.
#25 Truncus Arteriosus | Symptoms, Diagnosis & Treatment
https://www.cincinnatichildrens.org/health/t/truncus-arteriosus
Initial treatment begins with stabilizing the infant. Medications to control congestive heart failure are often started. […] Infants will need to be watched closely in the Cardiac Intensive Care Unit while they recover. […] The use of mechanical ventilation, special monitoring lines, and intravenous medicines is typical during this period. […] Gradually, as the infant recovers from surgery, the supporting measures are weaned. The infant is changed to medications by mouth and begins to work on feeding. […] Time in the hospital after surgery ranges from one to three weeks in most cases.
#26 Truncus Arteriosus | SpringerLink
https://link.springer.com/10.1007/978-1-4471-4999-6_48-2
Truncus Arteriosus is a rare congenital anomaly that is characterized by a single great vessel arising from the heart giving rise to both the systemic and pulmonary circulations in a variety of configurations. […] Untreated, Truncus Arteriosus is a fatal condition, which requires early surgical intervention for optimal outcomes. […] Postoperative care in the ICU centers around maintaining cardiac output and managing the effects of residual defects, truncal insufficiency, arrhythmias, or pulmonary hypertension. […] Results in the current era are excellent for straightforward Truncus and less so for those with complex associated anomalies. […] Late complications are related to truncal insufficiency and reoperation for conduit replacement.
#27 Truncus Arteriosus | Symptoms, Diagnosis & Treatment
https://www.cincinnatichildrens.org/health/t/truncus-arteriosus
Initial treatment begins with stabilizing the infant. Medications to control congestive heart failure are often started. […] Infants will need to be watched closely in the Cardiac Intensive Care Unit while they recover. […] The use of mechanical ventilation, special monitoring lines, and intravenous medicines is typical during this period. […] Gradually, as the infant recovers from surgery, the supporting measures are weaned. The infant is changed to medications by mouth and begins to work on feeding. […] Time in the hospital after surgery ranges from one to three weeks in most cases.
#28 Truncus arteriosus | Causes, symptoms, diagnosis | Children’s Wisconsin
https://childrenswi.org/medical-care/herma-heart/conditions/truncus-arteriosus
Children will spend time in the intensive care unit (ICU) after a truncus repair. […] While your child is in the ICU, special equipment will be used to help him/her recover, and may include the following: […] Your child will be kept as comfortable as possible with several different medications; some which relieve pain, and some which relieve anxiety. The staff will also be asking for your input as to how best to soothe and comfort your child. […] After being discharged from the ICU, your child will recuperate in another hospital unit for a few days before going home. You will learn how to care for your child at home before your child is discharged. Your child may need to take medications for a while at home, and these will be explained to you. The staff will give you instructions regarding medications, activity limitations, and follow-up appointments before your child is discharged.
#29 Truncus arteriosus | Causes, symptoms, diagnosis | Children’s Wisconsin
https://childrenswi.org/medical-care/herma-heart/conditions/truncus-arteriosus
Pain medications, such as acetaminophen or ibuprofen, may be recommended to keep your child comfortable at home. Your child’s physician will discuss pain control before your child is discharged from the hospital. […] You may receive additional instructions from your child’s physicians and the hospital staff.
#30 Truncus Arteriosus (TA)
https://library.valleymed.org/library/Wellness/Safety/90,P01826
Truncus arteriosus must be treated with surgery to fix the defects. Typically surgery needs to occur during the first few days or weeks of life. But your child may need medical support until it is time for the operation to take place. Support may include: […] Surgery is often done in the first few weeks after birth to prevent lung damage. The pulmonary arteries are separated from the aorta and reattached to the right ventricle. The pulmonary arteries may be reattached directly to the right ventricle typically using a conduit. The ventricular septal defect is also closed. Your child will stay in the hospital until after the surgical repair. […] Your baby may need high-calorie formula for several weeks or months after surgery. Your baby may also need tube feedings until they are able to feed better. […] Your child will need regular follow-up care at a pediatric or adult congenital cardiac care center throughout life.
#31 Truncus Arteriosus (TA) | Cedars-Sinai
https://www.cedars-sinai.org/health-library/diseases-and-conditions—pediatrics/t/truncus-arteriosus.html
Truncus arteriosus must be treated with surgery to fix the defects. Typically surgery needs to occur during the first few days or weeks of life. But your child may need medical support until it is time for the operation to take place. Support may include: […] Treatment will depend on your child’s symptoms, age, and general health. It will also depend on how severe the condition is. […] Your baby may need high-calorie formula for several weeks or months after surgery. Your baby may also need tube feedings until they are able to feed better. […] Most children who have had truncus arteriosus surgical repair will live healthy lives. Their activity levels, appetite, and growth will often return to normal. […] Your child will need regular follow-up care at a pediatric or adult congenital cardiac care center throughout life.
#32 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
After stabilization in the intensive care unit, removal from mechanical ventilatory and inotropic support, and discontinuation of intracardiac monitoring catheters, transfer the patient to the regular inpatient care area for advancement of feedings and additional postoperative care, depending on the experience and comfort level of the nursing staff on the ward. […] The presence of an interrupted arch and severe truncal regurgitation have been linked to elevated risks and poorer outcomes with surgery for common arterial trunk. […] Maintain close follow-up care in young children after repair of truncus arteriosus. […] Young infants are often discharged on cardiac medications and may usually be weaned over the following months. […] In most patients, conduit regurgitation and obstruction becomes an important issue after early repair; small conduits are utilized and become relatively stenotic with somatic growth or simple degeneration.
#33 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#34 Truncus Arteriosus NCLEX Review
https://www.registerednursern.com/truncus-arteriosus-nclex-review/
If not treated, truncus arteriosus can lead to heart failure within the first 7 days of life. […] Nursing Interventions for Truncus Arteriosus: Medications used to manage/prevent heart failure: Digoxin, Diuretics, ACE inhibitors. […] Digoxin: causes the heart to pump stronger but at a slower rate. NURSES ROLE measure apical pulse for 1 full minute. […] Hold if apical pulse is less than 60 in ADULTS, less than 70 in CHILD, less than 90-110 in INFANTS. […] Monitor intake and output very closely (renal function must be normal so the mediation can clear the body and not build-up, which would lead to toxicity). […] MONITOR potassium level. (hypokalemia increases digoxin toxicity). […] Other nursing interventions: think activity Intolerance, nutrition (will need high calorie supplements plus breast milk or formulafeeding tube), daily weights (infant gaining or losing weight?), assessing lung sounds (fluid in lungs?), think ineffective breathing pattern, strict intake and output, monitoring potassium level, monitor for edema, oxygenation status (skin color, oxygen saturation), post-opt care.
#35 Truncus Arteriosus | Children’s Hospital of Philadelphia
https://www.chop.edu/conditions-diseases/truncus-arteriosus
Open heart surgery is required to treat truncus arteriosus, usually before the baby is 2 months old. More than one operation may be required. […] Following surgery, your child will initially recover in the Evelyn and Daniel M. Tabas Cardiac Intensive Care Unit (CICU), where he will receive round-the-clock attention from a team of dedicated cardiac critical care medicine specialists. As his condition improves, he will be moved to the Cardiac Care Unit. […] A child who has had surgical repair of truncus arteriosus will require lifelong care by a cardiologist. […] Our pediatric cardiologists follow patients with truncus arteriosus until they are young adults, coordinating care with the primary care physician. Patients will need to carefully follow doctors’ advice, including staying on any medications prescribed and, in some cases, limiting certain types of exercise.
#36 Truncus Arteriosus | American Heart Association
https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/truncus-arteriosus
Children with truncus arteriosus need regular follow-up with a pediatric cardiologist and they may need to take medicine after surgery. Your childâs cardiologist will evaluate with a variety of tests including electrocardiograms and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] For patients with uncorrected or partially corrected truncus arteriosus, antibiotics are recommended before certain dental procedures to prevent endocarditis. […] Patients with truncus arteriosus need regular follow-up with a cardiologist with special training in adult congenital heart disease. You may need to take medicine after your operation to help your heart pump better. […] Your cardiologist will monitor you with a variety of tests. These include electrocardiograms, Holter monitors, exercise stress tests and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] People who have truncus arteriosus require endocarditis prophylaxis.
#37 Truncus Arteriosus | American Heart Association
https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/truncus-arteriosus
Children with truncus arteriosus need regular follow-up with a pediatric cardiologist and they may need to take medicine after surgery. Your childâs cardiologist will evaluate with a variety of tests including electrocardiograms and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] For patients with uncorrected or partially corrected truncus arteriosus, antibiotics are recommended before certain dental procedures to prevent endocarditis. […] Patients with truncus arteriosus need regular follow-up with a cardiologist with special training in adult congenital heart disease. You may need to take medicine after your operation to help your heart pump better. […] Your cardiologist will monitor you with a variety of tests. These include electrocardiograms, Holter monitors, exercise stress tests and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] People who have truncus arteriosus require endocarditis prophylaxis.
#38 Truncus arteriosus | Altru Health System
https://www.altru.org/health-library/conditions/truncus-arteriosus
Infants with truncus arteriosus need surgery to improve blood flow and oxygen levels. Many procedures or surgeries might be needed, especially as a child grows. Medicines might be given before surgery to help improve heart health. […] Children and adults with surgically repaired truncus arteriosus need regular health checkups for life. […] After surgery for truncus arteriosus, a person needs lifelong follow-up care with a heart doctor specializing in congenital disease. This type of healthcare professional is called a congenital cardiologist.
#39 Truncus Arteriosus | Children’s Hospital of Philadelphia
https://www.chop.edu/conditions-diseases/truncus-arteriosus
Sometimes children with truncus arteriosus experience heart problems later in life, including irregular heartbeat (arrhythmia), a restricted conduit or pulmonary artery, or a leaky aortic valve. Medicine, surgery and/or cardiac catheterization may be required. […] We will help patients who have had truncus arteriosus treatment transition care to an adult cardiologist.
#40 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Truncal valve regurgitation, which may progress even if it was not severe before repair, may become an important cause of persistent failure to thrive, and repair or replacement of the valve may be indicated. […] In patients with associated interruption of the aortic arch, pay particular attention to potential recurrent arch obstruction and compression of the bronchi, both of which may manifest within weeks or months of the initial repair. […] Routine clinical and echocardiographic follow-up care is sufficient to monitor most patients.
#41 Truncus Arteriosus Treatment & Management: Medical Care, Surgical Care, Consultations
https://emedicine.medscape.com/article/892489-treatment
Truncal valve regurgitation, which may progress even if it was not severe before repair, may become an important cause of persistent failure to thrive, and repair or replacement of the valve may be indicated. […] In patients with associated interruption of the aortic arch, pay particular attention to potential recurrent arch obstruction and compression of the bronchi, both of which may manifest within weeks or months of the initial repair. […] Routine clinical and echocardiographic follow-up care is sufficient to monitor most patients.
#42 Truncus Arteriosus | American Heart Association
https://www.heart.org/en/health-topics/congenital-heart-defects/about-congenital-heart-defects/truncus-arteriosus
Children with truncus arteriosus need regular follow-up with a pediatric cardiologist and they may need to take medicine after surgery. Your childâs cardiologist will evaluate with a variety of tests including electrocardiograms and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] For patients with uncorrected or partially corrected truncus arteriosus, antibiotics are recommended before certain dental procedures to prevent endocarditis. […] Patients with truncus arteriosus need regular follow-up with a cardiologist with special training in adult congenital heart disease. You may need to take medicine after your operation to help your heart pump better. […] Your cardiologist will monitor you with a variety of tests. These include electrocardiograms, Holter monitors, exercise stress tests and echocardiograms to determine when another procedure such as cardiac catheterization may be needed. […] People who have truncus arteriosus require endocarditis prophylaxis.
#43 Truncus Arteriosus â Tests & Treatment | MedStar Health
https://www.medstarhealth.org/services/truncus-arteriosus
Truncus arteriosus requires lifesaving surgery shortly after birth and regular, lifelong follow-up heart care. […] You may need to limit your physical activity or avoid some high-intensity sports if you were treated for truncus arteriosus as a baby. Youll also need to take antibiotics before any dental procedures or surgeries to avoid endocarditis, an infection of the hearts lining.
#44 Truncus Arteriosus (TA) | Valley Children’s Healthcare
https://www.valleychildrens.org/services/heart/conditions-we-treat/truncus-arteriosus
Truncus arteriosus must be treated with surgery to fix the defects. Typically surgery needs to occur during the first few days or weeks of life. But your child may need medical support until it is time for the operation to take place. Support may include: […] Nutritional support may include: […] Surgery is often done in the first few weeks after birth to prevent lung damage. The pulmonary arteries are separated from the aorta and reattached to the right ventricle. The pulmonary arteries may be reattached directly to the right ventricle typically using a conduit. The ventricular septal defect is also closed. Your child will stay in the hospital until after the surgical repair. […] Most children who have had truncus arteriosus surgical repair will live healthy lives. Their activity levels, appetite, and growth will often return to normal. Talk with your child’s cardiologist about what activities and sports are safe for your child. […] Your child will need regular follow-up care at a pediatric or adult congenital cardiac care center throughout life.
#45 Truncus arteriosus – Diagnosis and treatment – Mayo Clinic
https://www.mayoclinic.org/diseases-conditions/truncus-arteriosus/diagnosis-treatment/drc-20364277
Infants with truncus arteriosus need surgery to improve blood flow and oxygen levels. Many procedures or surgeries might be needed, especially as a child grows. Medicines might be given before surgery to help improve heart health. […] Children and adults with surgically repaired truncus arteriosus need regular health checkups for life. […] After surgery for truncus arteriosus, a person needs lifelong follow-up care with a heart doctor specializing in congenital disease. This type of healthcare professional is called a congenital cardiologist. […] Caring for a baby with a serious heart problem, such as truncus arteriosus, can be challenging. Here are some strategies that might be helpful. […] If you or your child had truncus arteriosus, your healthcare professional may recommend taking a few steps to protect the heart. […] Talk about your concerns. You might worry about the risks of strenuous activity, especially after heart repair surgery. Ask your child’s heart doctor, called a pediatric cardiologist, which activities are safe for your child.
#46 Truncus Arteriosus | Children’s Hospital of Philadelphia
https://www.chop.edu/conditions-diseases/truncus-arteriosus
Sometimes children with truncus arteriosus experience heart problems later in life, including irregular heartbeat (arrhythmia), a restricted conduit or pulmonary artery, or a leaky aortic valve. Medicine, surgery and/or cardiac catheterization may be required. […] We will help patients who have had truncus arteriosus treatment transition care to an adult cardiologist.
#47 Truncus Arteriosus | UK Healthcare
https://ukhealthcare.uky.edu/gill-heart-vascular-institute/conditions/adult-congenital-heart-disease/truncus-arteriosus
Truncus arteriosus is a congenital heart defect that is present at birth. It occurs when the blood vessels leading away from the heart don’t completely separate, allowing the aorta and pulmonary artery to connect. This results in whats known as a truncal valve. […] Truncus arteriosus is a critical congenital heart defect, which means surgery or another procedure is almost always needed immediately after birth. Additional surgeries or procedures may also be needed throughout the patients life, so follow-up care with a cardiologist experienced in the care of adults with congenital heart defects is critical. […] At all ages, close monitoring and expert care for CHD patients are essential. […] To guide teens and their families through the transition, UK Gill Heart Vascular Institute team members talk about the transition early and often.
#48 Truncus arteriosus – Diagnosis and treatment – Mayo Clinic
https://www.mayoclinic.org/diseases-conditions/truncus-arteriosus/diagnosis-treatment/drc-20364277
Infants with truncus arteriosus need surgery to improve blood flow and oxygen levels. Many procedures or surgeries might be needed, especially as a child grows. Medicines might be given before surgery to help improve heart health. […] Children and adults with surgically repaired truncus arteriosus need regular health checkups for life. […] After surgery for truncus arteriosus, a person needs lifelong follow-up care with a heart doctor specializing in congenital disease. This type of healthcare professional is called a congenital cardiologist. […] Caring for a baby with a serious heart problem, such as truncus arteriosus, can be challenging. Here are some strategies that might be helpful. […] If you or your child had truncus arteriosus, your healthcare professional may recommend taking a few steps to protect the heart. […] Talk about your concerns. You might worry about the risks of strenuous activity, especially after heart repair surgery. Ask your child’s heart doctor, called a pediatric cardiologist, which activities are safe for your child.
#49
https://myhealth.alberta.ca/Health/aftercareinformation/pages/conditions.aspx?hwid=abr8596
Your baby will be kept comfortable and warm. […] It’s hard to be apart from your baby, especially when you worry about your baby’s condition. Know that the hospital staff is well prepared to care for babies with this condition. They will do everything they can to help. If you need it, ask for support from friends and family. You can also ask the hospital staff about counselling and support. […] Follow-up care is a key part of your child’s treatment and safety. Be sure to make and go to all appointments, and call your doctor or nurse advice line (811 in most provinces and territories) if your child is having problems. It’s also a good idea to know your child’s test results and keep a list of the medicines your child takes.
#50 Truncus Arteriosus (for Parents) | Nemours KidsHealth
https://kidshealth.org/en/parents/truncus-arteriosus.html
Babies with truncus arteriosus need open-heart surgery to prevent problems. Most babies have this surgery in the first month of life. […] Before surgery, special medicines may be given to the infants to keep them stable and help prepare them for surgery. In some cases, more than one operation is needed. […] All children with truncus arteriosus need regular visits with their doctors to help prevent any problems. […] If your child has truncus arteriosus, it can feel overwhelming. But you’re not alone. The care team is there to support you and your child. Be sure to ask when you have questions.
#51 Truncus Arteriosus | SpringerLink
https://link.springer.com/10.1007/978-1-4471-4999-6_48-2
Truncus Arteriosus is a rare congenital anomaly that is characterized by a single great vessel arising from the heart giving rise to both the systemic and pulmonary circulations in a variety of configurations. […] Untreated, Truncus Arteriosus is a fatal condition, which requires early surgical intervention for optimal outcomes. […] Postoperative care in the ICU centers around maintaining cardiac output and managing the effects of residual defects, truncal insufficiency, arrhythmias, or pulmonary hypertension. […] Results in the current era are excellent for straightforward Truncus and less so for those with complex associated anomalies. […] Late complications are related to truncal insufficiency and reoperation for conduit replacement.
#52 Truncus Arteriosus
https://www.rwjbh.org/treatment-care/heart-and-vascular-care/diseases-conditions/congenital-heart-disease/truncus-arteriosus/
If not treated immediately, life-threatening consequences can occur. […] Surgery to repair truncus arteriosus is generally successful, especially if the repair occurs before your baby is one month old. […] Truncus arteriosus is most often fatal without early intervention. Therefore, intervention is critical. […] Some of treatment options include: […] Truncus arteriosus Treatment Care offered at these locations in your neighborhood.
#53 Truncus Arteriosus > Fact Sheets > Yale Medicine
https://www.yalemedicine.org/conditions/truncus-arteriosus
Truncus arteriosus is a congenital heart defect that prevents the heart from sending enough oxygen-rich blood throughout the body. This occurs because blood vessels within a fetus’s heart did not develop normally during pregnancy. The condition causes heart failure, and, without treatment, babies may die within the first year of life. […] Babies born with truncus arteriosus usually experience heart failure within the first few weeks of life. However, when the condition is surgically corrected during infancy, more than 80% of patients live to adulthood. Most patients do quite well, especially with improving surgical techniques and more options for aortic and pulmonic valve repairs and replacements. Follow-up cardiology care is lifelong for these patients. […] Doctors surgically correct truncus arteriosus within the first few months of a baby’s life. A newborn may need medication (diuretics, digoxin, and ACE inhibitors) to manage the symptoms of heart failure before surgery.
#54 Truncus Arteriosus > Fact Sheets > Yale Medicine
https://www.yalemedicine.org/conditions/truncus-arteriosus
The surgical correction of truncus arteriosus helps many patients lead normal lives. After surgery, more than 80% of patients live to age 20 or older. Patients will need to have their heart monitored by a cardiologist regularly for the rest of their lives. Most patients will need follow-up surgery as they get older.
#55 Truncus Arteriosus (TA) | Cedars-Sinai
https://www.cedars-sinai.org/health-library/diseases-and-conditions—pediatrics/t/truncus-arteriosus.html
Truncus arteriosus must be treated with surgery to fix the defects. Typically surgery needs to occur during the first few days or weeks of life. But your child may need medical support until it is time for the operation to take place. Support may include: […] Treatment will depend on your child’s symptoms, age, and general health. It will also depend on how severe the condition is. […] Your baby may need high-calorie formula for several weeks or months after surgery. Your baby may also need tube feedings until they are able to feed better. […] Most children who have had truncus arteriosus surgical repair will live healthy lives. Their activity levels, appetite, and growth will often return to normal. […] Your child will need regular follow-up care at a pediatric or adult congenital cardiac care center throughout life.
#56 Truncus arteriosus in children â Childrenâs Health Cardiology
https://www.childrens.com/specialties-services/conditions/truncus-arteriosus
A baby with truncus arteriosus needs corrective heart surgery within the first month of life. Our pediatric heart specialists assess your babys unique heart anatomy and overall health to design a customized treatment plan. Because of our extensive experience with complex pediatric heart surgeries in infants, you can feel confident placing your baby in our care. […] Even after surgery, a child may develop an obstructed valve (stenosis), leaky heart valve (regurgitation), an abnormal heart rhythm, arrhythmia or weakened heart muscle. Ongoing heart monitoring by a cardiologist can catch these problems early and prevent serious complications. […] Without surgery, truncus arteriosus is a life-threatening condition. With proper, ongoing heart monitoring, most children live full adult lives. A cardiologist should monitor your child’s heart health to diagnose potential problems quickly.